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Mammalian Phenotype Ontology Annotations
Query Results - Summary
264 genotypes with 382 annotations displayed of selected term and subterms
Searched Term: abnormal cochlear inner hair cell morphology
Allelic Composition
(Genetic Background)
Annotated Term Reference
Acancmd/Acancmd
(involves: STOCK T tlow Itpr3tf)
abnormal cochlear IHC afferent innervation pattern J:553
abnormal cochlear inner hair cell morphology J:553
Adgrv1tm1Msat/Adgrv1tm1Msat
(involves: 129P2/OlaHsd * C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:122415
Adgrv1tm1Pwh/Adgrv1tm1Pwh
(involves: 129S1/Sv * C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:109595
cochlear inner hair cell degeneration J:109595
Apoetm1Unc/Apoetm1Unc
(B6.129P2-Apoetm1Unc/J)
cochlear inner hair cell degeneration J:101576
Atoh1trhl/Atoh1trhl
(B6.Cg-Atoh1trhl)
cochlear inner hair cell degeneration J:209662
decreased inner hair cell stereocilia number J:209662
Atp2b2Obv/Atp2b2+
(C3HeB/FeJ-Atp2b2Obv)
cochlear inner hair cell degeneration J:151733
Atp8b1tm1Nbf/Atp8b1tm1Nbf
(involves: 129S4/SvJae)
cochlear inner hair cell degeneration J:150079
Baiap2l2tm1b(EUCOMM)Hmgu/Baiap2l2tm1b(EUCOMM)Hmgu
(C57BL/6N-Baiap2l2tm1b(EUCOMM)Hmgu)
decreased inner hair cell stereocilia number J:305454
Barhl1tm1Xia/Barhl1tm1Xia
(involves: 129S7/SvEvBrd * C57BL/6J)
cochlear inner hair cell degeneration J:77122
Bhlhe22tm3.1(cre)Meg/Bhlhe22+
Gata3tm1Jfz/Gata3tm2Gsv
Gt(ROSA)26Sortm1(CAG-Mafb,-tdTomato)Good/Gt(ROSA)26Sor+

(involves: 129S1/Sv * 129S4/SvJae * 129X1/SvJ)
abnormal inner hair cell synaptic ribbon morphology J:207904
BsnGt(OST486029)Lex/BsnGt(OST486029)Lex
(Not Specified)
abnormal inner hair cell synaptic ribbon morphology J:167745
Bsntm1Gund/Bsntm1Gund
(Not Specified)
abnormal inner hair cell synaptic ribbon morphology J:167745, J:114223
absent active-zone-anchored inner hair cell synaptic ribbon J:114223
Cacna1dtm1Jst/Cacna1dtm1Jst
(involves: 129S7/SvEvBrd * C57BL/6J)
cochlear inner hair cell degeneration J:63515
Cacna1dtm1Jst/Cacna1dtm1Jst
(B6.129S7-Cacna1dtm1Jst)
abnormal cochlear IHC afferent innervation pattern J:113161, J:88205, J:108908
abnormal cochlear IHC efferent innervation pattern J:113161, J:88205, J:108908
abnormal inner hair cell synaptic ribbon morphology J:113161
absent active-zone-anchored inner hair cell synaptic ribbon J:108908
cochlear inner hair cell degeneration J:113161, J:85915, J:108908
Calcatm1Eme/Calcatm1Eme
(involves: 129S6/SvEvTac * C57BL/6)
abnormal cochlear IHC afferent innervation pattern J:117774
Casp3tm1Flv/Casp3tm1Flv
(B6.129S1-Casp3tm1Flv)
cochlear inner hair cell degeneration J:68122
Casp3tm1Kin/Casp3tm1Kin
(B6.129P2-Casp3tm1Kin)
cochlear inner hair cell degeneration J:69809
Cdc14aem1Tbf/Cdc14aem1Tbf
(involves: C57BL/6J)
fused inner hair cell stereocilia J:257652
Cdc14atm1a(EUCOMM)Hmgu/Cdc14atm1b(EUCOMM)Hmgu
(involves: C57BL/6N * FVB)
cochlear inner hair cell degeneration J:257652
fused inner hair cell stereocilia J:257652
Cdc14atm1b(EUCOMM)Hmgu/Cdc14atm1b(EUCOMM)Hmgu
(involves: C57BL/6N * FVB)
cochlear inner hair cell degeneration J:257652
fused inner hair cell stereocilia J:257652
Cdc14atm1d(EUCOMM)Hmgu/Cdc14atm1d(EUCOMM)Hmgu
(involves: C57BL/6N * FVB)
cochlear inner hair cell degeneration J:257652
fused inner hair cell stereocilia J:257652
Cdh2312J/Cdh2312J
(involves: C57BL/6J)
decreased cochlear inner hair cell number J:174758
Cdh2312J/Cdh2312J
(involves: C3H/HeJ * C57BL/6J)
cochlear inner hair cell degeneration J:183808
Cdh23ahl/Cdh23ahl
(C57BL/6NJ)
cochlear inner hair cell degeneration J:241137
Cdh23Jera/Cdh23Jera
(involves: C57BL/6)
abnormal inner hair cell stereociliary bundle morphology J:174130
Cdh23tm1.1Kjn/Cdh23tm1.1Kjn
(129S/Sv-Cdh23tm1.1Kjn/Kjn)
decreased cochlear inner hair cell number J:241137
Cdh23tm1.1Ugds/Cdh23tm1.1Ugds
Myo15atm1.1(cre)Ugds/Myo15a+

