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Symbol
Name
ID
Lmna
lamin A
MGI:96794
Phenotype annotations related to mortality/aging
*Aspects of the system are reported to show a normal phenotype.
Darker colors indicate more annotations
Human Phenotypes
Death in infancy
Miscarriage
Sudden cardiac death
Disease(s) Associated with LMNA
autosomal dominant Emery-Dreifuss muscular dystrophy 2
congenital muscular dystrophy due to LMNA mutation
dilated cardiomyopathy 1A
Emery-Dreifuss muscular dystrophy
Werner syndrome

Mouse Phenotypes
mortality/aging
decreased survivor rate
premature death
postnatal lethality, complete penetrance
preweaning lethality, complete penetrance
premature aging
Availability Mouse Genotype
LmnaDhe/LmnaDhe
LmnaGt(S7-1F1)Sor/LmnaGt(S7-1F1)Sor *
Lmnatm1.1Bliu/Lmnatm1.1Bliu
Lmnatm1.1Otin/Lmnatm1.1Otin
Lmnatm1.2Yxz/Lmnatm1.2Yxz
Lmnatm1b(EUCOMM)Wtsi/Lmnatm1b(EUCOMM)Wtsi
Lmnatm1Gbon/Lmnatm1Gbon
Lmnatm1Lgf/Lmnatm1Lgf
Lmnatm1Stw/Lmnatm1Stw
Lmnatm2.1Gbon/Lmnatm2.1Gbon
Lmnatm2Stw/Lmnatm2Stw
Lmnatm3Lgf/Lmnatm3Lgf
Lmnatm3Stw/Lmnatm3Stw
Lmnatm5Lgf/Lmnatm5Lgf
Lmnatm7Lgf/Lmnatm7Lgf *
Lmnatm8Lgf/Lmnatm8Lgf *
Lmnatm9Lgf/Lmnatm9Lgf *
Lmnatm10Lgf/Lmnatm10Lgf *
Lmnatm11Lgf/Lmnatm11Lgf
LmnaDhe/Lmna+
Lmnatm1.1Bliu/Lmna+
Lmnatm1.1Otin/Lmna+
Lmnatm1Lgf/Lmna+
Lmnatm1Lgf/Lmnatm1Stw
Lmnatm2.1Gbon/Lmna+
Lmnatm3Lgf/Lmna+
Lmnatm4Lgf/Lmna+
Lmnatm11Lgf/Lmna+
Lmnatm4Stw/Lmnatm4Stw
Tg(Zp3-cre)93Knw/0  (conditional)
Lmnatm1Bliu/Lmna+
Tg(Tek-cre)1Ywa/0  (conditional)

Contributing Projects:
Mouse Genome Database (MGD), Gene Expression Database (GXD), Mouse Models of Human Cancer database (MMHCdb) (formerly Mouse Tumor Biology (MTB)), Gene Ontology (GO)
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last database update
04/16/2024
MGI 6.23
The Jackson Laboratory