Excel File Text File *Disease is associated/modeled with this Gene or a homolog. More...
      Disease Term Human Homologs Mouse Homologs Mouse Models Homology Source
     autosomal dominant auditory neuropathy 1 DIAPH3* Diaph3* 2 models Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 12 TECTA* Tecta* 4 models Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 13 COL11A2* Col11a2* 1 model Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 22 MYO6* Myo6* 2 models Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 25 SLC17A8* Slc17a8* 1 model Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 36 TMC1* Tmc1* 3 models Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 41 P2RX2* P2rx2* 1 model Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 67 OSBPL2* Osbpl2* 1 model Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 9 COCH* Coch* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 12 CDH23* Cdh23* 3 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 16 STRC*, STRCP1 Strc* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 18A USH1C* Ush1c* 3 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 18B OTOG* Otog* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 1A GJB6* Gjb6* 3 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 1A GJB2* Gjb2* 2 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 2 MYO7A* Myo7a* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 22 OTOA* Otoa* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 23 PCDH15* Pcdh15* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 28 TRIOBP* Triobp* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 29 CLDN14* Cldn14* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 3 MYO15A* Myo15a* 2 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 30 MYO3A* Myo3a* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 31 WHRN* Whrn* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 32 CDC14A* Cdc14a* 4 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 37 MYO6* Myo6* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 39 HGF* Hgf* 2 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 42 ILDR1* Ildr1* 3 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 48 CIB2* Cib2* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 49 MARVELD2* Marveld2* 2 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 59 PJVK* Pjvk* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 63 LRTOMT*, LRRC51, TOMT Tomt*, Lrrc51 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 68 S1PR2* S1pr2* 2 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 7 TMC1* Tmc1* 6 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 74 MSRB3* Msrb3* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 79 TPRN* Tprn* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 88 ELMOD3* Elmod3* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 9 OTOF* Otof* 2 models Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 93 CABP2* Cabp2* 1 model Alliance of Genome Resources
X-linked deafness 4 SMPX* Smpx* 6 models Alliance of Genome Resources
     auditory system disease FSCN2 Fscn2* 1 model Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 25 TRPV4 Trpv4* 1 model Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 4A CEACAM16 Ceacam16* 1 model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness ATP6V1B1 Atp6v1b1* 1 model Alliance of Genome Resources
enlarged vestibular aqueduct ATP6V1B1 Atp6v1b1* 1 model Alliance of Genome Resources
nonsyndromic deafness ALG10, ALG10B Alg10b* 1 model Alliance of Genome Resources
nonsyndromic deafness KLC2 Klc2* 1 model Alliance of Genome Resources
nonsyndromic deafness m12Anu* 1 model
nonsyndromic deafness PPIP5K2 Ppip5k2* 1 model Alliance of Genome Resources
nonsyndromic deafness WFS1 Wfs1* 1 model Alliance of Genome Resources
otitis media TP73 Trp73* 1 model Alliance of Genome Resources
otitis media TGIF1 Tgif1* 1 model Alliance of Genome Resources
otitis media TBX1 Tbx1* 1 model Alliance of Genome Resources
otitis media SH3PXD2B Sh3pxd2b* 1 model Alliance of Genome Resources
otitis media SALL4 Sall4* 1 model Alliance of Genome Resources
otitis media RPL38 Rpl38* 1 model Alliance of Genome Resources
otitis media PHEX Phex* 1 model Alliance of Genome Resources
otitis media NISCH Nisch* 1 model Alliance of Genome Resources
otitis media NF2 Nf2* 3 models Alliance of Genome Resources
otitis media NAGLU Naglu* 1 model Alliance of Genome Resources
otitis media MECOM Mecom* 2 models Alliance of Genome Resources
otitis media LMNA Lmna* 1 model Alliance of Genome Resources
otitis media IDUA Idua* 1 model Alliance of Genome Resources
otitis media FGFR1 Fgfr1* 2 models Alliance of Genome Resources
