Automated description from the Alliance of Genome Resources (Release 4.0)
Enables tripeptidyl-peptidase activity. Acts upstream of or within lysosomal protein catabolic process; lysosome organization; and neuromuscular process controlling balance. Located in lysosome. Is expressed in several structures, including alimentary system; central nervous system; eye; genitourinary system; and immune system. Used to study neuronal ceroid lipofuscinosis 2. Human ortholog(s) of this gene implicated in autosomal recessive spinocerebellar ataxia 7 and neuronal ceroid lipofuscinosis 2. Orthologous to human TPP1 (tripeptidyl peptidase 1).