Excel File Text File All mouse models of kidney disease with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      Alport syndrome 2 Col4a3tm1Dec/Col4a3tm1Dec 129-Col4a3tm1Dec/J J:158731 View
Alport syndrome 2 Col4a3tm1Dec/Col4a3tm1Dec 129X1/SvJ-Col4a3tm1Dec J:91619 View
Alport syndrome 2 Col4a3tm1Dec/Col4a3tm1Dec involves: 129X1/SvJ * C57BL/6 J:37963 View
Alport syndrome 2 Col4a3tm1Jhm/Col4a3tm1Jhm involves: 129S1/Sv * 129X1/SvJ J:37017, J:207595 View
Alport syndrome 2 Col4a3tm1Jhm/Col4a3tm1Jhm
Mmp9tm1Tvu/Mmp9tm1Tvu		 involves: 129S1/Sv * 129S6/SvEvTac * 129X1/SvJ J:63137 View
Alport syndrome 2 Col4a4bwk/Col4a4bwk 129S1.NON(NZO)-Col4a4bwk/PgnJ J:223185 View
Alport syndrome 2 Col4a4bwk/Col4a4bwk D2.NON(NZO)-Col4a4bwk/GrsrJ J:223185 View
Alport syndrome 2 Col4a4bwk/Col4a4bwk NON;NZO-Col4a4bwk/J J:223185 View
Alport syndrome 2 Col4a4m1Btlr/Col4a4m1Btlr C57BL/6J-Col4a4m1Btlr J:158794, J:170552 View
Alport syndrome 2 Col4a4m1H/Col4a4m1H involves: C3H/HeH * C57BL/6J J:285510 View
autosomal dominant polycystic kidney disease Pkd2tm1.1Gwu/Pkd2tm1.1Gwu
Tg(Vil1-cre)997Gum/0		 involves: C57BL/6 * C57BL/6J * SJL J:265516 View
autosomal dominant pseudohypoaldosteronism type 1 Nr3c2tm1Gsc/Nr3c2tm1Gsc involves: 129P2/OlaHsd * C57BL/6 J:77285 View
autosomal recessive polycystic kidney disease Pkhd1tm1.1Ggg/Pkhd1tm1.1Ggg involves: 129S/SvEv * 129S4/SvJae * C57BL/6 J:125113 View
autosomal recessive polycystic kidney disease Pkhd1tm1Cjwa/Pkhd1tm1Cjwa involves: 129S6/SvEvTac * FVB/N J:140302 View
autosomal recessive polycystic kidney disease Pkhd1tm1Gwu/Pkhd1tm1Gwu involves: C57BL/6 J:167782 View
autosomal recessive polycystic kidney disease Pkhd1tm1Gwu/Pkhd1tm1Gwu Not Specified J:143394 View
autosomal recessive polycystic kidney disease Pkhd1tm1Sswi/Pkhd1tm1Sswi B6.Cg-Pkhd1tm1Sswi J:186064 View
autosomal recessive polycystic kidney disease Pkhd1tm2Cjwa/Pkhd1tm2Cjwa either: B6.129(Cg)-Pkhd1tm2Cjwa or C.129(Cg)-Pkhd1tm2Cjwa J:187735 View
Bartter disease type 1 Slc12a1tm1Tkh/Slc12a1tm1Tkh involves: 129S6/SvEvTac J:62224 View
Bartter disease type 1 Slc12a1urehr3/Slc12a1urehr3 involves: C3HeB/FeJ J:159994 View
Bartter disease type 2 Kcnj1tm1Ges/Kcnj1tm1Ges involves: 129X1/SvJ * Black Swiss J:79354 View
Bartter disease type 3 Clcnkbem1Haca/Clcnkbem1Haca C57BL/6-Clcnkbem1Haca J:259681 View
Bartter disease type 4a Bsndtm1.1Suc/Bsndtm1.1Suc involves: 129S4/SvJae * C57BL/6 J:175265 View
Bartter disease type 4a Bsndtm1Tjj/Bsndtm1Tjj
Tg(Sox10-cre)1Wdr/0		 involves: 129/Sv * 129X1/SvJ * C57BL/6 J:143314 View
cystinuria Slc3a1m1Crl/Slc3a1m1Crl 129S2/SvPasCrl J:219017 View
cystinuria Slc3a1pbl/Slc3a1pbl C3HeB/FeJ-Slc3a1pbl J:85461 View
cystinuria Slc3a1pbl/Slc3a1pbl involves: C3HeB/FeJ * MRL/MpJ J:85461 View
cystinuria Slc3a1tm1Jat/Slc3a1tm1Jat involves: 129 * C57BL/6 J:254981, J:254803 View
cystinuria Slc7a9tm1Nune/Slc7a9+ involves: 129P2/OlaHsd * C57BL/6J J:85462 View
cystinuria Slc7a9tm1Nune/Slc7a9tm1Nune involves: 129P2/OlaHsd * C57BL/6J J:85462 View
focal segmental glomerulosclerosis 1 Actn4tm1Mrpk/Actn4tm1Mrpk involves: 129 * C57BL/6 J:83911 View
focal segmental glomerulosclerosis 2 Tg(NPHS2-Trpc6)F419Walz/0 involves: C57BL/6J * CBA/J J:165112 View
focal segmental glomerulosclerosis 2 Tg(NPHS2-Trpc6*E896K)F75aWalz/0 involves: C57BL/6J * CBA/J J:165112 View
focal segmental glomerulosclerosis 2 Tg(NPHS2-Trpc6*P111Q)F615Walz/0 involves: C57BL/6J * CBA/J J:165112 View
focal segmental glomerulosclerosis 3 Cd2apem1Irgu/Cd2apem1Irgu C57BL/6-Cd2apem1Irgu J:294238 View
