| Disease Term | Human Homologs | Mouse Homologs | Mouse Models | Homology Source | |||
| spinocerebellar ataxia 1 | ATXN1* | Atxn1* | 1 model | Alliance of Genome Resources | ||
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Transgenes and other genome features developed in mice to model this disease.
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| Disease Term | Transgenes and Other Genome Features | Mouse Models | |
| spinocerebellar ataxia 1 | Tg(Pcp2-ATXN1*82Q)5Horr | 1 model | |
| spinocerebellar ataxia 1 | Tg(tetO-ATXN1*82Q)#Horr | 1 model | |