Excel File Text File All mouse models of autoimmune disease of musculoskeletal system with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      systemic lupus erythematosus C4btm1Crr/C4btm1Crr involves: 129S4/SvJae * C57BL/6J J:111811 View
systemic lupus erythematosus Ccr2tm1Blck/Ccr2tm1Blck
Faslpr/Faslpr
MRL.Cg-Ccr2tm1Blck Faslpr J:113343 View
systemic lupus erythematosus Dnase1tm1Tmo/Dnase1tm1Tmo involves: 129P2/OlaHsd * C57BL/6 J:62549 View
systemic lupus erythematosus Dnase1tm2092.1Arte/Dnase1tm2092.1Arte involves: C57BL/6 J:277126 View
systemic lupus erythematosus Faslpr/Faslpr MRL/Mp-Faslpr J:27634, J:28885, J:108760, J:131138 View
systemic lupus erythematosus Faslpr/Faslpr
Igh-Jtm2(3H9-VDJ*)Mwg/Igh-J+
MRL.Cg-Faslpr Igh-Jtm2(3H9-VDJ*)Mwg J:131138 View
systemic lupus erythematosus Faslpr/Faslpr
Tlr9tm1Aki/Tlr9tm1Aki
MRL.Cg-Tlr9tm1Aki Faslpr J:113557 View
systemic lupus erythematosus Faslpr/Faslpr
Tnfrsf9tm1Byk/Tnfrsf9tm1Byk
MRL.Cg-Tnfrsf9tm1Byk Faslpr J:120559 View
systemic lupus erythematosus Fcgr2btm1Ttk/Fcgr2btm1Ttk B6.129S4-Fcgr2btm1Ttk J:64152 View
systemic lupus erythematosus Fcgr2btm1Ttk/Fcgr2btm1Ttk
Traf3ip2tm1Sbn/Traf3ip2+
involves: 129 * 129S4/SvJae * C57BL/6 J:191090 View
systemic lupus erythematosus Pdcd1tm1Hon/Pdcd1tm1Hon B6.129S2-Pdcd1tm1Hon J:78802 View
systemic lupus erythematosus Pdcd1tm1Hon/Pdcd1tm1Hon involves: 129S2/SvPas * C57BL/6 J:50688 View
      alopecia areata Cchcr1em1Aoka/Cchcr1em1Aoka C57BL/6NJcl-Cchcr1em1Aoka J:309941 View
cutaneous lupus erythematosus Trex1tm1Tld/Trex1tm1Tld involves: 129P2/OlaHsd * C57BL/6J J:243357 View
pemphigus vulgaris Dsg3bal-Pas/Dsg3bal-Pas 129S2.Cg-Dsg3bal-Pas J:46865 View
pemphigus vulgaris Dsg3bal/Dsg3bal C57BL/6J-Dsg3bal/J J:42792 View
pemphigus vulgaris Dsg3tm1Stan/Dsg3tm1Stan involves: 129X1/SvJ * C57BL/6J J:40804 View
systemic lupus erythematosus Atg5tm1Myok/Atg5tm1Myok
Lyz2tm1(cre)Ifo/Lyz2+
involves: 129P2/OlaHsd * 129S/SvEv J:235399 View
systemic lupus erythematosus Atg7tm1Tchi/Atg7tm1Tchi
Lyz2tm1(cre)Ifo/Lyz2+
involves: 129P2/OlaHsd * C57BL/6NCrlj * CBA/JNCrlj J:235399 View
systemic lupus erythematosus Becn1tm1Ebr/Becn1tm1Ebr
Lyz2tm1(cre)Ifo/Lyz2+
involves: 129P2/OlaHsd J:235399 View
systemic lupus erythematosus C1qatm1Mjw/C1qatm1Mjw involves: 129P2/Ola * 129S/SvEv * C57BL/6 J:47315 View
systemic lupus erythematosus Cd19tm1(cre)Cgn/Cd19+
Ep300tm2Reck/Ep300+
involves: 129/Sv * 129P2/OlaHsd * C57BL/6 J:147840 View
systemic lupus erythematosus Cd79atm1(cre)Reth/Cd79a+
Inpp5dtm1Rav/Inpp5dtm1Rav
involves: 129 * BALB/c * C57BL/6 J:178833 View
systemic lupus erythematosus Cdkn1atm1Led/Cdkn1atm1Led involves: 129S6/SvEvTac J:76041 View
systemic lupus erythematosus Cdkn1atm1Led/Cdkn1atm1Led
Gadd45atm1Ajf/Gadd45atm1Ajf
either: (involves: 129P2/OlaHsd * 129S6/SvEvTac * C57BL/6) or (involves: 129S6/SvEvTac * 129X1/SvJ * C57BL/6) J:76041 View
