Automated description from the Alliance of Genome Resources (Release 7.0.0)
Enables protein kinase activity. Predicted to be involved in several processes, including branched-chain amino acid catabolic process; regulation of glucose metabolic process; and spermatogenesis. Located in mitochondrion. Is expressed in several structures, including genitourinary system; heart; liver; lung; and skeletal muscle. Used to study autism spectrum disorder and branched-chain keto acid dehydrogenase kinase deficiency. Human ortholog(s) of this gene implicated in branched-chain keto acid dehydrogenase kinase deficiency. Orthologous to human BCKDK (branched chain keto acid dehydrogenase kinase).