(involves: 129S1/SvImJ * C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:171218
decreased inner hair cell stereocilia number J:171218
short inner hair cell stereocilia J:171218
Cdh23v-2J/Cdh23+
Pcdh15av-3J/Pcdh15+

(C57BL/6J-Cdh23v-2J Pcdh15av-3J)
abnormal inner hair cell stereociliary bundle morphology J:95655
Cdh23v-2J/Cdh23v-2J
(B6(V)-Cdh23v-2J/J)
abnormal inner hair cell kinocilium morphology J:135991
abnormal inner hair cell stereociliary bundle morphology J:135991, J:66698
Cdh23v-Alb/Cdh23v-Alb
(involves: C3H/HeJ * C57BL/6)
abnormal inner hair cell stereociliary bundle morphology J:66698
Cdh23v-bus/Cdh23v-bus
(involves: KYF/MsIdr)
abnormal inner hair cell stereociliary bundle morphology J:34019
abnormal orientation of inner hair cell stereociliary bundles J:34019
Cdh23v/Cdh23+
(involves: BALB/cRl * 47BS/Rl * CBA/Ca)
decreased cochlear inner hair cell number J:134369
Cdh23v/Cdh23v
(involves: CBA/Ca)
abnormal inner hair cell stereociliary bundle morphology J:108877
Cdkn1atm1Tyj/Cdkn1atm1Tyj
Cdkn2dtm1Maro/Cdkn2dtm1Maro

(involves: 129P2/OlaHsd * 129S2/SvPas * 129X1/SvJ * C57BL/6 * CD-1)
abnormal cochlear inner hair cell morphology J:118337
decreased cochlear inner hair cell number J:118337
Cdkn1btm1Mlf/Cdkn1b+
(involves: 129S4/SvJaeSor * C57BL/6NHsd)
increased cochlear inner hair cell number J:53290
Cdkn1btm1Mlf/Cdkn1btm1Mlf
(involves: 129S4/SvJaeSor * C57BL/6NHsd)
increased cochlear inner hair cell number J:53290
Cdkn2dtm1Maro/Cdkn2dtm1Maro
(involves: 129X1/SvJ * C57BL/6 * CD-1)
cochlear inner hair cell degeneration J:83482
Cdkn2dtm1Maro/Cdkn2dtm1Maro
(involves: 129P2/OlaHsd * 129X1/SvJ * C57BL/6 * CD-1)
decreased cochlear inner hair cell number J:118337
Chd7tm2c(EUCOMM)Wtsi/Chd7+
Tg(Atoh1-cre)1Bfri/0

(involves: C57BL/6 * C57BL/6J * C57BL/6N * CBA)
cochlear inner hair cell degeneration J:314588
Chd7tm2c(EUCOMM)Wtsi/Chd7tm2c(EUCOMM)Wtsi
Tg(Atoh1-cre)1Bfri/0