otitis media FBXO11 Fbxo11* 3 models Alliance of Genome Resources
otitis media EYA4 Eya4* 1 model Alliance of Genome Resources
otitis media ENPP1 Enpp1* 1 model Alliance of Genome Resources
otitis media E2F4 E2f4* 1 model Alliance of Genome Resources
otitis media DNAH5 Dnah5* 1 model Alliance of Genome Resources
otitis media CBY1 Cby1* 1 model Alliance of Genome Resources
otitis media BPIFA1 Bpifa1*, Bpifa5 1 model Alliance of Genome Resources
sensorineural hearing loss SLITRK6 Slitrk6* 1 model Alliance of Genome Resources
sensorineural hearing loss SLC7A14 Slc7a14* 2 models Alliance of Genome Resources
sensorineural hearing loss SLC7A8 Slc7a8* 1 model Alliance of Genome Resources
sensorineural hearing loss GAS2 Gas2* 1 model Alliance of Genome Resources
tympanosclerosis ENPP1 Enpp1* 1 model Alliance of Genome Resources
vestibular disease KCNA10 Kcna10* 1 model Alliance of Genome Resources
     aminoglycoside-induced deafness TRMU* Trmu   Alliance of Genome Resources
autosomal dominant auditory neuropathy 3 TMEM43* Tmem43   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness ATOH1* Atoh1   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness USP48* Usp48   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness THOC1* Thoc1   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness PI4KB* Pi4kb   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness MYO3A* Myo3a   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness MAP1B* Map1b   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness GREB1L* Greb1l   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness EPHA10* Epha10   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness ELMOD3* Elmod3   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness COL11A1* Col11a1   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness ATP11A* Atp11a   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness ATP2B2* Atp2b2   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 1 DIAPH1* Diaph1   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 10 EYA4* Eya4   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 11 MYO7A* Myo7a   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 15 POU4F3* Pou4f3 1 "NOT" model Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 17 MYH9* Myh9   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 20 ACTG1* Actg1   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 21 RIPOR2* Ripor2   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 23 SIX1* Six1   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 27 REST* Rest   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 28 GRHL2* Grhl2   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 2A KCNQ4* Kcnq4   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 34 NLRP3* Nlrp3   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 3A GJB2* Gjb2   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 3B GJB6* Gjb6   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 40 CRYM* Crym   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 44 CCDC50* Ccdc50   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 4A MYH14* Myh14   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 4B CEACAM16* Ceacam16   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 5 GSDME* Gsdme   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 50 MIR96* Mir96   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 56 TNC* Tnc   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 6 WFS1* Wfs1   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 64 DIABLO* Diablo   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 65 TBC1D24* Tbc1d24 2 "NOT" models Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 66 CD164* Cd164   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 68 HOMER2* Homer2   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 69 KITLG* Kitl   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 7 LMX1A* Lmx1a   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 70 MCM2* Mcm2   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 71 DMXL2* Dmxl2   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 72 SLC44A4* Slc44a4   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 73 PTPRQ* Ptprq   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 74 PDE1C* Pde1c   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 75 TRRAP* Trrap   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 76 PLS1* Pls1   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 77 ABCC1* Abcc1   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 78 SLC12A2* Slc12a2   Alliance of Genome Resources
