Automated description from the Alliance of Genome Resources (Release 7.0.0)
Enables pyruvate carboxylase activity. Involved in gluconeogenesis. Located in mitochondrion. Is active in mitochondrial matrix. Is expressed in several structures, including alimentary system; genitourinary system; integumental system; nervous system; and sensory organ. Human ortholog(s) of this gene implicated in pyruvate carboxylase deficiency disease. Orthologous to human PC (pyruvate carboxylase).