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Disease Ontology Browser
Gerstmann-Straussler-Scheinker syndrome (DOID:4249)
Alliance: disease page
Synonyms: Gerstmann-Straussler-Scheinker disease; PRION DEMENTIA
Alt IDs: OMIM:137440, ICD10CM:A81.82, ICD9CM:046.71, MESH:D016098, NCI:C84727, UMLS_CUI:C0017495
Definition: A prion disease characterized by adult onset of memory loss, dementia, ataxia, and pathologic deposition of amyloid-like plaques in the brain.

Disease References using Mouse Models (4)

Contributing Projects:
Mouse Genome Database (MGD), Gene Expression Database (GXD), Mouse Models of Human Cancer database (MMHCdb) (formerly Mouse Tumor Biology (MTB)), Gene Ontology (GO)
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last database update
04/09/2024
MGI 6.23
The Jackson Laboratory