systemic lupus erythematosus Cybbtm1Din/Cybbtm1Din B6.129S-Cybbtm1Din/J J:235399 View
systemic lupus erythematosus Def6Gt(OST307148)Lex/Def6Gt(OST307148)Lex involves: 129S5/SvEvBrd * C57BL/6 J:106469 View
systemic lupus erythematosus Fam210bem1Cya/Fam210bem1Cya involves: C57BL/6N J:351618 View
systemic lupus erythematosus Gadd45atm1Ajf/Gadd45atm1Ajf either: (involves: 129P2/OlaHsd * C57BL/6) or (involves: 129X1/SvJ * C57BL/6) J:76041 View
systemic lupus erythematosus Ifih1Rgsc422/Ifih1+ D2JJcl.B6JJcl-Ifih1Rgsc422 J:209917 View
systemic lupus erythematosus Ifih1Rgsc422/Ifih1Rgsc422 D2JJcl.B6JJcl-Ifih1Rgsc422 J:209917 View
systemic lupus erythematosus Ikzf3tm1Kge/Ikzf3tm1Kge involves: 129S4/SvJae * C57BL/6 J:50626, J:81805 View
systemic lupus erythematosus Jak1M1Mhda/Jak1+ C3HeB/FeJ-Jak1M1Mhda J:199153 View
systemic lupus erythematosus Junbtm3Wag/Junbtm3Wag
Tg(KRT5-cre)1Tak/0
involves: 129/Sv * 129P2/OlaHsd * C3H * C57BL/6 J:155575 View
systemic lupus erythematosus KitW-sh/KitW-sh
Lyntm1Ard/Lyntm1Ard
involves: 101 * 129P2/OlaHsd * C3H/HeH J:161523 View
systemic lupus erythematosus Lbric-J/Lbr+ (NZW/LacJ x C57BL/6J-Lbric-J/J)F1 J:234168 View
systemic lupus erythematosus Lyntm1Ard/Lyntm1Ard involves: 129P2/OlaHsd J:161523 View
systemic lupus erythematosus Man2a1tm1Jxm/Man2a1tm1Jxm involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:74579 View
systemic lupus erythematosus Mta2tm1.1Yzha/Mta2tm1.1Yzha involves: 129S4/SvJae * C57BL/6 * FVB/N J:137101 View
systemic lupus erythematosus Pld4thss/Pld4thss BALB/cJ-Pld4thss/GrsrJ J:278304 View
systemic lupus erythematosus Polbtm1.1Jbsw/Polbtm1.1Jbsw involves: 129/Sv * C57BL/6 J:206872 View
systemic lupus erythematosus Ppargtm1.1Gonz/Ppargtm1.1Gonz
Lyz2tm1(cre)Ifo/Lyz2+
involves: 129P2/OlaHsd * 129X1/SvJ * C57BL/6 J:168799 View
systemic lupus erythematosus Prdm1tm1Clme/Prdm1tm1Clme
Tg(Itgax-cre)1-1Reiz/0
involves: 129S1/Sv * 129X1/SvJ * C57BL/6 * CBA J:178876 View
systemic lupus erythematosus Ptpn22tm2Achn/Ptpn22tm2Achn
Ptprctm1Weis/Ptprctm1Weis
B6.Cg-Ptprctm1Weis Ptpn22tm2Achn J:147129 View
systemic lupus erythematosus Ptprctm1Weis/Ptprc+ involves: 129X1/SvJ * C57BL/6 J:66501 View
systemic lupus erythematosus Ptprctm1Weis/Ptprctm1Weis involves: 129X1/SvJ * C57BL/6 J:66501 View
systemic lupus erythematosus Rasgrp1lag/Rasgrp1lag involves: 129 * C57BL/6 J:85189 View
systemic lupus erythematosus Rassf5tm1Kina/Rassf5tm1Kina B6.Cg-Rassf5tm1Kina J:168749 View
systemic lupus erythematosus Rc3h1san/Rc3h1san either: C57BL/6JSfdAnu-Rc3h1san/Anu or (involves: C57BL/6JSfdAnu * CBA/Ca) J:98938 View
systemic lupus erythematosus Ro60tm1Woln/Ro60+ involves: 129S1/Sv * C57BL/6 J:84627 View
systemic lupus erythematosus Ro60tm1Woln/Ro60tm1Woln B6.129S1-Ro60tm1Woln J:84627 View
systemic lupus erythematosus Ro60tm1Woln/Ro60tm1Woln involves: 129S1/Sv * C57BL/6 J:84627 View
systemic lupus erythematosus Rubcnem1Dgre/Rubcnem1Dgre involves: C57BL/6 * C57BL/6N J:235399 View
