Excel File Text File All mouse models of autosomal dominant polycystic kidney disease with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      autosomal dominant polycystic kidney disease Pkd2tm1.1Gwu/Pkd2tm1.1Gwu
Tg(Vil1-cre)997Gum/0
involves: C57BL/6 * C57BL/6J * SJL J:265516 View
polycystic kidney disease 1 Gpsm1tm1.1Lajb/Gpsm1tm1.1Lajb
Pkd1tm1.1Fqi/Pkd1tm1.1Fqi
involves: 129S6/SvEvTac J:193175 View
polycystic kidney disease 1 Pkd1b2b1585Clo/Pkd1b2b1585Clo C57BL/6J-Pkd1b2b1585Clo J:175213 View
polycystic kidney disease 1 Pkd1tm1.1Fqi/Pkd1tm1.1Fqi involves: 129S6/SvEvTac J:193175 View
polycystic kidney disease 1 Pkd1tm1.1Pcha/Pkd1tm1.1Pcha involves: 129S1/Sv * C57BL/6 J:193544 View
polycystic kidney disease 1 Pkd1tm1.1Pcha/Pkd1tm2Som
Tg(Cdh16-cre)91Igr/0
involves: 129 * 129S4/SvJae * C57BL/6 * ICR J:244067 View
polycystic kidney disease 1 Pkd1tm1Bdgz/Pkd1+ involves: 129S1/Sv * 129X1/SvJ J:130086 View
polycystic kidney disease 1 Pkd1tm1Djmp/Pkd1tm1Djmp involves: 129P2/OlaHsd * C57BL/6 J:94582 View
polycystic kidney disease 1 Pkd1tm1Ggg/Pkd1tm1Ggg Not Specified J:76062 View
polycystic kidney disease 1 Pkd1tm1Gztn/Pkd1tm1Gztn
Gt(ROSA)26Sortm9(cre/ESR1)Arte/Gt(ROSA)26Sor+
involves: 129S/Sv * 129S7/SvEvBrd * C57BL/6 J:162080 View
polycystic kidney disease 1 Pkd1tm1Jzh/Pkd1+ either: (involves: 129S4/SvJae * C57BL/6) or (involves: 129S4/SvJae * BALB/c) J:43193, J:52573, J:72627 View
polycystic kidney disease 1 Pkd1tm1Jzh/Pkd1tm1Jzh either: (involves: 129S4/SvJae * C57BL/6) or (involves: 129S4/SvJae * BALB/c) J:43193, J:72627, J:81443 View
polycystic kidney disease 1 Pkd1tm1Rsa/Pkd1+ involves: 129S4/SvJaeSor J:72238 View
polycystic kidney disease 1 Pkd1tm1Shh/Pkd1tm1.1Pcha involves: 129P2/OlaHsd * 129S1/Sv * C57BL/6 J:193544 View
polycystic kidney disease 1 Pkd1tm1Som/Pkd1+
Tg(Pkd1*)39Mtru/0
involves: 129/Sv * C57BL/6J * CBA/J * SJL J:198147 View
polycystic kidney disease 1 Pkd1tm2.1Ggg/Pkd1tm2.1Ggg involves: 129S4/SvJae * Black Swiss * C57BL/6 J:103719 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(Col1a1-cre)1Bek/0
involves: 129S4/SvJae * CD-1 J:191967 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(Hoxb7-cre)13Amc/0
involves: 129S4/SvJae * C57BL/6 J:171619 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(MMTV-cre)4Mam/0
involves: 129S4/SvJae * FVB J:103719 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(Nes-cre)Wme/0
involves: 129S4/SvJae * C57BL/6 * CBA J:185855 View
polycystic kidney disease 1 Pkd1tm2Jzh/Pkd1+ either: (involves: 129S4/SvJae * BALB/c) or (involves: 129S4/SvJae * C57BL/6) J:72627 View
polycystic kidney disease 1 Pkd1tm2Jzh/Pkd1tm2Jzh either: (involves: 129S4/SvJae * BALB/c) or (involves: 129S4/SvJae * C57BL/6) J:72627 View
polycystic kidney disease 1 Pkd1tm2Jzh/Pkd1tm2Jzh involves: 129S4/SvJae * C57BL/6 J:140012 View
polycystic kidney disease 1 Pkd1tm2Som/Pkd1tm2.1Som
Tg(Cdh16-cre)91Igr/0
involves: C57BL/6 * ICR * SJL J:135301 View
polycystic kidney disease 1 Pkd1tm2Som/Pkd1tm2Som
Tg(Cdh16-cre)91Igr/0
involves: 129S4/SvJae * C57BL/6 * ICR J:244067 View
polycystic kidney disease 1 Pkd1tm3.1Jzh/Pkd1tm3.1Jzh involves: 129P2/OlaHsd * C57BL/6 J:140012 View
polycystic kidney disease 1 Pkd1tm3Jzh/Pkd1tm3Jzh
Tg(Ggt1-cre)M3Egn/0
involves: 129P2/OlaHsd * C57BL/6 * SJL J:140012 View
polycystic kidney disease 1 Tg(Pkd1*)39Mtru/0 involves: C57BL/6J * CBA/J J:198147 View
polycystic kidney disease 2 Pkd2tm1Dwo/Pkd2tm1Dwo either: (involves: 129S1/Sv * 129X1/SvJ) or (involves: 129S1/Sv * 129X1/SvJ * C57BL/6) J:77401 View
polycystic kidney disease 2 Pkd2tm1Som/Pkd2+ involves: 129/Sv * C57BL/6J * SJL J:47035 View
polycystic kidney disease 2 Pkd2tm1Som/Pkd2tm1Som involves: 129/Sv * C57BL/6J * SJL J:47035 View
polycystic kidney disease 2 Pkd2tm1Som/Pkd2tm2Som involves: 129/Sv * C57BL/6J * SJL J:47035 View
polycystic kidney disease 2 Pkd2tm2Som/Pkd2+ involves: 129/Sv * C57BL/6J * SJL J:59314 View
polycystic kidney disease 2 Pkd2tm2Som/Pkd2tm2Som involves: 129/Sv * C57BL/6J * SJL J:59314 View
polycystic kidney disease 2 Pkd2tm3Som/Pkd2tm3Som
Tg(Pkhd1-cre)1Igr/0
involves: 129S4/SvJae * C57BL/6 J:244067 View
      autosomal dominant polycystic kidney disease Bicc1jcpk/Bicc1+ involves: 101 * C3H * T STOCK J:23047 View
autosomal dominant polycystic kidney disease Nphp3pcy/Nphp3pcy either: D2.KK-Nphp3pcy or (involves: DBA/2Fg * DBA/2J * KK) J:11399 View
autosomal dominant polycystic kidney disease Nphp3pcy/Nphp3pcy involves: KK J:244067 View
autosomal dominant polycystic kidney disease Nphp3pcy/Nphp3pcy KK-Nphp3pcy J:8302 View
autosomal dominant polycystic kidney disease Tg(HBB-Myc)#Cos/0 involves: C57BL/6J * CBA/J J:45203 View
Transgenes and
Other Mutations
     polycystic kidney disease 2 Tg(CAG-PKD2)#Hwl/? involves: FVB/NJ J:148377 View