Automated description from the Alliance of Genome Resources
Exhibits protein xylosyltransferase activity. Involved in cellular response to heat; chondroitin sulfate biosynthetic process; and skeletal system development. Localizes to the Golgi cis cisterna. Human ortholog(s) of this gene implicated in Desbuquois dysplasia; pseudoxanthoma elasticum; and type 1 diabetes mellitus. Is expressed in lens. Orthologous to human XYLT1 (xylosyltransferase 1).