Excel File Text File All mouse models of arrhythmogenic right ventricular cardiomyopathy with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      arrhythmogenic right ventricular cardiomyopathy \Dsg2em1Spin/\Dsg2+ involves: C57BL/6J J:342765 View
arrhythmogenic right ventricular dysplasia 8 \Dsptm1Efu/\Dsptm1Efu
\Myl2tm1(cre)Krc/\Myl2+
involves: 129 * 129S4/SvJae * C57BL/6 J:205990 View
arrhythmogenic right ventricular dysplasia 10 \Dsg2tm1d(EUCOMM)Wtsi/\Dsg2tm1d(EUCOMM)Wtsi involves: C57BL/6J * C57BL/6N J:235770 View
arrhythmogenic right ventricular dysplasia 12 \Juptm1.1Glr/\Juptm1.1Glr
\A1cfTg(Myh6-cre/Esr1*)1Jmk/\A1cf+
involves: 129S6/SvEvTac * C57BL/6 * FVB/N * SJL J:170618 View
arrhythmogenic right ventricular dysplasia 12 \Juptm1.1Shou/\Juptm1.1Shou
\Tg(Myh6-cre)2182Mds/0
involves: 129 * C57BL/6J J:177567 View
arrhythmogenic right ventricular dysplasia 12 \Juptm1Ruiz/\Jup+
\Tg(Myh6-Jup*)1Ajm/0
involves: 129P2/OlaHsd * C57BL/6 * FVB/N J:192719 View
arrhythmogenic right ventricular dysplasia 12 \Tg(Myh6-Jup*)1Ajm/0 involves: FVB/N J:192719 View
      arrhythmogenic right ventricular cardiomyopathy \Pdlim3tm1Krc/\Pdlim3tm1Krc either: (involves: 129S) or (involves: C57BL/6) or (involves: Black Swiss) J:69097 View
arrhythmogenic right ventricular cardiomyopathy \Ppp1r13ltm1.1Xlu/\Ppp1r13ltm1.1Xlu involves: 129 * C57BL/6J J:220162 View
arrhythmogenic right ventricular dysplasia 5 \Rpsatp1/\Rpsatp1 involves: KK J:87868 View
Transgenes and
Other Mutations
     arrhythmogenic right ventricular cardiomyopathy \Tg(CMV-cat,-ROCK2*)3-1Koba/0
\Tg(Tagln-cre)1Her/0
involves: C57BL/6 * C57BL/6JJcl * DBA/2 * SJL J:242116 View
arrhythmogenic right ventricular dysplasia 9 \Tg(Myh6-Pkp2*/mRuby)4Rbrug/0 involves: C57BL/6 * DBA/2 J:237859 View
arrhythmogenic right ventricular dysplasia 9 \Tg(Myh6-Pkp2*/mRuby)4Rbrug/0
\Tg(Myh6-Pkp2*/mRuby)5Rbrug/0
involves: C57BL/6 * DBA/2 J:237859 View
arrhythmogenic right ventricular dysplasia 9 \Tg(Myh6-Pkp2*/mRuby)5Rbrug/0 involves: C57BL/6 * DBA/2 J:237859 View
arrhythmogenic right ventricular dysplasia 12 \Tg(Myh6-JUP*)1Dpju/0 FVB/N-Tg(Myh6-JUP*)1Dpju J:235770 View