Automated description from the Alliance of Genome Resources (Release 3.2)
Involved in several processes, including fat cell differentiation; mitochondrion morphogenesis; and neuromuscular process. Localizes to mitochondrion. Is expressed in several structures, including eye; hair follicle; jaw; musculoskeletal system; and optic nerve. Used to study 3-methylglutaconic aciduria type 3. Human ortholog(s) of this gene implicated in 3-methylglutaconic aciduria type 3 and optic atrophy 3. Orthologous to human OPA3 (outer mitochondrial membrane lipid metabolism regulator OPA3).