Automated description from the Alliance of Genome Resources
Exhibits cytochrome-c oxidase activity. Predicted to be involved in mitochondrial respiratory chain complex IV assembly and oxidative phosphorylation. Localizes to the mitochondrion. Used to study Leigh disease. Human ortholog(s) of this gene implicated in Charcot-Marie-Tooth disease type 4K and Leigh disease. Orthologous to human SURF1 (SURF1 cytochrome c oxidase assembly factor).