prion disease (DOID:649)
Alliance: disease page
Synonyms: Prion disease pathway; prion induced disorder; Prion protein disease; Spongiform Encephalopathy; transmissible spongiform encephalopathy
Alt IDs: ICD10CM:A81.9, KEGG:05020, MESH:D017096, NCI:C128346, UMLS_CUI:C0162534
Definition: A brain disease that is characterized by brain damage resulting from the abnormal folding, clumping and accumulation of cellular proteins in the brain induced by prion proteins.