Automated description from the Alliance of Genome Resources
Exhibits RNA binding activity and single-stranded DNA binding activity. Involved in negative regulation of mitochondrial RNA catabolic process and regulation of mitochondrial translation. Localizes to the mitochondrion; nucleus; and ribonucleoprotein complex. Human ortholog(s) of this gene implicated in Leigh disease. Orthologous to human LRPPRC (leucine rich pentatricopeptide repeat containing).