• the remnants of the pupillary membrane connect the opacity with the cornea

• failure of lens vesicle to separate from ectoderm

• pyramidal opacity at anterior pole of lens; uni- or bilateral and incomplete penetrance

• the opacity frequently protrudes into the anterior chamber and attaches to the cornea

• fusion of the lens to the cornea is associated with a defect in the corneal stroma and endothelium, which is filled with epithelial cells continuous with those covering the conically projecting anterior surface of the lens

• defect in the corneal stroma, which is filled with epithelial cells

• in the lens, a plaque of multilayered epithelial cells and degenerated cortical fibers underlay the fusion point

• the anterior pole of the lens is fused to the cornea

• failure of lens vesicle to separate from ectoderm

• eyes in which the lens and cornea are separated display an anterior polar cataract and central corneal defect involving the stroma, Descemet's membrane, and endothelium