ModelCategory	Disease Term	Allele Composition	Genetic Background	Reference
MouseAndHuman	Alport syndrome 2	Col4a3<tm1Dec>/Col4a3<tm1Dec> 	129-Col4a3<tm1Dec>/J	J:158731 
MouseAndHuman	Alport syndrome 2	Col4a3<tm1Dec>/Col4a3<tm1Dec> 	129X1/SvJ-Col4a3<tm1Dec>	J:91619 
MouseAndHuman	Alport syndrome 2	Col4a3<tm1Dec>/Col4a3<tm1Dec> 	involves: 129X1/SvJ * C57BL/6	J:37963 
MouseAndHuman	Alport syndrome 2	Col4a3<tm1Jhm>/Col4a3<tm1Jhm> 	involves: 129S1/Sv * 129X1/SvJ	J:37017 J:207595 
MouseAndHuman	Alport syndrome 2	Col4a3<tm1Jhm>/Col4a3<tm1Jhm> Mmp9<tm1Tvu>/Mmp9<tm1Tvu> 	involves: 129S1/Sv * 129S6/SvEvTac * 129X1/SvJ	J:63137 
MouseAndHuman	Alport syndrome 2	Col4a4<bwk>/Col4a4<bwk> 	129S1.NON(NZO)-Col4a4<bwk>/PgnJ	J:223185 
MouseAndHuman	Alport syndrome 2	Col4a4<bwk>/Col4a4<bwk> 	D2.NON(NZO)-Col4a4<bwk>/GrsrJ	J:223185 
MouseAndHuman	Alport syndrome 2	Col4a4<bwk>/Col4a4<bwk> 	NON;NZO-Col4a4<bwk>/J	J:223185 
MouseAndHuman	Alport syndrome 2	Col4a4<m1Btlr>/Col4a4<m1Btlr> 	C57BL/6J-Col4a4<m1Btlr>	J:158794 J:170552 
MouseAndHuman	Alport syndrome 2	Col4a4<m1H>/Col4a4<m1H> 	involves: C3H/HeH * C57BL/6J	J:285510 
MouseAndHuman	autosomal dominant polycystic kidney disease	Pkd2<tm1.1Gwu>/Pkd2<tm1.1Gwu> Tg(Vil1-cre)997Gum/0 	involves: C57BL/6 * C57BL/6J * SJL	J:265516 
MouseAndHuman	polycystic kidney disease 1	Gpsm1<tm1.1Lajb>/Gpsm1<tm1.1Lajb> Pkd1<tm1.1Fqi>/Pkd1<tm1.1Fqi> 	involves: 129S6/SvEvTac	J:193175 
MouseAndHuman	polycystic kidney disease 1	Pkd1<b2b1585Clo>/Pkd1<b2b1585Clo> 	C57BL/6J-Pkd1<b2b1585Clo>	J:175213 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1.1Fqi>/Pkd1<tm1.1Fqi> 	involves: 129S6/SvEvTac	J:193175 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1.1Pcha>/Pkd1<tm1.1Pcha> 	involves: 129S1/Sv * C57BL/6	J:193544 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1.1Pcha>/Pkd1<tm2Som> Tg(Cdh16-cre)91Igr/0 	involves: 129 * 129S4/SvJae * C57BL/6 * ICR	J:244067 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1Bdgz>/Pkd1<+> 	involves: 129S1/Sv * 129X1/SvJ	J:130086 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1Djmp>/Pkd1<tm1Djmp> 	involves: 129P2/OlaHsd * C57BL/6	J:94582 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1Ggg>/Pkd1<tm1Ggg> 	Not Specified	J:76062 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1Gztn>/Pkd1<tm1Gztn> Gt(ROSA)26Sor<tm9(cre/ESR1)Arte>/Gt(ROSA)26Sor<+> 	involves: 129S/Sv * 129S7/SvEvBrd * C57BL/6	J:162080 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1Jzh>/Pkd1<+> 	either: (involves: 129S4/SvJae * C57BL/6) or (involves: 129S4/SvJae * BALB/c)	J:43193 J:52573 J:72627 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1Jzh>/Pkd1<tm1Jzh> 	either: (involves: 129S4/SvJae * C57BL/6) or (involves: 129S4/SvJae * BALB/c)	J:43193 J:72627 J:81443 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1Rsa>/Pkd1<+> 	involves: 129S4/SvJaeSor	J:72238 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1Shh>/Pkd1<tm1.1Pcha> 	involves: 129P2/OlaHsd * 129S1/Sv * C57BL/6	J:193544 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm1Som>/Pkd1<+> Tg(Pkd1*)39Mtru/0 	involves: 129/Sv * C57BL/6J * CBA/J * SJL	J:198147 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2.1Ggg>/Pkd1<tm2.1Ggg> 	involves: 129S4/SvJae * Black Swiss * C57BL/6	J:103719 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Ggg>/Pkd1<tm2Ggg> Tg(Col1a1-cre)1Bek/0 	involves: 129S4/SvJae * CD-1	J:191967 