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desquamative interstitial pneumonia (DOID:0050158)
Alliance: disease page
Synonyms: familial desquamative interstitial pneumonitis; RBILD; respiratory bronchiolitis-associated interstitial lung disease
Alt IDs: OMIM:263000, DOID:2796, ICD10CM:J84.117, ICD9CM:516.34, ICD9CM:516.37, MESH:C562470, NCI:C35288, UMLS_CUI:C0238378
Definition: An idiopathic interstitial pneumonia that is characterized by the accumulation of bronchiolocentric alveolar macrophages in alveolar spaces and interstitial inflammation and involves mild bronchiolar fibrosis and chronic inflammation.

Disease References using Mouse Models (1)

Contributing Projects:
Mouse Genome Database (MGD), Gene Expression Database (GXD), Mouse Models of Human Cancer database (MMHCdb) (formerly Mouse Tumor Biology (MTB)), Gene Ontology (GO)
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last database update
04/16/2024
MGI 6.23
The Jackson Laboratory