Gitelman syndrome Slc12a3em3Gpt/Slc12a3em4Gpt involves: C57BL/6 J:336073 View
Gitelman syndrome Slc12a3tm1Ges/Slc12a3tm1Ges Not Specified J:50596 View
hemolytic-uremic syndrome Cfhtm1Mbo/Cfhtm1Mbo
Tg(CAG-Cfh*)#Mcp/0		 involves: 129/Sv * C57BL/6 * CBA J:125860 View
IgA glomerulonephritis Scgb1a1tm1Abm/Scgb1a1tm1Abm involves: 129S1/Sv * 129X1/SvJ J:57504 View
IgA glomerulonephritis Tg(MMTV-Scgb1a1)#Abm/0 involves: C57BL/6 * SJL J:57504 View
karyomegalic interstitial nephritis Fan1tm1.1Jrou/Fan1tm1.1Jrou involves: 129P2/OlaHsd J:232403 View
karyomegalic interstitial nephritis Fan1tm1a(KOMP)Wtsi/Fan1tm1a(KOMP)Wtsi 129S1.B6-Fan1tm1a(KOMP)Wtsi J:242198 View
karyomegalic interstitial nephritis Fan1tm1d(KOMP)Wtsi/Fan1tm1d(KOMP)Wtsi involves: C57BL/6N * FVB/N J:232402 View
Liddle syndrome Scnn1btm1.1Ipt/Scnn1btm1.1Ipt involves: 129P2/OlaHsd * C57BL/6J * FVB/N J:59840 View
nephrogenic diabetes insipidus Aqp2F204V/Aqp2F204V C57BL/6-Aqp2F204V J:105809 View
nephrogenic diabetes insipidus Aqp2tm1(AQP2)Suc/Aqp2+ involves: 129S4/SvJae * C57BL/6 J:113716 View
nephrogenic diabetes insipidus Aqp2tm1(cre)Blyg/Aqp2tm1(cre)Blyg involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:121445 View
nephrogenic diabetes insipidus Avpr2tm1Jwe/Avpr2+ involves: 129S1/Sv * 129X1/SvJ * CF-1 J:66094 View
nephrogenic diabetes insipidus Avpr2tm1Jwe/Y involves: 129S1/Sv * 129X1/SvJ * CF-1 J:66094 View
nephrogenic diabetes insipidus type 2 Aqp2cph/Aqp2cph C57BL/6J-Aqp2cph J:109463 View
nephronophthisis 1 Nphp1em1Lisu/Nphp1em1Lisu C57BL/6J-Nphp1em1Lisu J:324503 View
nephronophthisis 1 Nphp1em1Ssau/Nphp1em1Ssau C57BL/6J-Nphp1em1Ssau J:360848 View
nephronophthisis 2 Invsinv/Invsinv involves: FVB/N J:132552 View
nephronophthisis 3 Nphp3pcy/Nphp3pcy involves: KK J:91453 View
nephronophthisis 3 Nphp3pcy/Nphp3tm1Cbe involves: C57BL/6 * CD-1 * KK/Upj J:139258 View
nephronophthisis 4 Nphp4nmf192/Nphp4nmf192 involves: C57BL/6J J:167232 View
nephronophthisis 7 Glis2tm1Tre/Glis2tm1Tre B6.129P2-Glis2tm1Tre J:123510 View
nephrotic syndrome type 26 Lama5mpc205H/Lama5mpc205H B6(Cg)-Lama5mpc205H J:344185 View
nephrotic syndrome type 26 Lama5mpc205H/Lama5mpc205H C3.B6(C)-Lama5mpc205H J:344185 View
neurohypophyseal diabetes insipidus Avptm1Hari/Avp+ involves: 129S1/Sv * 129X1/SvJ * C57BL/6J J:147993 View
neurohypophyseal diabetes insipidus Avptm1Lja/Avp+ involves: 129S1/Sv * 129X1/SvJ J:148012 View
polycystic kidney disease 1 Gpsm1tm1.1Lajb/Gpsm1tm1.1Lajb
Pkd1tm1.1Fqi/Pkd1tm1.1Fqi		 involves: 129S6/SvEvTac J:193175 View
polycystic kidney disease 1 Pkd1b2b1585Clo/Pkd1b2b1585Clo C57BL/6J-Pkd1b2b1585Clo J:175213 View
polycystic kidney disease 1 Pkd1tm1.1Fqi/Pkd1tm1.1Fqi involves: 129S6/SvEvTac J:193175 View
polycystic kidney disease 1 Pkd1tm1.1Pcha/Pkd1tm1.1Pcha involves: 129S1/Sv * C57BL/6 J:193544 View
polycystic kidney disease 1 Pkd1tm1.1Pcha/Pkd1tm2Som
Tg(Cdh16-cre)91Igr/0		 involves: 129 * 129S4/SvJae * C57BL/6 * ICR J:244067 View
polycystic kidney disease 1 Pkd1tm1Bdgz/Pkd1+ involves: 129S1/Sv * 129X1/SvJ J:130086 View
polycystic kidney disease 1 Pkd1tm1Djmp/Pkd1tm1Djmp involves: 129P2/OlaHsd * C57BL/6 J:94582 View
polycystic kidney disease 1 Pkd1tm1Ggg/Pkd1tm1Ggg Not Specified J:76062 View
polycystic kidney disease 1 Pkd1tm1Gztn/Pkd1tm1Gztn
Gt(ROSA)26Sortm9(cre/ESR1)Arte/Gt(ROSA)26Sor+		 involves: 129S/Sv * 129S7/SvEvBrd * C57BL/6 J:162080 View
polycystic kidney disease 1 Pkd1tm1Jzh/Pkd1+ either: (involves: 129S4/SvJae * C57BL/6) or (involves: 129S4/SvJae * BALB/c) J:43193, J:52573, J:72627 View