(involves: C57BL/6 * C57BL/6J * C57BL/6N * CBA)
cochlear inner hair cell degeneration J:314588
Chd7Whi/Chd7+
(C3HeB/FeJ-Chd7Whi)
increased cochlear inner hair cell number J:99481
Chrna9tm1Bedv/Chrna9tm1Bedv
(either: CB.129S1-Chrna9tm1Bedv or (involves: 129S1/Sv) or (involves: 129S1/Sv * CBA/CaJ))
abnormal cochlear IHC efferent innervation pattern J:55406
Chrna10tm1Jbou/Chrna10tm1Jbou
(Not Specified)
abnormal cochlear IHC efferent innervation pattern J:130585
Cib2em1Xuzg/Cib2em1Xuzg
(C57BL/6-Cib2em1Xuzg)
abnormal inner hair cell kinocilium morphology J:280151
abnormal inner hair cell stereociliary bundle morphology J:280151
Cldn14tm1Tbf/Cldn14tm1Tbf
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6)
abnormal inner hair cell stereociliary bundle morphology J:85071
cochlear inner hair cell degeneration J:85071
Clic5jbg/Clic5jbg
(C3H/HeJ-Clic5jbg/J)
cochlear inner hair cell degeneration J:112741
Clrn1tm1.1Kuna/Clrn1tm1.1Kuna
(involves: C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:255408
absent cochlear inner hair cells J:150215
Clrn1tm1.1Kuna/Clrn1tm1.1Kuna
Tg(Atoh1-Clrn1)#Kuna/0

(involves: C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:255408
Clrn1tm1.1Ugpa/Clrn1tm1.1Ugpa
Myo15atm1.1(cre)Ugds/Myo15a+

(involves: 129S1/SvImJ * C57BL/6N)
abnormal cochlear IHC afferent innervation pattern J:265318
abnormal inner hair cell stereociliary bundle morphology J:265318
cochlear inner hair cell degeneration J:265318
Clrn1tm1.2Ugpa/Clrn1tm1.2Ugpa
(involves: BALB/c * C57BL/6 * C57BL/6N)
abnormal cochlear IHC afferent innervation pattern J:265318
abnormal inner hair cell stereociliary bundle morphology J:265318
Cm/+
(C3Sn.Cg-Cm/J)
increased cochlear inner hair cell number J:72108
Col11a1cho/Col11a1cho
(involves: C57BL/6Fr)
absent cochlear inner hair cells J:999
Crsl/Crsl+
(C3HeB/FeJ-Crsl/Ieg)
increased cochlear inner hair cell number J:99481
Cthrc1tm1Hssk/Cthrc1tm1Hssk
Vangl2Lp/Vangl2+

(involves: 129P2/OlaHsd * C57BL/6)
abnormal cochlear inner hair cell morphology J:140886
Cys1cpk/Cys1+
(B6(Cg)-Cys1cpk/J)
abnormal cochlear inner hair cell morphology J:1001
Dll1tm1Gos/Dll1+
Jag2tm1Grid/Jag2+

(involves: 129S1/Sv * 129S1/SvImJ * 129X1/SvJ * C57BL/6J)
increased cochlear inner hair cell number J:132241
Dll1tm1Gos/Dll1+
Jag2tm1Grid/Jag2tm1Grid

(involves: 129S1/Sv * 129S1/SvImJ * 129X1/SvJ * C57BL/6J)
increased cochlear inner hair cell number J:132241
Dll1tm1Gos/Dll1tm2Gos
Jag2tm1Grid/Jag2tm1Grid

(involves: 129S1/Sv * 129S1/SvImJ * 129X1/SvJ * C57BL/6J)
increased cochlear inner hair cell number J:132241
Dll1tm1Mjo/Dll1tm1Mjo
Foxg1tm1(cre)Skm/Foxg1+

(involves: 129P2/OlaHsd * C57BL/6J)
increased cochlear inner hair cell number J:107414
Dll1tm2Gos/Dll1+
Jag2tm1Grid/Jag2+

(involves: 129S1/Sv * 129S1/SvImJ * C57BL/6J)
increased cochlear inner hair cell number J:132241
Dvl1tm1Awb/Dvl1tm1Awb
Dvl2tm1Awb/Dvl2tm1Awb

(involves: 129S6/SvEvTac)
abnormal cochlear inner hair cell morphology J:108512
Dvl2tm1Awb/Dvl2tm1Awb
Vangl2Lp/Vangl2+

