| Disease Term | Human Homologs | Mouse Homologs | Mouse Models | Homology Source | |||
| X-linked deafness 4 | SMPX* | Smpx* | 6 models | Alliance of Genome Resources | ||
| X-linked deafness 1 | PRPS1* | Prps1, Prps1l3 | Alliance of Genome Resources | ||||
| X-linked deafness 2 | POU3F4* | Pou3f4 | Alliance of Genome Resources | ||||
| X-linked deafness 6 | COL4A6* | Col4a6 | Alliance of Genome Resources | ||||
| X-linked deafness 7 | GPRASP2*, ARMCX5-GPRASP2 | Gprasp2 | Alliance of Genome Resources | ||||