polycystic kidney disease 1 Pkd1tm1Jzh/Pkd1tm1Jzh either: (involves: 129S4/SvJae * C57BL/6) or (involves: 129S4/SvJae * BALB/c) J:43193, J:72627, J:81443 View
polycystic kidney disease 1 Pkd1tm1Rsa/Pkd1+ involves: 129S4/SvJaeSor J:72238 View
polycystic kidney disease 1 Pkd1tm1Shh/Pkd1tm1.1Pcha involves: 129P2/OlaHsd * 129S1/Sv * C57BL/6 J:193544 View
polycystic kidney disease 1 Pkd1tm1Som/Pkd1+
Tg(Pkd1*)39Mtru/0		 involves: 129/Sv * C57BL/6J * CBA/J * SJL J:198147 View
polycystic kidney disease 1 Pkd1tm2.1Ggg/Pkd1tm2.1Ggg involves: 129S4/SvJae * Black Swiss * C57BL/6 J:103719 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(Col1a1-cre)1Bek/0		 involves: 129S4/SvJae * CD-1 J:191967 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(Hoxb7-cre)13Amc/0		 involves: 129S4/SvJae * C57BL/6 J:171619 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(MMTV-cre)4Mam/0		 involves: 129S4/SvJae * FVB J:103719 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(Nes-cre)Wme/0		 involves: 129S4/SvJae * C57BL/6 * CBA J:185855 View
polycystic kidney disease 1 Pkd1tm2Jzh/Pkd1+ either: (involves: 129S4/SvJae * BALB/c) or (involves: 129S4/SvJae * C57BL/6) J:72627 View
polycystic kidney disease 1 Pkd1tm2Jzh/Pkd1tm2Jzh either: (involves: 129S4/SvJae * BALB/c) or (involves: 129S4/SvJae * C57BL/6) J:72627 View
polycystic kidney disease 1 Pkd1tm2Jzh/Pkd1tm2Jzh involves: 129S4/SvJae * C57BL/6 J:140012 View
polycystic kidney disease 1 Pkd1tm2Som/Pkd1tm2.1Som
Tg(Cdh16-cre)91Igr/0		 involves: C57BL/6 * ICR * SJL J:135301 View
polycystic kidney disease 1 Pkd1tm2Som/Pkd1tm2Som
Tg(Cdh16-cre)91Igr/0		 involves: 129S4/SvJae * C57BL/6 * ICR J:244067 View
polycystic kidney disease 1 Pkd1tm2Som/Pkd1tm2Som
Tg(Pkhd1-cre)1Igr/0		 involves: C57BL/6 * SJL J:379194 View
polycystic kidney disease 1 Pkd1tm3.1Jzh/Pkd1tm3.1Jzh involves: 129P2/OlaHsd * C57BL/6 J:140012 View
polycystic kidney disease 1 Pkd1tm3Jzh/Pkd1tm3Jzh
Tg(Ggt1-cre)M3Egn/0		 involves: 129P2/OlaHsd * C57BL/6 * SJL J:140012 View
polycystic kidney disease 1 Tg(Pkd1*)39Mtru/0 involves: C57BL/6J * CBA/J J:198147 View
polycystic kidney disease 2 Pkd2tm1Dwo/Pkd2tm1Dwo either: (involves: 129S1/Sv * 129X1/SvJ) or (involves: 129S1/Sv * 129X1/SvJ * C57BL/6) J:77401 View
polycystic kidney disease 2 Pkd2tm1Som/Pkd2+ involves: 129/Sv * C57BL/6J * SJL J:47035 View
polycystic kidney disease 2 Pkd2tm1Som/Pkd2tm1Som involves: 129/Sv * C57BL/6J * SJL J:47035 View
polycystic kidney disease 2 Pkd2tm1Som/Pkd2tm2Som involves: 129/Sv * C57BL/6J * SJL J:47035 View
polycystic kidney disease 2 Pkd2tm2Som/Pkd2+ involves: 129/Sv * C57BL/6J * SJL J:59314 View
polycystic kidney disease 2 Pkd2tm2Som/Pkd2tm2Som involves: 129/Sv * C57BL/6J * SJL J:59314 View
polycystic kidney disease 2 Pkd2tm3Som/Pkd2tm3Som
Tg(Pkhd1-cre)1Igr/0		 involves: 129S4/SvJae * C57BL/6 J:244067 View
polycystic kidney disease 4 Pkhd1em1Mrug/Pkhd1+ involves: C57BL/6J J:281464 View
polycystic kidney disease 4 Pkhd1em1Mrug/Pkhd1em1Mrug involves: C57BL/6J J:281464 View
pseudohypoaldosteronism Klhl3tm1.1Esoh/Klhl3+ involves: C57BL/6 J:214330 View
pseudohypoaldosteronism Klhl3tm1.1Slin/Klhl3+ Not Specified J:284284 View
pseudohypoaldosteronism Klhl3tm1.1Slin/Klhl3tm1.1Slin Not Specified J:284284 View
pseudohypoaldosteronism Klhl3tm2.1Esoh/Klhl3tm2.1Esoh involves: C57BL/6 * C57BL/6J J:244278 View
pseudohypoaldosteronism Wnk4em1Cjc/Wnk4em1Cjc Not Specified J:274218 View
renal tubular acidosis Atp6v0a4tm1.1Fekf/Atp6v0a4tm1.1Fekf involves: C57BL/6 J:188593 View
