Automated description from the Alliance of Genome Resources (Release 3.2)
Predicted to have 3'-tRNA processing endoribonuclease activity and tRNA-specific ribonuclease activity. Predicted to be involved in mitochondrial tRNA 3'-trailer cleavage, endonucleolytic. Localizes to mitochondrial nucleoid. Is expressed in extraembryonic component. Human ortholog(s) of this gene implicated in combined oxidative phosphorylation deficiency 17. Orthologous to human ELAC2 (elaC ribonuclease Z 2).