autosomal dominant nonsyndromic deafness 79 SCD5*  
autosomal recessive nonsyndromic deafness GPR156* Gpr156   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness AFG2B* Afg2b   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness CDH23* Cdh23   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness CLRN2* Clrn2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness TMTC4* Tmtc4   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness MINAR2* Minar2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 100 PPIP5K2* Ppip5k2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 101 GRXCR2* Grxcr2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 102 EPS8* Eps8   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 103 CLIC5* Clic5   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 104 RIPOR2* Ripor2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 106 EPS8L2* Eps8l2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 107 WBP2* Wbp2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 108 ROR1* Ror1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 109 ESRP1* Esrp1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 110 COCH* Coch   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 111 MPZL2* Mpzl2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 112 BDP1* Bdp1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 113 CEACAM16* Ceacam16   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 114 GRAP*, GRAPL Grap   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 115 SPNS2* Spns2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 116 CLDN9* Cldn9   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 12 ATP2B2* Atp2b2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 15 GIPC3* Gipc3   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 1B GJB6* Gjb6   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 21 TECTA* Tecta   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 24 RDX* Rdx   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 25 GRXCR1* Grxcr1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 26 GAB1* Gab1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 35 ESRRB* Esrrb   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 36 ESPN* Espn   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 4 FOXI1* Foxi1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 4 KCNJ10* Kcnj10   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 4 SLC26A4* Slc26a4   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 44 ADCY1* Adcy1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 53 COL11A2* Col11a2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 57 PDZD7* Pdzd7   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 6 TMIE* Tmie   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 61 SLC26A5* Slc26a5   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 66 DCDC2* Dcdc2a   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 67 LHFPL5* Lhfpl5   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 70 PNPT1* Pnpt1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 76 SYNE4* Syne4   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 77 LOXHD1* Loxhd1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 8 TMPRSS3* Tmprss3   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 84A PTPRQ* Ptprq   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 84B OTOGL* Otogl   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 86 TBC1D24* Tbc1d24 1 "NOT" model Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 89 KARS1* Kars1   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 91 SERPINB6* Serpinb6a, Serpinb6b, Serpinb6c, Serpinb6d, Serpinb6e   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 94 NARS2* Nars2   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 97 MET* Met   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 98 TSPEAR* Tspear   Alliance of Genome Resources
autosomal recessive nonsyndromic deafness 99 TMEM132E* Tmem132e   Alliance of Genome Resources
cholesteatoma of middle ear IL2* Il2   Alliance of Genome Resources
inner ear disease CENPB* Cenpb   Alliance of Genome Resources
Meniere's disease PTPN22* Ptpn22   Alliance of Genome Resources
Meniere's disease MTHFR* Mthfr   Alliance of Genome Resources
Meniere's disease AQP4* Aqp4   Alliance of Genome Resources
Meniere's disease HLA-B*, HLA-A, HLA-C, HLA-E, HLA-F, HLA-G, HLA-H H2-D1, H2-K1, H2-L, H2-M1, H2-M2, H2-M3, H2-M5, H2-M9, H2-M10.1, H2-M10.2, H2-M10.3, H2-M10.4, H2-M10.5, H2-M10.6, H2-M11, H2-Q1, H2-Q2, H2-Q4, H2-Q6, H2-Q7, H2-Q8, H2-Q10, H2-T3, H2-T10, H2-T22, H2-T23   Alliance of Genome Resources