renal tubular acidosis Slc4a1tm1Llp/Slc4a1tm1Llp involves: 129S4/SvJae * C57BL/6J J:148154 View
renal tubular acidosis Slc4a4tm1.1Slin/Slc4a4tm1.1Slin involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:186877 View
X-linked Alport syndrome Col4a5em1Keha/Y C57BL/6J-Col4a5em1Keha J:283613 View
X-linked Alport syndrome Col4a5tm1Yseg/Col4a5+ B6.Cg-Col4a5tm1Yseg J:102306, J:210414 View
X-linked Alport syndrome Col4a5tm1Yseg/Y B6.Cg-Col4a5tm1Yseg J:102306, J:210414 View
X-linked nephrogenic diabetes insipidus Avpr2tm2.1Jwe/Y
Tg(CAG-cre/Esr1*)5Amc/0		 involves: 129 * C57BL/6 J:324922 View
      Alport syndrome 2 Mpv17/Mpv17 CFW-Mpv17/J J:48653 View
autosomal dominant polycystic kidney disease Bicc1jcpk/Bicc1+ involves: 101 * C3H * T STOCK J:23047 View
autosomal dominant polycystic kidney disease Nphp3pcy/Nphp3pcy either: D2.KK-Nphp3pcy or (involves: DBA/2Fg * DBA/2J * KK) J:11399 View
autosomal dominant polycystic kidney disease Nphp3pcy/Nphp3pcy involves: KK J:244067 View
autosomal dominant polycystic kidney disease Nphp3pcy/Nphp3pcy KK-Nphp3pcy J:8302 View
autosomal dominant polycystic kidney disease Tg(HBB-Myc)#Cos/0 involves: C57BL/6J * CBA/J J:45203 View
autosomal dominant tubulointerstitial kidney disease Tg(Umod*C147W)958Lura/0 involves: FVB J:161532 View
autosomal dominant tubulointerstitial kidney disease Umodtm1Kuma/Umodtm1Kuma involves: 129 J:96653 View
autosomal recessive polycystic kidney disease Arl3Gt(OST263303)Lex/Arl3Gt(OST263303)Lex involves: 129S5/SvEvBrd J:107331 View
autosomal recessive polycystic kidney disease Bicc1jcpk-bpk/Bicc1jcpk-bpk BALB/c-Bicc1jcpk-bpk J:13276, J:21554, J:36348 View
autosomal recessive polycystic kidney disease Bicc1jcpk-bpk/Bicc1jcpk-bpk involves: BALB/c * CAST/EiJ J:36348 View
autosomal recessive polycystic kidney disease Bicc1jcpk/Bicc1jcpk-bpk involves: 101 * BALB/c * C3H * C57BL/6J * T STOCK J:36348 View
autosomal recessive polycystic kidney disease Bicc1jcpk/Bicc1jcpk involves: 101 * C3H * C57BL/6J * T STOCK J:36348 View
autosomal recessive polycystic kidney disease Bicc1jcpk/Bicc1jcpk involves: 101 * C3H * T STOCK J:23047 View
autosomal recessive polycystic kidney disease Bicc1tm1Emdr/Bicc1tm1Emdr B6SJL-Bicc1tm1Emdr J:121683 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk B6(Cg)-Cys1cpk/J J:6718, J:9290 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk B6(Cg)-Cys1cpk/JUnc J:7202 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk C.B6(Cg)-Cys1cpk J:99616 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk D2J.B6(Cg)-Cys1cpk J:99620 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk involves: C57BL/6J * CD-1 J:33739 View
autosomal recessive polycystic kidney disease Dzip1lwarpy/Dzip1lwarpy involves: C3H * C57BL/6 J:249936 View
autosomal recessive polycystic kidney disease Dzip1lwarpy/Dzip1lwarpy involves: C57BL/6 * CD-1 J:249936 View
autosomal recessive polycystic kidney disease Ift88Tg737Rpw/Ift88Tg737Rpw C3.FVB-Ift88Tg737Rpw J:18508, J:73583 View
autosomal recessive polycystic kidney disease Ift88Tg737Rpw/Ift88Tg737Rpw FVB/N-Ift88Tg737Rpw J:18508, J:37149, J:73583, J:95813 View
autosomal recessive polycystic kidney disease Ift88Tg737Rpw/Ift88Tg737Rpw involves: C3H * FVB/N J:73583 View
autosomal recessive polycystic kidney disease Ift88Tg737Rpw/Ift88Tg737Rpw involves: FVB/N J:65500, J:90990 View
autosomal recessive polycystic kidney disease Nek1kat-2J/Nek1kat-2J C57BL/6J-Nek1kat-2J/J J:37799 View
