Automated description from the Alliance of Genome Resources (Release 7.0.0)
Enables protein xylosyltransferase activity. Involved in chondroitin sulfate biosynthetic process; embryonic skeletal system development; and ossification involved in bone maturation. Acts upstream of or within cellular response to heat. Located in Golgi cis cisterna. Is active in Golgi apparatus. Is expressed in lens. Human ortholog(s) of this gene implicated in Desbuquois dysplasia; pseudoxanthoma elasticum; and type 1 diabetes mellitus. Orthologous to human XYLT1 (xylosyltransferase 1).