Automated description from the Alliance of Genome Resources
Predicted to have ATPase binding activity; identical protein binding activity; and peptidase activity, acting on L-amino acid peptides. Predicted to be involved in protein homooligomerization and protein quality control for misfolded or incompletely synthesized proteins. Localizes to the mitochondrion. Used to study Perrault syndrome. Human ortholog(s) of this gene implicated in Perrault syndrome. Is expressed in several structures, including genitourinary system; gut gland; musculature; salivary gland; and thymus. Orthologous to human CLPP (caseinolytic mitochondrial matrix peptidase proteolytic subunit).