autosomal recessive polycystic kidney disease Nek1kat/Nek1kat involves: C3HeB/FeJLe * C57BL/6J * RBF/Dn J:37799 View
autosomal recessive polycystic kidney disease Nek8jck/Nek8jck involves: C57BL/6J J:11885 View
autosomal recessive polycystic kidney disease Pkd1m1Bei/Pkd1m1Bei involves: A/J * FVB/N J:75360 View
autosomal recessive polycystic kidney disease Sclt1Tg(CAG-sb10)1Dla/Sclt1Tg(CAG-sb10)1Dla FVB/N-Sclt1Tg(CAG-sb10)1Dla J:243427 View
autosomal recessive polycystic kidney disease Tg(Pkd1)26Mtru/0 involves: C57BL/6J * CBA/J J:157952 View
autosomal recessive polycystic kidney disease Tsc1tm1Djk/Tsc1tm1Djk
Tg(Pax8-rtTA2S*M2)1Koes/0
Tg(tetO-cre)LC1Bjd/0		 involves: 129S4/SvJae * BALB/c * C57BL/6 * DBA J:140925 View
autosomal recessive pseudohypoaldosteronism type 1 Scnn1btm1Wsh/Scnn1btm1Wsh involves: 129S1/Sv * 129X1/SvJ * C57BL/6J J:53058 View
autosomal recessive pseudohypoaldosteronism type 1 Scnn1gtm1Bhk/Scnn1gtm1Bhk involves: 129P2/OlaHsd * C57BL/6 * DBA/2 J:50528 View
Bartter disease Clcnkbtm1.1Doel/Clcnkbtm1.1Doel involves: 129S1/Sv * 129X1/SvJ J:259639 View
bilateral renal aplasia Npntem1Zhwe/Npntem1Zhwe C57BL/6-Npntem1Zhwe J:314482 View
chronic kidney disease Ermp1em1Gjom/Ermp1+ Not Specified J:361886 View
chronic kidney disease Rtn3tm1Yanr/Rtn3tm1Yanr involves: 129S6/SvEvTac * C57BL/6 J:326034 View
congenital anomalies of kidney and urinary tract Lifrtm1Imx/Lifrtm1Imx B6;129S7-Lifrtm1Imx/J J:242320 View
congenital anomalies of kidney and urinary tract Zng1em1Skan/Zng1em1Skan C57BL/6N-Zng1em1Skan J:326010 View
congenital anomalies of kidney and urinary tract Zng1em2Skan/Zng1em2Skan C57BL/6N-Zng1em2Skan J:326010 View
cystic kidney disease b2b243.2Clo/b2b243.2Clo C57BL/6J-b2b243.2Clo J:175213 View
cystic kidney disease b2b243Clo/b2b243Clo C57BL/6J-b2b243Clo J:175213 View
cystic kidney disease b2b1146Clo/b2b1146Clo C57BL/6J-b2b1146Clo J:175213 View
cystic kidney disease b2b1163Clo/b2b1163Clo C57BL/6J-b2b1163Clo J:175213 View
cystic kidney disease b2b1200.2Clo/b2b1200.2Clo C57BL/6J-b2b1200.2Clo J:175213 View
cystic kidney disease b2b1200Clo/b2b1200Clo C57BL/6J-b2b1200Clo J:175213 View
cystic kidney disease b2b1291.2Clo/b2b1291.2Clo C57BL/6J-b2b1291.2Clo J:175213 View
cystic kidney disease b2b1291Clo/b2b1291Clo C57BL/6J-b2b1291Clo J:175213 View
cystic kidney disease b2b2059Clo/b2b2059Clo C57BL/6J-b2b2059Clo J:175213 View
cystic kidney disease b2b2459Clo/b2b2459Clo C57BL/6J-b2b2459Clo J:175213 View
cystic kidney disease Bicc1b2b222Clo/Bicc1b2b222Clo C57BL/6J-Bicc1b2b222Clo J:175213 View
cystic kidney disease Cep290b2b1454Clo/Cep290b2b1454Clo C57BL/6J-Cep290b2b1454Clo J:175213 View
cystic kidney disease Dnm2b2b2159Clo/Dnm2b2b2159Clo C57BL/6J-Dnm2b2b2159Clo J:175213 View
cystic kidney disease Ephb4b2b2412Clo/Ephb4b2b2412Clo C57BL/6J-Ephb4b2b2412Clo J:175213 View
cystic kidney disease Lama5tm3Jhm/Lama5tm3Jhm involves: 129S1/Sv * 129X1/SvJ J:128225 View
cystic kidney disease Robo1b2b872Clo/Robo1b2b872Clo C57BL/6J-Robo1b2b872Clo J:175213 View
cystic kidney disease Slit2b2b1200.1Clo/Slit2b2b1200.1Clo C57BL/6J-Slit2b2b1200.1Clo J:175213 View
cystic kidney disease Tmem67b2b1163.1Clo/Tmem67b2b1163.1Clo C57BL/6J-Tmem67b2b1163.1Clo J:175213 View
cystic kidney disease Tmem67b2b1291.1Clo/Tmem67b2b1291.1Clo C57BL/6J-Tmem67b2b1291.1Clo J:175213 View
cystic kidney disease Ttc21btm2c(KOMP)Wtsi/Ttc21baln
Gt(ROSA)26Sortm1(cre/ERT)Nat/Gt(ROSA)26Sor+		 involves: 129S1/Sv * 129X1/SvJ * A/J * C57BL/6N J:213263 View
Dent disease Clcn5tm1Gug/Y involves: 129S1/Sv * 129X1/SvJ * C57BL/6J J:66560 View
