Automated description from the Alliance of Genome Resources (Release 3.1.1)
Predicted to have microfibril binding activity. Involved in supramolecular fiber organization. Localizes to collagen-containing extracellular matrix. Is expressed in several structures, including cardiovascular system; connective tissue; limb segment; sensory organ; and skeleton. Human ortholog(s) of this gene implicated in Weill-Marchesani syndrome. Orthologous to human LTBP2 (latent transforming growth factor beta binding protein 2).