| Disease Term | Human Homologs | Mouse Homologs | Mouse Models | Homology Source | |||
| amyotrophic lateral sclerosis type 4 | SETX* | Setx* | 1 model | Alliance of Genome Resources | ||
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Transgenes and other genome features developed in mice to model this disease.
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| Disease Term | Transgenes and Other Genome Features | Mouse Models | |
| amyotrophic lateral sclerosis type 4 | Tg(Prnp-SETX*R2136H)1920Als | 1 model | |