systemic lupus erythematosus Rxratm1Krc/Rxratm1Krc
Lyz2tm1(cre)Ifo/Lyz2+
involves: 129P2/OlaHsd * 129S4/SvJae * C57BL/6 J:168799 View
systemic lupus erythematosus Tg(Igh-V-CD40lg)#Tsub/0 C57BL/6-Tg(Igh-V-CD40lg)#Tsub J:128824 View
systemic lupus erythematosus Tg(Tlr7)1Boll/0 involves: C57BL/6 J:193610 View
systemic lupus erythematosus Timd4tm1Kuch/Timd4tm1Kuch involves: C57BL/6 J:235399 View
systemic lupus erythematosus Tlr7em2Anu/Tlr7+ C57BL/6NCrl-Tlr7em2Anu J:324448 View
systemic lupus erythematosus Tlr7em2Anu/Tlr7em2Anu C57BL/6NCrl-Tlr7em2Anu J:324448 View
systemic lupus erythematosus Tlr7em2Anu/Y C57BL/6NCrl-Tlr7em2Anu J:324448 View
systemic lupus erythematosus Tnfrsf13btm1Vmd/Tnfrsf13btm1Vmd involves: C57BL/6 J:82331 View
systemic lupus erythematosus Traf3ip2tm1.1Lix/Traf3ip2tm1.1Lix B6.129-Traf3ip2tm1.1Lix J:187766 View
Transgenes and
Other Mutations
     systemic lupus erythematosus Cd4tm1Mak/Cd4tm1Mak
Igh-Jtm2(3H9-VDJ*)Mwg/Igh-J+
B6.Cg-Cd4tm1Mak Igh-Jtm2(3H9-VDJ*)Mwg J:142389 View
systemic lupus erythematosus Igh-Jtm2(3H9-VDJ*)Mwg/Igh-J+ B6.129P2-Igh-Jtm2(3H9-VDJ*)Mwg J:142389 View
systemic lupus erythematosus Tcrbtm1Mom/Tcrbtm1Mom
Tcrdtm1Mom/Tcrdtm1Mom
Igh-Jtm2(3H9-VDJ*)Mwg/Igh-J+
B6.129P2-Tcrbtm1Mom Igh-Jtm2(3H9-VDJ*)Mwg Tcrdtm1Mom J:142389 View
systemic lupus erythematosus Tg(ACTB-TNFRSF6B)754Jwu/? B6.Cg-Tg(Actb-TNFRSF6B)754Jwu J:148162 View
systemic lupus erythematosus X/Yaa (NZB x BXSB)F1 J:6235 View
systemic lupus erythematosus X/Yaa (NZW x BXSB)F1 J:7276 View
systemic lupus erythematosus X/Yaa (NZW x SB)F1 J:7276 View
systemic lupus erythematosus X/Yaa BXSB/MpJ J:6235, J:108760, J:7308 View
systemic lupus erythematosus X/Yaa BXSB/MpJScr J:10973 View
Additional
Complex
Models
     bullous pemphigoid Col17a1tm1.1(COL17A1)Zliu/Col17a1tm1.1(COL17A1)Zliu involves: 129P2/OlaHsd * C57BL/6J J:261781 View
systemic lupus erythematosus Apoetm1Unc/Apoetm1Unc
Faslgld/Faslgld
B6.Cg-Faslgld Apoetm1Unc J:91058, J:200141 View
systemic lupus erythematosus Csf2tm1Dran/Csf2tm1Dran
Il3tm1Glli/Il3tm1Glli
B6.129S2-Csf2tm1Dran Il3tm1Glli J:83086 View
systemic lupus erythematosus Ightm1.1(Igh564)Tik/Ightm1.1(Igh564)Tik
Igktm1(Igk564)Tik/Igktm1(Igk564)Tik
B6.129S4-Igktm1(Igk564)Tik Ightm1(Igh564)Tik J:113555 View
systemic lupus erythematosus Psen1tm1Bdes/Psen1+
Psen2tm1Bdes/Psen2tm1Bdes
involves: 129P2/OlaHsd J:91235 View


       
No similarity to the expected human disease phenotype was found.
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
NOT Models      Hailey-Hailey disease Atp2c1tm1Ges/Atp2c1+ involves: 129X1/SvJ * Black Swiss J:124662 View
systemic lupus erythematosus Csf2tm1Dran/Csf2tm1Dran
Ifngtm1Ts/Ifngtm1Ts
Il3tm1Glli/Il3tm1Glli
involves: 129S2/SvPas * 129S7/SvEvBrd * C57BL/6 J:83086 View
systemic lupus erythematosus Tlr7tm1Flv/Y
X/Yaa
B6.Cg-Tlr7tm1Flv Yaa J:127600 View