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Symbol
Name
ID

Lonp1
lon peptidase 1, mitochondrial
MGI:1921392

Phenotype annotations related to homeostasis/metabolism

Darker colors indicate more annotations

Human Phenotypes	Abnormal circulating amino acid concentration	Increased circulating pyruvate concentration
Disease(s) Associated with LONP1	Abnormal circulating amino acid concentration	Increased circulating pyruvate concentration
CODAS syndrome

Mouse Phenotypes		increased circulating HDL cholesterol level	decreased circulating iron level	decreased incidence of tumors by chemical induction
Availability	Mouse Genotype	increased circulating HDL cholesterol level	decreased circulating iron level	decreased incidence of tumors by chemical induction
	Lonp1^{tm1b(EUCOMM)Hmgu}/Lonp1⁺
	Lonp1^tm1Otin/Lonp1⁺

Contributing Projects: Mouse Genome Database (MGD), Gene Expression Database (GXD), Mouse Models of Human Cancer database (MMHCdb) (formerly Mouse Tumor Biology (MTB)), Gene Ontology (GO)
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