Dent disease Clcn5tm1Tjj/Y B6.129-Clcn5tm1Tjj J:77111 View
end stage renal disease Cd2apem1Irgu/Cd2apem1Irgu C57BL/6-Cd2apem1Irgu J:294238 View
Fanconi syndrome Hnf4atm1Sad/Hnf4atm1Sad
Six2tm1(tTA,tetO-EGFP/cre)Amc/Six2+		 involves: 129 * 129S1/Sv * 129X1/SvJ * C57BL/6J J:266356 View
Fanconi syndrome Lrp2tm1Her/Lrp2tm1Her involves: 129S7/SvEvBrd J:108230 View
Fanconi syndrome Whammtm1b(KOMP)Wtsi/Whammtm1b(KOMP)Wtsi B6N(Cg)-Whammtm1b(KOMP)Wtsi/3J J:349712 View
focal segmental glomerulosclerosis Cmastm1.1Bwei/Cmastm1.1Bwei
Tg(NPHS2-cre)295Lbh/0		 involves: 129P2/OlaHsd * C57BL/6 * SJL J:286022 View
focal segmental glomerulosclerosis Gt(ROSA)26Sortm3(tetO-Mir193)Arte/Gt(ROSA)26Sor+ involves: 129 * BALB/c * C57BL/6 J:197989 View
focal segmental glomerulosclerosis Gt(ROSA)26Sortm3(tetO-Mir193)Arte/Gt(ROSA)26Sortm3(tetO-Mir193)Arte involves: 129 * BALB/c * C57BL/6 J:197989 View
focal segmental glomerulosclerosis Myo9aem1Atuf/Myo9a+ C57BL/6J-Myo9aem1Atuf J:302901 View
focal segmental glomerulosclerosis Srgap1tm1a(KOMP)Wtsi/Srgap1tm1a(KOMP)Wtsi
Six2tm1(tTA,tetO-EGFP/cre)Amc/Six2+		 involves: 129 * C57BL/6J * C57BL/6N J:333727 View
focal segmental glomerulosclerosis Tnfaip2tm1.1Ohno/Tnfaip2tm1.1Ohno C.Cg-Tnfaip2tm1.1Ohno J:343202 View
Gitelman syndrome Stk39tm1.2Slin/Stk39tm1.2Slin involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:165706 View
Gitelman syndrome Stk39tm1Pawe/Stk39tm1Pawe involves: 129S6/SvEvTac * C57BL/6J J:287773 View
Gitelman syndrome Stk39tm2.1Arte/Stk39tm2.1Arte involves: C57BL/6J J:224087 View
Gitelman syndrome Wnk4tm1Pfi/Wnk4tm1Pfi involves: 129S6/SvEvTac * C57BL/6J J:184790 View
glomerulonephritis Cfiem1Jiwe/Cfiem1Jiwe involves: C57BL/6J J:308307 View
IgA glomerulonephritis B4galt1tm1Yiw/B4galt1tm1Yiw involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:117891 View
IgA glomerulonephritis Tg(Lck-Tnfsf14)24Yxf/? C57BL/6-Tg(Lck-Tnfsf14)24Yxf J:128976 View
IgA glomerulonephritis Tg(Tnfsf13b)1Fma/Tg(Tnfsf13b)1Fma involves: C57BL/6 * DBA/2 J:178227 View
IgA glomerulonephritis Wastm1Sbs/Wastm1Sbs 129S6/SvEvTac-Wastm1Sbs/J J:180407 View
kidney disease Col4a1tm1.1Ics/Col4a1+ involves: 129S2/SvPas * C57BL/6 J:240798 View
kidney disease Col4a1tm1.1Ics/Col4a1tm1.1Ics involves: 129S2/SvPas * C57BL/6 J:240798 View
kidney disease Tg(Umod*C147W)958Lura/0 involves: FVB J:161532 View
kidney disease Umodem1Duf/Umod+ C57BL/6J-Umodem1Duf J:252597 View
kidney disease UmodUrehd1/Umod+ involves: C3HeB/FeJ J:201084 View
kidney disease UmodUrehd1/UmodUrehd1 involves: C3HeB/FeJ J:201084 View
kidney disease Umodurehr4/Umodurehr4 C3HeB/FeJ-Umodurehr4 J:153895 View
membranoproliferative glomerulonephritis C3tm2(C3)Lgmo/C3tm2(C3)Lgmo involves: 129 * C57BL/6 J:369997 View
membranoproliferative glomerulonephritis Cfhtm1Mbo/Cfhtm1Mbo involves: 129/Sv * C57BL/6 J:78193 View
membranoproliferative glomerulonephritis Tg(Lck-Tslp)1Chea/0 B6.Cg-Tg(Lck-Tslp)1Chea J:72982 View
nephroblastoma Tg(Ddx4-cre)1Dcas/0
Tg(EIF1AX-Lin28a)#Gqda/0		 involves: 129S4/SvJae * C57BL/6 * CD-1 * FVB/N J:211179 View
nephrocalcinosis Brd4M1Rvt/Brd4+ involves: BALB/cAnNCrl * C3H/HeH J:277882 View
nephrocalcinosis Polg2M1Rvt/Polg2+ involves: BALB/c * C3H/HeH J:277879 View
nephrogenic diabetes insipidus Aqp3tm1Ask/Aqp3tm1Ask involves: C57BL/6J J:61675 View
nephrogenic diabetes insipidus Clcnkatm1Suc/Clcnkatm1Suc involves: 129P2/OlaHsd * C57BL/6 J:51917 View
nephrogenic diabetes insipidus Grntm1.1Aidi/Grntm1.1Aidi involves: C57BL/6J J:268827 View
