Automated description from the Alliance of Genome Resources (Release 3.2)
Exhibits cytochrome-c oxidase activity. Predicted to be involved in mitochondrial cytochrome c oxidase assembly and oxidative phosphorylation. Localizes to mitochondrion. Is expressed in brain; embryo; and skeletal muscle. Used to study Leigh disease. Human ortholog(s) of this gene implicated in Charcot-Marie-Tooth disease type 4K and Leigh disease. Orthologous to human SURF1 (SURF1 cytochrome c oxidase assembly factor).