| Disease Term | Human Homologs | Mouse Homologs | Mouse Models | Homology Source | |||
| Leigh disease | NDUFS4* | Ndufs4* | 3 models | Alliance of Genome Resources | ||
| Leigh disease | SURF1* | Surf1* | 1 model | Alliance of Genome Resources | |||
| Leigh disease | PARL | Parl* | 2 models | Alliance of Genome Resources | ||
| Leigh disease | SDHC | Sdhc* | 1 model | Alliance of Genome Resources | |||
| Leigh disease | SOD2 | Sod2* | 1 model | Alliance of Genome Resources | |||
| Leigh disease | COX15* | Cox15 | Alliance of Genome Resources | ||||
| Leigh disease | LRPPRC* | Lrpprc | Alliance of Genome Resources | ||||
| Leigh disease | ND3* | mt-Nd3 | Alliance of Genome Resources | ||||
| Leigh disease | ND5* | mt-Nd5 | Alliance of Genome Resources | ||||
| Leigh disease | ND6* | mt-Nd6 | Alliance of Genome Resources | ||||
| Leigh disease | NDUFS2* | Ndufs2 | Alliance of Genome Resources | ||||
| Leigh disease | SDHA* | Sdha | Alliance of Genome Resources | ||||
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Transgenes and other genome features developed in mice to model this disease.
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| Disease Term | Transgenes and Other Genome Features | Mouse Models | |
| Leigh disease | Tg(ATP6*)#aJguy | 1 model | |