(involves: 129S6/SvEvTac * LPT/LeJ)
abnormal cochlear inner hair cell morphology J:108512
Elmod3em1Jili/Elmod3em1Jili
(involves: C57BL/6)
abnormal inner hair cell stereociliary bundle morphology J:293683
cochlear inner hair cell degeneration J:293683
fused inner hair cell stereocilia J:293683
short inner hair cell stereocilia J:293683
Emx2Pdo/Emx2+
(involves: BALB/c * C3H/HeN)
increased cochlear inner hair cell number J:82809, J:89093
Emx2Pdo/Emx2+
(involves: BALB/c)
abnormal cochlear inner hair cell morphology J:250208
Emx2tm1Pgr/Emx2+
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6)
increased cochlear inner hair cell number J:89093
Eps8l2tm1Wma/Eps8l2tm1Wma
(B6.129P2-Eps8l2tm1Wma)
decreased inner hair cell stereocilia number J:200669
Ercc6tm1Gvh/Ercc6tm1Gvh
(B6J.129P2-Ercc6tm1Gvh)
cochlear inner hair cell degeneration J:219993
Ercc8tm1Jhjh/Ercc8tm1Jhjh
(B6J.129P2-Ercc8tm1Jhjh)
cochlear inner hair cell degeneration J:219993
Espnje/Espn+
(involves: fancier's dancing mouse)
abnormal inner hair cell stereociliary bundle morphology J:1646
cochlear inner hair cell degeneration J:1646
Espnje/Espnje
(involves: fancier's dancing mouse)
cochlear inner hair cell degeneration J:7124
Esr2tm1Unc/Esr2tm1Unc
(involves: 129P2/OlaHsd * C57BL/6J)
abnormal cochlear IHC afferent innervation pattern J:108892
Eya1bor/Eya1bor
(involves: C3HeB/FeJ)
increased cochlear inner hair cell number J:140027
Eya1tm1Rilm/Eya1+
(involves: 129 * C3HeB/FeJ)
increased cochlear inner hair cell number J:140027
Eya1tm2Px/Eya1tm2Px
Tg(Atoh1-cre/Esr1*)14Fsh/0

(involves: FVB/N)
decreased cochlear inner hair cell number J:181471
Fgf20tm1.1Dor/Fgf20tm1.1Dor
(involves: 129X1/SvJ * C57BL/6J)
abnormal cochlear inner hair cell morphology J:184501
Fgfr1tm1Upir/Fgfr1tm1.1Upir
Foxg1tm1(cre)Skm/Foxg1+

(involves: 129P2/OlaHsd * ICR)
abnormal orientation of inner hair cell stereociliary bundles J:78879
increased cochlear inner hair cell number J:78879
Fgfr1tm6Jrt/Fgfr1tm6Jrt
(involves: 129S1/Sv * 129X1/SvJ * ICR)
abnormal orientation of inner hair cell stereociliary bundles J:78879
increased cochlear inner hair cell number J:78879
Fscn2ahl8/Fscn2ahl8
(DBA/2J)
decreased inner hair cell stereocilia number J:162868
Fzd3tm1Nat/Fzd3tm1Nat
Fzd6tm1Nat/Fzd6tm1Nat

(involves: 129S1/Sv * 129X1/SvJ * C57BL/6)
abnormal orientation of inner hair cell stereociliary bundles J:105752
Fzd4tm1Nat/Fzd4tm1Nat
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6)
cochlear inner hair cell degeneration J:107732
Gabra5tm1Twr/Gabra5tm1Twr
(involves: 129S7/SvEvBrd * C57BL/6)
cochlear inner hair cell degeneration J:112951
Gabrb2tm1.1Twr/Gabrb2tm1.1Twr
(involves: 129S7/SvEvBrd * C57BL/6)
cochlear inner hair cell degeneration J:112951
Gabrb3tm1Geh/Gabrb3tm1Geh
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6)
abnormal cochlear IHC afferent innervation pattern J:112951
cochlear inner hair cell degeneration J:112951
Gata3tm1Gsv/Gata3+
(involves: 129S7/SvEvBrd * C57BL/6 * FVB/N)
cochlear inner hair cell degeneration J:116235
Gfi1tm1(cre)Gan/Gfi1+
Rfx1tm1.1Wrth/Rfx1tm1.1Wrth
Rfx3tm2Wrth/Rfx3tm2Wrth

(involves: 129 * 129S7/SvEvBrd)
abnormal inner hair cell kinocilium morphology J:227631
cochlear inner hair cell degeneration J:227631
Gfi1tm1Sho/Gfi1tm1Sho
(involves: 129S1/Sv * C57BL/6J)
cochlear inner hair cell degeneration J:80025
Gfi1tm1Tmo/Gfi1tm1Tmo
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6)
abnormal cochlear inner hair cell morphology J:92833
abnormal inner hair cell stereociliary bundle morphology J:92833
short inner hair cell stereocilia J:92833
Gfi1tm3(Gfib1)Tmo/Gfi1tm3(Gfib1)Tmo
(involves: 129S1/Sv * 129X1/SvJ)
abnormal cochlear inner hair cell morphology J:116870
Gfi1tm4Tmo/Gfi1tm4Tmo
(involves: 129S1/Sv * 129X1/SvJ)
abnormal cochlear inner hair cell morphology J:116870
Gjb2tm1Ugds/Gjb2tm1Ugds
Tg(Otog-cre)1Ugds/0

