| Disease Term | Human Homologs | Mouse Homologs | Mouse Models | Homology Source | |||
| autosomal recessive nonsyndromic deafness 1A | GJB2* | Gjb2* | 2 models | Alliance of Genome Resources | ||
| autosomal recessive nonsyndromic deafness 1A | GJB6* | Gjb6* | 3 models | Alliance of Genome Resources | |||
| autosomal recessive nonsyndromic deafness 1A | GJB3* | Gjb3 | Alliance of Genome Resources | ||||
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Transgenes and other genome features developed in mice to model this disease.
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| Disease Term | Transgenes and Other Genome Features | Mouse Models | |
| autosomal recessive nonsyndromic deafness 1A | Del(14Gjb6-Cryl1)1Lmon | 1 model | |