Automated description from the Alliance of Genome Resources (Release 7.0.0)
Predicted to enable several functions, including anion binding activity; identical protein binding activity; and ornithine carbamoyltransferase activity. Predicted to be involved in several processes, including ammonium homeostasis; non-proteinogenic amino acid metabolic process; and urea cycle. Predicted to act upstream of or within arginine biosynthetic process. Located in mitochondrial inner membrane. Is expressed in alimentary system; intestine; liver; and small intestine. Used to study ornithine carbamoyltransferase deficiency. Human ortholog(s) of this gene implicated in ornithine carbamoyltransferase deficiency. Orthologous to human OTC (ornithine transcarbamylase).