Automated description from the Alliance of Genome Resources (Release 7.0.0)
Located in mitochondrial inner membrane. Part of mitochondrial respiratory chain complex I and mitochondrial respiratory chain complex IV. Is expressed in several structures, including alimentary system; central nervous system; integumental system; metanephros; and sensory organ. Human ortholog(s) of this gene implicated in mitochondrial complex IV deficiency nuclear type 21. Orthologous to human NDUFA4 (NDUFA4 mitochondrial complex associated).