Excel File Text File All mouse models of focal segmental glomerulosclerosis with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      focal segmental glomerulosclerosis 1 \Actn4tm1Mrpk/\Actn4tm1Mrpk involves: 129 * C57BL/6 J:83911 View
focal segmental glomerulosclerosis 2 \Tg(NPHS2-Trpc6)F419Walz/0 involves: C57BL/6J * CBA/J J:165112 View
focal segmental glomerulosclerosis 2 \Tg(NPHS2-Trpc6*E896K)F75aWalz/0 involves: C57BL/6J * CBA/J J:165112 View
focal segmental glomerulosclerosis 2 \Tg(NPHS2-Trpc6*P111Q)F615Walz/0 involves: C57BL/6J * CBA/J J:165112 View
focal segmental glomerulosclerosis 3 \Cd2apem1Irgu/\Cd2apem1Irgu C57BL/6-Cd2apem1Irgu J:294238 View
      focal segmental glomerulosclerosis \Cmastm1.1Bwei/\Cmastm1.1Bwei
\Tg(NPHS2-cre)295Lbh/0
involves: 129P2/OlaHsd * C57BL/6 * SJL J:286022 View
focal segmental glomerulosclerosis \Gt(ROSA)26Sortm3(tetO-Mir193)Arte/\Gt(ROSA)26Sor+ involves: 129 * BALB/c * C57BL/6 J:197989 View
focal segmental glomerulosclerosis \Gt(ROSA)26Sortm3(tetO-Mir193)Arte/\Gt(ROSA)26Sortm3(tetO-Mir193)Arte involves: 129 * BALB/c * C57BL/6 J:197989 View
focal segmental glomerulosclerosis \Myo9aem1Atuf/\Myo9a+ C57BL/6J-Myo9aem1Atuf J:302901 View
focal segmental glomerulosclerosis \Srgap1tm1a(KOMP)Wtsi/\Srgap1tm1a(KOMP)Wtsi
\Six2tm1(tTA,tetO-EGFP/cre)Amc/\Six2+
involves: 129 * C57BL/6J * C57BL/6N J:333727 View
focal segmental glomerulosclerosis \Tnfaip2tm1.1Ohno/\Tnfaip2tm1.1Ohno C.Cg-Tnfaip2tm1.1Ohno J:343202 View
Transgenes and
Other Mutations
     focal segmental glomerulosclerosis \Tg(Thy1/THY1)T6Gsv/0 involves: C57BL/10 * CBA J:294728, J:294621 View
Additional
Complex
Models
     focal segmental glomerulosclerosis \Gt(ROSA)26Sortm1Sor/\Gt(ROSA)26Sortm1Sor
\Tg(NPHS2-rtTA2*M2)1Jbk/\Tg(NPHS2-rtTA2*M2)1Jbk
\Tg(tetO-cre)LC1Bjd/\Tg(tetO-cre)LC1Bjd
involves: 129S4/SvJaeSor * BALB/c * C57BL/6 * FVB/N J:285673 View


       
No similarity to the expected human disease phenotype was found.
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
NOT Models      focal segmental glomerulosclerosis 1 \Tg(CMV-Plaur*)19Lbh/0 FVB/N-Tg(CMV-Plaur*)19Lbh J:217443 View