GeneCategory	Disease Term	Mouse Homologs	Human Homologs	Transgenes And Other Features	Mouse Models	Homology Source
MouseAndHuman	Alport syndrome 2	 Col4a4* 	 COL4A4* 	 	5	Alliance Clustered	
MouseAndHuman	Alport syndrome 2	 Col4a3* 	 COL4A3* 	 	5	Alliance Clustered	
MouseAndHuman	autosomal dominant polycystic kidney disease	 Pkd2* 	 PKD2* 	 	1	Alliance Clustered	
MouseAndHuman	polycystic kidney disease 1	 Pkd1* 	 PKD1* 	 	28	Alliance Clustered	
MouseAndHuman	polycystic kidney disease 2	 Pkd2* 	 PKD2* 	 	7	Alliance Clustered	
MouseAndHuman	X-linked Alport syndrome	 Col4a5* 	 COL4A5* 	 	3	Alliance Clustered	
MouseOnly	Alport syndrome 2	 Mpv17* 	 MPV17 	 	1	Alliance Clustered	
MouseOnly	autosomal dominant polycystic kidney disease	 Bicc1* 	 BICC1 	 	1	Alliance Clustered	
MouseOnly	autosomal dominant polycystic kidney disease	 Myc* 	 MYC 	 	1	Alliance Clustered	
MouseOnly	autosomal dominant polycystic kidney disease	 Nphp3* 	 NPHP3 	 	3	Alliance Clustered	
HumanOnly	Alport syndrome	 Col4a3 	 COL4A3* 	 	0	Alliance Clustered	
HumanOnly	Alport syndrome	 Col4a5 	 COL4A5* 	 	0	Alliance Clustered	
HumanOnly	Alport syndrome	 H2-Eb1 H2-Eb2 	 HLA-DRB1* HLA-DRB3 HLA-DRB4 HLA-DRB5 	 	0	Alliance Clustered	
HumanOnly	Alport syndrome 3A	 Col4a3 	 COL4A3* 	 	0	Alliance Clustered	
HumanOnly	Alport syndrome 3A	 Myh9 	 MYH9* 	 	0	Alliance Clustered	
HumanOnly	autosomal dominant polycystic kidney disease	 Mtor 	 MTOR* 	 	0	Alliance Clustered	
HumanOnly	autosomal dominant polycystic kidney disease	 Lrp5 	 LRP5* 	 	0	Alliance Clustered	
HumanOnly	autosomal dominant polycystic kidney disease	 Pkd1 	 PKD1* 	 	0	Alliance Clustered	
HumanOnly	polycystic kidney disease 3	 Ganab 	 GANAB* 	 	0	Alliance Clustered	
HumanOnly	polycystic kidney disease 6	 Dnajb11 	 DNAJB11* 	 	0	Alliance Clustered	
HumanOnly	polycystic kidney disease 7	 Alg5 	 ALG5* 	 	0	Alliance Clustered	
TransgenesAndOtherMutations	autosomal dominant polycystic kidney disease	 	 	 Tg(HBB-Myc)#Cos 	1	 	
TransgenesAndOtherMutations	polycystic kidney disease 1	 	 	 Tg(Pkd1*)39Mtru 	2	 	
TransgenesAndOtherMutations	polycystic kidney disease 2	 	 	 Tg(CAG-PKD2)#Hwl 	1	 	
