Automated description from the Alliance of Genome Resources
Exhibits aconitate hydratase activity. Predicted to be involved in citrate metabolic process; isocitrate metabolic process; and tricarboxylic acid cycle. Localizes to the mitochondrion. Human ortholog(s) of this gene implicated in infantile cerebellar-retinal degeneration and optic atrophy. Is expressed in several structures, including alimentary system; central nervous system; genitourinary system; integumental system; and sensory organ. Orthologous to human ACO2 (aconitase 2).