Automated description from the Alliance of Genome Resources (Release 7.0.0)
Acts upstream of or within several processes, including fatty acid metabolic process; mitochondrial respiratory chain complex I assembly; and respiratory electron transport chain. Located in mitochondrion. Part of mitochondrial respiratory chain complex I. Is expressed in limb; respiratory system; and skeleton. Used to study mitochondrial complex I deficiency. Human ortholog(s) of this gene implicated in cervical cancer and nuclear type mitochondrial complex I deficiency 9. Orthologous to human NDUFS6 (NADH:ubiquinone oxidoreductase subunit S6).