Excel File Text File All mouse models of progeria with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      progeria \LmnaDhe/\Lmna+ B6(D2)-LmnaDhe/TyGrsrJ J:171665 View
progeria \Lmnaem1Fenz/\Lmna+ C57BL/6-Lmnaem1Fenz J:338760 View
progeria \Lmnatm1.1Bliu/\Lmna+ involves: C57BL/6 * FVB/N J:287256 View
progeria \Lmnatm1.1Bliu/\Lmnatm1.1Bliu involves: C57BL/6 * FVB/N J:287256 View
progeria \Lmnatm1.1Otin/\Lmna+ involves: 129P2/OlaHsd * C57BL/6 J:211388 View
progeria \Lmnatm1.1Otin/\Lmna+ involves: 129P2/OlaHsd * C57BL/6NTac J:261974 View
progeria \Lmnatm1.1Otin/\Lmna+
\Nat10tm1a(KOMP)Wtsi/\Nat10+
involves: 129P2/OlaHsd * C57BL/6NTac J:261974 View
progeria \Lmnatm1.1Otin/\Lmnatm1.1Otin involves: 129P2/OlaHsd * C57BL/6 J:177575, J:177632, J:211388 View
progeria \Lmnatm1.1Otin/\Lmnatm1.1Otin involves: 129P2/OlaHsd * C57BL/6NTac J:261974 View
progeria \Lmnatm1.1Otin/\Lmnatm1.1Otin
\Nat10tm1a(KOMP)Wtsi/\Nat10+
involves: 129P2/OlaHsd * C57BL/6NTac J:261974 View
progeria \Lmnatm1Bliu/\Lmnatm1Bliu
\Tg(Tek-cre)1Ywa/0
involves: C57BL/6 * SJL J:287256 View
progeria \Lmnatm1Lgf/\Lmna+ involves: 129P2/OlaHsd * C57BL/6 J:113119 View
progeria \Lmnatm2Stw/\Lmnatm2Stw involves: 129S1/Sv J:83382 View
progeria \Lmnatm12Lgf/\Lmnatm12Lgf involves: 129P2/OlaHsd * C57BL/6 J:234711 View
      progeria \Sirt6tm1Fwa/\Sirt6tm1Fwa involves: 129S6/SvEvTac * 129X1/SvJ J:112817 View
progeria \Vcpip1em1Zlou/\Vcpip1em1Zlou C57BL/6NHsd-Vcpip1em1Zlou J:297179 View
progeria \Zmpste24tm1Otin/\Zmpste24tm1Otin involves: 129P2/OlaHsd J:164373 View
progeria \Zmpste24tm1Sgy/\Zmpste24tm1Sgy B6.129S4-Zmpste24tm1Sgy J:106706 View
progeria \Zmpste24tm1Sgy/\Zmpste24tm1Sgy involves: 129S4/SvJae * C57BL/6 J:95274 View
Transgenes and
Other Mutations
     progeria \Tg(KRT5-tTA)1216Glk/0
\Tg(tetO-LMNA*G608G,-EGFP)VF1-07Maer/0
involves: FVB/N J:145312 View
progeria \Tg(LMNA*G608G)HClns/? C57BL/6-Tg(LMNA*G608G)HClns/J J:107176 View


       
No similarity to the expected human disease phenotype was found.
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
NOT Models      progeria \Lmnatm5Lgf/\Lmnatm5Lgf involves: 129P2/OlaHsd * C57BL/6 J:160705 View
progeria \Lmnatm8Lgf/\Lmnatm8Lgf involves: 129P2/OlaHsd J:167229 View