Excel File Text File All mouse models of von Hippel-Lindau disease with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      von Hippel-Lindau disease Hif1atm3Rsjo/Hif1atm3Rsjo
Hprt1tm1(Pck1-cre)Vhh/Y
Vhltm1Jae/Vhltm1Jae
involves: 129 * BALB/c * C57BL/6 J:97652, J:106705 View
von Hippel-Lindau disease Hif1atm3Rsjo/Hif1atm3Rsjo
Vhltm1Jae/Vhltm1Jae
Speer6-ps1Tg(Alb-cre)21Mgn/Speer6-ps1+
involves: 129 * BALB/c * C57BL/6 * DBA J:97652 View
von Hippel-Lindau disease Hprt1tm1(Pck1-cre)Vhh/Y
Vhltm1Jae/Vhltm1Jae
involves: 129P2/OlaHsd * 129S4/SvJae * BALB/c * C57BL/6 J:97652, J:106705 View
von Hippel-Lindau disease Ptentm1Hwu/Ptentm1Hwu
Vhltm1Jae/Vhltm1Jae
Tg(Cdh16-cre)91Igr/0
involves: 129S4/SvJae * BALB/c * C57BL/6J * ICR J:137073 View
von Hippel-Lindau disease Ptentm1Hwu/Ptentm1Hwu
Vhltm1Jae/Vhltm1Jae
Tg(Cdh16-cre)91Igr/0
involves: 129S4/SvJae * ICR J:137442 View
von Hippel-Lindau disease Vhltm1.1Jae/Vhl+ involves: 129S4/SvJae * BALB/c J:67505 View
von Hippel-Lindau disease Vhltm1.1Lss/Vhl+ involves: A/J J:85513 View
von Hippel-Lindau disease Vhltm1.1Lss/Vhl+ involves: BALB/c J:85513 View
von Hippel-Lindau disease Vhltm1.1Wkr/Vhl+ involves: 129S4/SvJae * C57BL/6 J:157369 View
von Hippel-Lindau disease Vhltm1Jae/Vhltm1Jae
Speer6-ps1Tg(Alb-cre)21Mgn/Speer6-ps1+
involves: 129S4/SvJae * BALB/c * C57BL/6 * DBA J:67505, J:97652 View
von Hippel-Lindau disease Vhltm1Lss/Vhltm1.1Lss involves: 129X1/SvJ * C57BL/6 J:85513 View
von Hippel-Lindau disease Vhltm1Lss/Vhltm1.1Lss
Tg(ACTB-cre)1Tes/0
involves: 129X1/SvJ * C3H * C57BL/6 J:85513 View
von Hippel-Lindau disease Vhltm1Lss/Vhltm1Lss
Tg(Gcg-cre)1Slib/0
either: (involves: 129X1/SvJ * A/J) or (involves: 129X1/SvJ * C57BL/6) J:148174 View
von Hippel-Lindau disease Vhltm1Lss/Vhltm1Lss
Tg(Ins2-cre)25Mgn/0
either: (involves: 129X1/SvJ * C57BL/6 * DBA) or (involves: 129X1/SvJ * A/J * C57BL/6 * DBA) J:148174 View
von Hippel-Lindau disease Vhltm1Lss/Vhltm1Lss
Tg(Pdx1-cre)89.1Dam/0
involves: 129X1/SvJ * C57BL/6 * CBA J:148174 View
von Hippel-Lindau disease Vhltm1Wml/Vhltm1Wml involves: 129S4/SvJae * C57BL/6 J:42846, J:88492 View
Transgenes and
Other Mutations
     von Hippel-Lindau disease Tg(Ggt1-Hif1a*)43Log/0 involves: C57BL/6 J:177381 View