Automated description from the Alliance of Genome Resources
Predicted to have GTP binding activity and GTPase activity. Predicted to be involved in embryonic organ development; tRNA methylation; and tRNA wobble uridine modification. Localizes to the mitochondrion. Human ortholog(s) of this gene implicated in combined oxidative phosphorylation deficiency. Orthologous to human GTPBP3 (GTP binding protein 3, mitochondrial).