Meniere's disease HLA-DRB1*, HLA-DRB3, HLA-DRB4, HLA-DRB5 H2-Eb1, H2-Eb2   Alliance of Genome Resources
Meniere's disease HSPA1A*, HSPA1B Hspa1a, Hspa1b   Alliance of Genome Resources
nonsyndromic deafness TBC1D24* Tbc1d24   Alliance of Genome Resources
nonsyndromic deafness USH2A* Ush2a   Alliance of Genome Resources
otitis media MBL2* Mbl2   Alliance of Genome Resources
otitis media IL10* Il10   Alliance of Genome Resources
otitis media IL6* Il6   Alliance of Genome Resources
otitis media CX3CR1* Cx3cr1   Alliance of Genome Resources
otitis media A2ML1*  
otosclerosis VDR* Vdr   Alliance of Genome Resources
otosclerosis BMP4* Bmp4   Alliance of Genome Resources
otosclerosis COL1A1* Col1a1   Alliance of Genome Resources
otosclerosis BMP2* Bmp2   Alliance of Genome Resources
otosclerosis HLA-B*, HLA-A, HLA-C, HLA-E, HLA-F, HLA-G, HLA-H H2-D1, H2-K1, H2-L, H2-M1, H2-M2, H2-M3, H2-M5, H2-M9, H2-M10.1, H2-M10.2, H2-M10.3, H2-M10.4, H2-M10.5, H2-M10.6, H2-M11, H2-Q1, H2-Q2, H2-Q4, H2-Q6, H2-Q7, H2-Q8, H2-Q10, H2-T3, H2-T10, H2-T22, H2-T23   Alliance of Genome Resources
otosclerosis AGT* Agt   Alliance of Genome Resources
otosclerosis 11 FOXL1* Foxl1   Alliance of Genome Resources
sensorineural hearing loss EYA4* Eya4   Alliance of Genome Resources
sensorineural hearing loss DIAPH1* Diaph1   Alliance of Genome Resources
sensorineural hearing loss CLCNKA*, CLCNKB Clcnka, Clcnkb   Alliance of Genome Resources
sensorineural hearing loss BSND* Bsnd   Alliance of Genome Resources
sensorineural hearing loss BCAP31* Bcap31   Alliance of Genome Resources
sensorineural hearing loss APOE* Apoe   Alliance of Genome Resources
sensorineural hearing loss MYO1A* Myo1a   Alliance of Genome Resources
sensorineural hearing loss HLA-B*, HLA-A, HLA-C, HLA-E, HLA-F, HLA-G, HLA-H H2-D1, H2-K1, H2-L, H2-M1, H2-M2, H2-M3, H2-M5, H2-M9, H2-M10.1, H2-M10.2, H2-M10.3, H2-M10.4, H2-M10.5, H2-M10.6, H2-M11, H2-Q1, H2-Q2, H2-Q4, H2-Q6, H2-Q7, H2-Q8, H2-Q10, H2-T3, H2-T10, H2-T22, H2-T23   Alliance of Genome Resources
sensorineural hearing loss GSDME* Gsdme   Alliance of Genome Resources
sensorineural hearing loss GPSM2* Gpsm2   Alliance of Genome Resources
sensorineural hearing loss GATA3* Gata3   Alliance of Genome Resources
sensorineural hearing loss F5* F5   Alliance of Genome Resources
sensorineural hearing loss F2* F2   Alliance of Genome Resources
sensorineural hearing loss MYO6* Myo6   Alliance of Genome Resources
sensorineural hearing loss HLA-DRB1*, HLA-DRB3, HLA-DRB4, HLA-DRB5 H2-Eb1, H2-Eb2   Alliance of Genome Resources
sensorineural hearing loss MYH14* Myh14   Alliance of Genome Resources
sensorineural hearing loss MYH9* Myh9   Alliance of Genome Resources
sensorineural hearing loss MBL2* Mbl2   Alliance of Genome Resources
sensorineural hearing loss KCNQ4* Kcnq4   Alliance of Genome Resources
sensorineural hearing loss ITGA2* Itga2   Alliance of Genome Resources
sensorineural hearing loss IL2* Il2   Alliance of Genome Resources
sensorineural hearing loss IFNG* Ifng   Alliance of Genome Resources
sensorineural hearing loss WHRN* Whrn   Alliance of Genome Resources
sensorineural hearing loss WFS1* Wfs1   Alliance of Genome Resources
sensorineural hearing loss TNF* Tnf   Alliance of Genome Resources
sensorineural hearing loss TMPRSS3* Tmprss3   Alliance of Genome Resources
sensorineural hearing loss TMIE* Tmie   Alliance of Genome Resources
sensorineural hearing loss TMC1* Tmc1   Alliance of Genome Resources
sensorineural hearing loss TECTA* Tecta   Alliance of Genome Resources
sensorineural hearing loss TBX1* Tbx1   Alliance of Genome Resources
sensorineural hearing loss STRC*, STRCP1 Strc   Alliance of Genome Resources
sensorineural hearing loss MYO15A* Myo15a   Alliance of Genome Resources
sensorineural hearing loss MYO7A* Myo7a   Alliance of Genome Resources
tympanosclerosis TLR4* Tlr4   Alliance of Genome Resources
X-linked deafness 1 PRPS1* Prps1   Alliance of Genome Resources
X-linked deafness 2 POU3F4* Pou3f4   Alliance of Genome Resources
X-linked deafness 6 COL4A6* Col4a6   Alliance of Genome Resources
X-linked deafness 7 GPRASP2*, ARMCX5-GPRASP2, GPRASP3 Bhlhb9, Gprasp2   Alliance of Genome Resources
Y-linked deafness 2 TBL1Y*, TBL1X Tbl1x   Alliance of Genome Resources

 
Transgenes and other genome features developed in mice to model this disease.
     Disease Term Transgenes and Other Genome Features Mouse Models
  autosomal dominant auditory neuropathy 1 Tg(CAG-Diaph3)771Lesp 1 model
  autosomal dominant auditory neuropathy 1 Tg(CAG-Diap3)924Lesp 1 model
  autosomal recessive nonsyndromic deafness 1A Del(14Gjb6-Cryl1)1Lmon 1 model
  autosomal recessive nonsyndromic deafness 38 Phl1 2 models