nephrogenic diabetes insipidus Sirt1tm1Mcby/Sirt1tm1Mcby involves: 129S1/Sv * 129X1/SvJ * CD-1 J:160869 View
nephrogenic diabetes insipidus Uoxtm1Bay/Uoxtm1Bay involves: 129S7/SvEvBrd * C57BL/6J J:103187 View
nephronophthisis Ahi1tm1Jgg/Ahi1+
Lrp6Gt(Ex187)Byg/Lrp6+		 involves: 129P2/OlaHsd * 129S1/Sv * 129X1/SvJ J:154321 View
nephronophthisis Ahi1tm1Jgg/Ahi1tm1Jgg
Tg(TCF/Lef1-lacZ)34Efu/0		 involves: 129S1/Sv * 129X1/SvJ J:154321 View
nephronophthisis Cep290Gt(CC0582)Wtsi/Cep290Gt(CC0582)Wtsi 129P2/OlaHsd-Cep290Gt(CC0582)Wtsi J:212182 View
nephronophthisis Cntrlb2b1468.1Clo/Cntrlb2b1468.1Clo C57BL/6J-Cntrlb2b1468.1Clo J:175213 View
nephronophthisis Sdccag8Gt(OST40418)Lex/Sdccag8Gt(OST40418)Lex involves: 129S5/SvEvBrd * C57BL/6J J:226661 View
nephronophthisis Wwtr1tm1Whun/Wwtr1tm1Whun either: (involves: 129S6/SvEvTac) or (involves: 129S6/SvEvTac * C57BL/6) J:119488 View
nephrosis Lamb2tm1Jrs/Lamb2tm1Jrs involves: 129S1/Sv * 129X1/SvJ J:27732 View
nephrotic syndrome Arhgdiatm1Ytk/Arhgdiatm1Ytk involves: 129S/SvEv * C57BL/6 * DBA J:57995 View
nephrotic syndrome Fat1tm1.1Nsib/Fat1tm1.1Nsib
Tg(NPHS2-cre)295Lbh/0		 involves: 129/Sv * 129S4/SvJaeSor * C57BL/6 * C57BL/6J * SJL J:234732 View
nephrotic syndrome Itsn2tm1Kure/Itsn2tm1Kure involves: C57BL/6 J:262845 View
nephrotic syndrome Mpv17/Mpv17 CFW-Mpv17/J J:10661, J:108252 View
nephrotic syndrome Nphs1Gt(pT1Betageo)1Ruiz/Nphs1+ involves: 129P2/OlaHsd * C57BL/6 J:86048 View
nephrotic syndrome Nphs1Gt(pT1Betageo)1Ruiz/Nphs1Gt(pT1Betageo)1Ruiz involves: 129P2/OlaHsd * C57BL/6 J:86048 View
nephrotic syndrome Nphs1tm1Ktry/Nphs1tm1Ktry involves: 129X1/SvJ * C57BL/6 J:66970 View
nephrotic syndrome Nphs1tm1Rkl/Nphs1tm1Rkl involves: 129S2/SvPasCrl J:78616 View
nephrotic syndrome Nphs2tm1Antc/Nphs2tm1Antc 129-Nphs2tm1Antc J:87577 View
nephrotic syndrome Nphs2tm1Antc/Nphs2tm1Antc involves: 129 * C57BL/6J J:87577 View
nephrotic syndrome Nphs2tm1Antc/Nphs2tm3.1Antc
Tg(CAG-cre/Esr1*)86Lbgn/0		 involves: 129 * C57BL/6 * DBA J:166320 View
nephrotic syndrome Nphs2tm2.1Antc/Nphs2tm3.1Antc
Tg(CAG-cre/Esr1*)86Lbgn/0		 involves: 129S2/SvPas * C57BL/6 * DBA J:245693 View
nonpapillary renal cell carcinoma Flcntm1Btt/Flcntm1Btt
Tg(Cdh16-cre)91Igr/0		 involves: 129S4/SvJaeSor * C57BL/6 * ICR J:143922 View
obstructive nephropathy Aqp2cph/Aqp2cph C57BL/6J-Aqp2cph J:109463 View
obstructive nephropathy Exoc5tm1c(KOMP)Mbp/Exoc5tm1c(KOMP)Mbp
Tg(Cdh16-cre)91Igr/0		 involves: 129S4/SvJaeSor * C57BL/6N * ICR J:226950, J:250161 View
obstructive nephropathy Mocosem2(IMPC)Ics/Mocosem2(IMPC)Ics involves: C57BL/6N J:336718 View
oligomeganephronia Bcl2tm1Dlo/Bcl2tm1Dlo involves: 129P2/OlaHsd * C57BL/6 J:111022 View
polycystic kidney disease Kif3atm1Gsn/Kif3atm2Gsn
Tg(Cdh16-cre)91Igr/0		 involves: 129S1/Sv * 129X1/SvJ * C57BL/6 * ICR J:83293 View
polycystic kidney disease Tg(Actb-Ptma)T12Clwu/Tg(Actb-Ptma)T12Clwu involves: FVB/N J:128557 View
polycystic kidney disease Tulp3m1Kflj/Tulp3m1Kflj involves: C57BL/6J * FVB/NJ J:284006 View
polycystic kidney disease Xylt2tm1Meh/Xylt2tm1Meh involves: 129P2/OlaHsd J:122291 View
pseudohypoaldosteronism Stk39tm1Pawe/Stk39tm1Pawe
Pvalbtm1(cre)Arbr/Pvalb+		 B6.129-Stk39tm1Pawe Pvalbtm1(cre)Arbr J:287773 View
renal cell carcinoma Nf2tm2Gth/Nf2tm2Gth
Tg(Vil1-cre)20Syr/0		 involves: 129P2/OlaHsd * C57BL/6 * DBA/2 J:150071 View
renal glycosuria Hnrnpftm1Jsdc/Hnrnpftm1Jsdc
Pax8tm1.1(cre)Mbu/Pax8+		 involves: 129P2/OlaHsd * C57BL/6 J:284239 View
