Excel File Text File All mouse models of progeria with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      progeria LmnaDhe/Lmna+ B6(D2)-LmnaDhe/TyGrsrJ J:171665 View
progeria Lmnaem1Fenz/Lmna+ C57BL/6-Lmnaem1Fenz J:338760 View
progeria Lmnatm1.1Otin/Lmna+ involves: 129P2/OlaHsd * C57BL/6 J:211388 View
progeria Lmnatm1.1Otin/Lmna+ involves: 129P2/OlaHsd * C57BL/6NTac J:261974 View
progeria Lmnatm1.1Otin/Lmna+
Nat10tm1a(KOMP)Wtsi/Nat10+
involves: 129P2/OlaHsd * C57BL/6NTac J:261974 View
progeria Lmnatm1.1Otin/Lmnatm1.1Otin involves: 129P2/OlaHsd * C57BL/6 J:177575, J:177632, J:211388 View
progeria Lmnatm1.1Otin/Lmnatm1.1Otin involves: 129P2/OlaHsd * C57BL/6NTac J:261974 View
progeria Lmnatm1.1Otin/Lmnatm1.1Otin
Nat10tm1a(KOMP)Wtsi/Nat10+
involves: 129P2/OlaHsd * C57BL/6NTac J:261974 View
progeria Lmnatm1Bliu/Lmna+
Tg(Tek-cre)1Ywa/0
involves: C57BL/6 * SJL J:287256 View
progeria Lmnatm1Lgf/Lmna+ involves: 129P2/OlaHsd * C57BL/6 J:113119 View
progeria Lmnatm2Stw/Lmnatm2Stw involves: 129S1/Sv J:83382 View
progeria Lmnatm12Lgf/Lmnatm12Lgf involves: 129P2/OlaHsd * C57BL/6 J:234711 View
      progeria Sirt6tm1Fwa/Sirt6tm1Fwa involves: 129S6/SvEvTac * 129X1/SvJ J:112817 View
progeria Vcpip1em1Zlou/Vcpip1em1Zlou C57BL/6NHsd-Vcpip1em1Zlou J:297179 View
progeria Zmpste24tm1Otin/Zmpste24tm1Otin involves: 129P2/OlaHsd J:164373 View
progeria Zmpste24tm1Sgy/Zmpste24tm1Sgy B6.129S4-Zmpste24tm1Sgy J:106706 View
progeria Zmpste24tm1Sgy/Zmpste24tm1Sgy involves: 129S4/SvJae * C57BL/6 J:95274 View
Transgenes and
Other Mutations
     progeria Tg(KRT5-tTA)1216Glk/0
Tg(tetO-LMNA*G608G,-EGFP)VF1-07Maer/0
involves: FVB/N J:145312 View
progeria Tg(LMNA*G608G)HClns/? C57BL/6-Tg(LMNA*G608G)HClns/J J:107176 View


       
No similarity to the expected human disease phenotype was found.
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
NOT Models      progeria Lmnatm5Lgf/Lmnatm5Lgf involves: 129P2/OlaHsd * C57BL/6 J:160705 View
progeria Lmnatm8Lgf/Lmnatm8Lgf involves: 129P2/OlaHsd J:167229 View