Automated description from the Alliance of Genome Resources (Release 7.1.0)
Predicted to enable 3-demethoxyubiquinol 3-hydroxylase activity and chromatin binding activity. Acts upstream of or within several processes, including chordate embryonic development; determination of adult lifespan; and mitochondrial ATP synthesis coupled electron transport. Located in mitochondrion. Is expressed in several structures, including alimentary system; ear; heart; respiratory system; and skeleton. Human ortholog(s) of this gene implicated in autosomal recessive distal hereditary motor neuronopathy 9 and primary coenzyme Q10 deficiency 8. Orthologous to human COQ7 (coenzyme Q7, hydroxylase).