| Disease Term | Human Homologs | Mouse Homologs | Mouse Models | Homology Source | |||
| PCWH syndrome | SOX10* | Sox10* | 1 model | Alliance of Genome Resources | ||
| PCWH syndrome | MPZ | Mpz* | 1 model | Alliance of Genome Resources | ||
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Transgenes and other genome features developed in mice to model this disease.
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| Disease Term | Transgenes and Other Genome Features | Mouse Models | |
| PCWH syndrome | Tg(Venus/SOX10*)55Kein | 2 models | |