      nephroblastoma Col1a1tm2(tetO-LIN28B)Gqda/Col1a1+
Gt(ROSA)26Sortm1(rtTA,EGFP)Nagy/Gt(ROSA)26Sor+
Wt1tm2(cre/ERT2)Wtp/Wt1+		 involves: 129S1/Sv * 129S4/SvJae * 129X1/SvJ * C57BL/6 J:211179 View
Transgenes and
Other Mutations		     autosomal dominant tubulointerstitial kidney disease Tg(Umod*C217G)1Xrw/0 involves: FVB/N J:252420 View
autosomal recessive polycystic kidney disease T(2;10)67Gso/T(2;10)67Gso involves: 101 * C3H * C3H/Rl * C57BL/RlGso * SEC/RlGso J:75799 View
cystic kidney disease Tg(Pax8-rtTA2S*M2)1Koes/0
Tg(tetO-MYC)36aBop/0		 involves: C57BL/6 * DBA * FVB/N J:140925 View
cystic kidney disease Tg(Pklr-HRAS*G12V)21Ak/0 involves: C57BL/6 * DBA/2 J:44803 View
focal segmental glomerulosclerosis Tg(Thy1/THY1)T6Gsv/0 involves: C57BL/10 * CBA J:294728, J:294621 View
IgA glomerulonephritis Tg(Itgam-FCAR)83Rcmo/0 involves: C57BL/6 * NOD J:120534 View
kidney disease mgb/mgb involves: C57BL/6 * FVB/N J:207566 View
kidney disease Tg(Nphs1-rtTA*3G)8Jhm/0
Tg(tetO-GFP,-APOL1*)#Susz/0		 involves: C57BL/6J * CBA/J * FVB/N J:251848 View
kidney disease Tg(Nphs1-rtTA*3G)8Jhm/0
Tg(tetO-GFP,-APOL1*S342G*I384M)#Susz/0		 involves: C57BL/6J * CBA/J * FVB/N J:251848 View
polycystic kidney disease 2 Tg(CAG-PKD2)#Hwl/? involves: FVB/NJ J:148377 View
Additional
Complex
Models		     autosomal recessive pseudohypoaldosteronism type 1 Scnn1atm1Rss/Scnn1atm1Rss
Tg(CMV-Scnn1a)1352Rss/0		 involves: 129P2/OlaHsd * NMRI J:43583 View
Dent disease Inpp5btm1Nbm/Inpp5btm1Nbm
Ocrltm1Nbm/Ocrltm1Nbm
Tg(INPP5B)CNbm/0		 involves: 129S/SvEv * 129S6/SvEvTac * FVB/N J:185879 View
Dent disease Inpp5btm1Nbm/Inpp5btm1Nbm
Ocrltm1Nbm/Y
Tg(INPP5B)CNbm/0		 involves: 129S/SvEv * 129S6/SvEvTac * FVB/N J:185879 View
focal segmental glomerulosclerosis Gt(ROSA)26Sortm1Sor/Gt(ROSA)26Sortm1Sor
Tg(NPHS2-rtTA2*M2)1Jbk/Tg(NPHS2-rtTA2*M2)1Jbk
Tg(tetO-cre)LC1Bjd/Tg(tetO-cre)LC1Bjd		 involves: 129S4/SvJaeSor * BALB/c * C57BL/6 * FVB/N J:285673 View
kidney disease Uoxin/Uoxin involves: C57BL/6J * DBA/2J J:70677 View
membranous glomerulonephritis Faslpr/Faslpr
Il27ratm1Mak/Il27ratm1Mak		 MRL.Cg-Il27ratm1Mak Faslpr J:122148 View
nephrogenic diabetes insipidus Nos1tm1Plh/Nos1tm1Plh
Nos2tm1Mrl/Nos2tm1Mrl
Nos3tm1Plh/Nos3tm1Plh		 involves: 129S4/SvJae * 129S7/SvEvBrd J:100308 View
nephrotic syndrome Hprt1tm1(Nphs1-CMIP)Dsah/Hprt1+ B6.Cg-Hprt1tm1(Nphs1-CMIP)Dsah J:185411 View
polycystic kidney disease MitfTg(Tff3-Tmem207)2Tamo/Mitf+ involves: C57BL/6 J:244533 View
polycystic kidney disease MitfTg(Tff3-Tmem207)2Tamo/MitfTg(Tff3-Tmem207)2Tamo involves: C57BL/6 J:244533 View
renal tubular transport disease Igktm1.1Cog/Igktm1.1Cog involves: 129P2/OlaHsd * C57BL/6 * FVB/N J:135758 View
renal tubular transport disease Igktm1.1Cog/Igktm1.2Cog involves: 129P2/OlaHsd * C57BL/6 * FVB/N J:135758 View

       
No similarity to the expected human disease phenotype was found.
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
NOT Models      autosomal recessive polycystic kidney disease Pkhd1tm1Rbu/Pkhd1tm1Rbu involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:112509 View
autosomal recessive polycystic kidney disease Pkhd1tm2Ggg/Pkhd1tm2Ggg involves: 129 * C57BL/6 * FVB J:348336 View
focal segmental glomerulosclerosis 1 Tg(CMV-Plaur*)19Lbh/0 FVB/N-Tg(CMV-Plaur*)19Lbh J:217443 View
nephronophthisis 1 Nphp1tm1.1Hung/Nphp1tm1.1Hung B6.Cg-Nphp1tm1.1Hung J:140205 View
pseudohypoaldosteronism Cul3tm1Suc/Cul3+ involves: C57BL/6 J:226618 View
pseudohypoaldosteronism Cul3tm2Suc/Cul3tm2Suc involves: C57BL/6 J:226618 View