Automated description from the Alliance of Genome Resources
Predicted to have acetyltransferase activity; lipoic acid binding activity; and ubiquitin protein ligase binding activity. Localizes to the mitochondrion. Used to study maple syrup urine disease. Human ortholog(s) of this gene implicated in maple syrup urine disease. Orthologous to human DBT (dihydrolipoamide branched chain transacylase E2).