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Symbol
Name
ID
Lonp1
lon peptidase 1, mitochondrial
MGI:1921392
Phenotype annotations related to growth/size/body
Darker colors indicate more annotations
Human Phenotypes
Omphalocele
Umbilical hernia
Short stature
Disease(s) Associated with LONP1
CODAS syndrome

Mouse Phenotypes
embryonic growth retardation
decreased embryo size
increased lean body mass
Availability Mouse Genotype
Lonp1tm1Otin/Lonp1tm1Otin
Lonp1tm1b(EUCOMM)Hmgu/Lonp1+

Contributing Projects:
Mouse Genome Database (MGD), Gene Expression Database (GXD), Mouse Models of Human Cancer database (MMHCdb) (formerly Mouse Tumor Biology (MTB)), Gene Ontology (GO)
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last database update
03/31/2026
MGI 6.24
The Jackson Laboratory