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Disease Ontology Browser
idiopathic pulmonary fibrosis (DOID:0050156)
Synonyms: cryptogenic fibrosing alveolitis; FIBROCYSTIC PULMONARY DYSPLASIA; IDIOPATHIC PULMONARY FIBROSIS, FAMILIAL
Alt IDs: OMIM:178500, EFO:0000768, ICD10CM:J84.112, ICD9CM:516.31, MESH:D054990, NCI:C35715, NCI:C35716, UMLS_CUI:C1800706
Definition: An idiopathic interstitial pneumonia which is a distinctive type of chronic fibrosing interstitial pneumonia with thick scarring in the lung creating a honeycomb appearance. The main symptoms start insidiously as shortness of breath on exertion, cough, and diminished stamina. Other common complaints include weight loss and fatigue. The level of oxygen in the blood decreases, and the skin may take on a bluish tinge (called cyanosis) and the ends of the fingers may become thick or club-shape. In most people, symptoms worsen over a period ranging from about 6 months to several years.

Disease References using Mouse Models (2)

Contributing Projects:
Mouse Genome Database (MGD), Gene Expression Database (GXD), Mouse Tumor Biology (MTB), Gene Ontology (GO), MouseCyc
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last database update
06/13/2017
MGI 6.10
The Jackson Laboratory