About   Help   FAQ
Symbol
Name
ID
Mto1
mitochondrial tRNA translation optimization 1
MGI:1915541
Phenotype annotations related to homeostasis/metabolism
Darker colors indicate more annotations
Human Phenotypes
Decreased activity of mitochondrial complex III
Hyperalaninemia
Hyperammonemia
Hypoglycemia
Increased circulating lactate concentration
Lactic acidosis
Metabolic acidosis
Pleural effusion
Ascites
Disease(s) Associated with MTO1
combined oxidative phosphorylation deficiency 10

Mouse Phenotypes
increased susceptibility to xenobiotic induced morbidity/mortality
increased physiological sensitivity to xenobiotic
Availability Mouse Genotype
Mto1Gt(G019A03)Wrst/Mto1Gt(G019A03)Wrst

Contributing Projects:
Mouse Genome Database (MGD), Gene Expression Database (GXD), Mouse Models of Human Cancer database (MMHCdb) (formerly Mouse Tumor Biology (MTB)), Gene Ontology (GO)
Citing These Resources
Funding Information
Warranty Disclaimer, Privacy Notice, Licensing, & Copyright
Send questions and comments to User Support.
last database update
04/30/2024
MGI 6.23
The Jackson Laboratory