Automated description from the Alliance of Genome Resources (Release 7.0.0)
Predicted to enable ATPase activator activity. Involved in regulation of cardiolipin metabolic process. Located in matrix side of mitochondrial inner membrane. Part of inner mitochondrial membrane protein complex. Human ortholog(s) of this gene implicated in 3-methylglutaconic aciduria type 5. Orthologous to human DNAJC19 (DnaJ heat shock protein family (Hsp40) member C19).