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Ggg>/Pkd1<tm2Ggg> Tg(Hoxb7-cre)13Amc/0 	involves: 129S4/SvJae * C57BL/6	J:171619 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Ggg>/Pkd1<tm2Ggg> Tg(MMTV-cre)4Mam/0 	involves: 129S4/SvJae * FVB	J:103719 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Ggg>/Pkd1<tm2Ggg> Tg(Nes-cre)Wme/0 	involves: 129S4/SvJae * C57BL/6 * CBA	J:185855 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Jzh>/Pkd1<+> 	either: (involves: 129S4/SvJae * BALB/c) or (involves: 129S4/SvJae * C57BL/6)	J:72627 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Jzh>/Pkd1<tm2Jzh> 	either: (involves: 129S4/SvJae * BALB/c) or (involves: 129S4/SvJae * C57BL/6)	J:72627 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Jzh>/Pkd1<tm2Jzh> 	involves: 129S4/SvJae * C57BL/6	J:140012 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Som>/Pkd1<tm2.1Som> Tg(Cdh16-cre)91Igr/0 	involves: C57BL/6 * ICR * SJL	J:135301 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Som>/Pkd1<tm2Som> Tg(Cdh16-cre)91Igr/0 	involves: 129S4/SvJae * C57BL/6 * ICR	J:244067 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm2Som>/Pkd1<tm2Som> Tg(Pkhd1-cre)1Igr/0 	involves: C57BL/6 * SJL	J:379194 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm3.1Jzh>/Pkd1<tm3.1Jzh> 	involves: 129P2/OlaHsd * C57BL/6	J:140012 
MouseAndHuman	polycystic kidney disease 1	Pkd1<tm3Jzh>/Pkd1<tm3Jzh> Tg(Ggt1-cre)M3Egn/0 	involves: 129P2/OlaHsd * C57BL/6 * SJL	J:140012 
MouseAndHuman	polycystic kidney disease 1	Tg(Pkd1*)39Mtru/0 	involves: C57BL/6J * CBA/J	J:198147 
MouseAndHuman	polycystic kidney disease 2	Pkd2<tm1Dwo>/Pkd2<tm1Dwo> 	either: (involves: 129S1/Sv * 129X1/SvJ) or (involves: 129S1/Sv * 129X1/SvJ * C57BL/6)	J:77401 
MouseAndHuman	polycystic kidney disease 2	Pkd2<tm1Som>/Pkd2<+> 	involves: 129/Sv * C57BL/6J * SJL	J:47035 
MouseAndHuman	polycystic kidney disease 2	Pkd2<tm1Som>/Pkd2<tm1Som> 	involves: 129/Sv * C57BL/6J * SJL	J:47035 
MouseAndHuman	polycystic kidney disease 2	Pkd2<tm1Som>/Pkd2<tm2Som> 	involves: 129/Sv * C57BL/6J * SJL	J:47035 
MouseAndHuman	polycystic kidney disease 2	Pkd2<tm2Som>/Pkd2<+> 	involves: 129/Sv * C57BL/6J * SJL	J:59314 
MouseAndHuman	polycystic kidney disease 2	Pkd2<tm2Som>/Pkd2<tm2Som> 	involves: 129/Sv * C57BL/6J * SJL	J:59314 
MouseAndHuman	polycystic kidney disease 2	Pkd2<tm3Som>/Pkd2<tm3Som> Tg(Pkhd1-cre)1Igr/0 	involves: 129S4/SvJae * C57BL/6	J:244067 
MouseAndHuman	X-linked Alport syndrome	Col4a5<em1Keha>/Y 	C57BL/6J-Col4a5<em1Keha>	J:283613 
MouseAndHuman	X-linked Alport syndrome	Col4a5<tm1Yseg>/Col4a5<+> 	B6.Cg-Col4a5<tm1Yseg>	J:102306 J:210414 
MouseAndHuman	X-linked Alport syndrome	Col4a5<tm1Yseg>/Y 	B6.Cg-Col4a5<tm1Yseg>	J:102306 J:210414 
MouseOnly	Alport syndrome 2	Mpv17/Mpv17 	CFW-Mpv17/J	J:48653 
MouseOnly	autosomal dominant polycystic kidney disease	Bicc1<jcpk>/Bicc1<+> 	involves: 101 * C3H * T STOCK	J:23047 
MouseOnly	autosomal dominant polycystic kidney disease	Nphp3<pcy>/Nphp3<pcy> 	either: D2.KK-Nphp3<pcy> or (involves: DBA/2Fg * DBA/2J * KK)	J:11399 
MouseOnly	autosomal dominant polycystic kidney disease	Nphp3<pcy>/Nphp3<pcy> 	involves: KK	J:244067 
MouseOnly	autosomal dominant polycystic kidney disease	Nphp3<pcy>/Nphp3<pcy> 	KK-Nphp3<pcy>	J:8302 
MouseOnly	autosomal dominant polycystic kidney disease	Tg(HBB-Myc)#Cos/0 	involves: C57BL/6J * CBA/J	J:45203 
TransgenesAndOtherMutations	polycystic kidney disease 2	Tg(CAG-PKD2)#Hwl/? 	involves: FVB/NJ	J:148377