Automated description from the Alliance of Genome Resources
Predicted to have ATP binding activity and ATPase activity. Predicted to be involved in cellular response to heat. Localizes to the mitochondrion. Human ortholog(s) of this gene implicated in 3-methylglutaconic aciduria with cataracts, neurologic involvement and neutropenia. Is expressed in several structures, including central nervous system; inner cell mass; limb; paravertebral ganglion; and retina. Orthologous to human CLPB (caseinolytic mitochondrial matrix peptidase chaperone subunit B).