(involves: 129P2/OlaHsd * C57BL/6)
abnormal cochlear inner hair cell morphology J:77823
abnormal inner hair cell synaptic ribbon morphology J:77823
Gjb6tm1Kwi/Gjb6tm1Kwi
(involves: 129P2/OlaHsd * C57BL/6)
cochlear inner hair cell degeneration J:80917, J:119517
Gpsm2tm1.2Fuma/Gpsm2tm1.2Fuma
(involves: C57BL/6 * C57BL/6NCrlj * CBA/JNCrlj)
abnormal inner hair cell stereociliary bundle morphology J:230725
short inner hair cell stereocilia J:230725
Gpx1tm1Ysh/Gpx1tm1Ysh
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6J)
cochlear inner hair cell degeneration J:113167
Grxcr1pi-3J/Grxcr1pi-3J
(BKS(Cg)-Grxcr1pi-3J/J)
short inner hair cell stereocilia J:156811
Grxcr1pi-Tg(Eno2-Gabrb3)0370Brll/Grxcr1pi-Tg(Eno2-Gabrb3)0370Brll
(involves: C3H * C57BL/6J)
abnormal cochlear inner hair cell morphology J:93174
abnormal inner hair cell stereociliary bundle morphology J:93174
Grxcr1pi/Grxcr1pi
(B6.C3-Grxcr1pi/J)
abnormal cochlear inner hair cell morphology J:94385
abnormal inner hair cell stereociliary bundle morphology J:94385
absent inner hair cell kinocilia J:94385
decreased inner hair cell stereocilia number J:94385
short inner hair cell stereocilia J:94385
Gt(ROSA)26Sorem1(ptxA)Btar/?
Tg(Atoh1-cre)1Bfri/?

(B6.Cg-Gt(ROSA)26Sorem1(ptxA)Btar Tg(Atoh1-cre)1Bfri/Btar)
abnormal inner hair cell stereociliary bundle morphology J:236519
short inner hair cell stereocilia J:236519
Gt(ROSA)26Sortm1(CAG-Mafb,-tdTomato)Good/Gt(ROSA)26Sor+
Tg(Neurog1-cre)1Jejo/0

(involves: 129S4/SvJae * C57BL/6J * SJL/J)
abnormal inner hair cell synaptic ribbon morphology J:207904
Hes1tm1Fgu/Hes1tm1Fgu
(involves: 129S1/Sv * 129X1/SvJ * CD-1)
increased cochlear inner hair cell number J:70081, J:64679
Hes1tm1Fgu/Hes1tm1Fgu
Hes5tm1Fgu/Hes5+

(involves: 129S1/Sv * 129X1/SvJ * CD-1)
increased cochlear inner hair cell number J:70081
Hes5tm1Fgu/Hes5tm1Fgu
(involves: 129S1/Sv * 129X1/SvJ * CD-1)
increased cochlear inner hair cell number J:70081
Hrrh/Hrrh
(RHJ/LeJ)
decreased cochlear inner hair cell number J:57947
Igf1rtm2.1Arge/Igf1rtm2.1Arge
(involves: 129 * C57BL/6)
abnormal cochlear inner hair cell morphology J:178908
abnormal inner hair cell kinocilium morphology J:178908
decreased cochlear inner hair cell number J:178908
Ildr1Gt(D178D03)Wrst/Ildr1Gt(D178D03)Wrst
(involves: 129S2/SvPas * Swiss Webster)
cochlear inner hair cell degeneration J:217755
Ildr1tm1(KOMP)Wtsi/Ildr1tm1(KOMP)Wtsi
(involves: C57BL/6N)
abnormal inner hair cell stereociliary bundle morphology J:221592
cochlear inner hair cell degeneration J:221592
Jag1Mhdahtu/Jag1+
(C3HeB/FeJ-Jag1Mhdahtu)
increased cochlear inner hair cell number J:72108
Jag1Slalom/Jag1+
(involves: BALB/c * C3H)
increased cochlear inner hair cell number J:67728
Jag1tm1Jlew/Jag1tm1Jlew
(involves: C57BL/6J)
increased cochlear inner hair cell number J:107414
Jag2tm1Grid/Jag2+
(involves: 129S1/Sv * C57BL/6J)
increased cochlear inner hair cell number J:53432
Jag2tm1Grid/Jag2tm1Grid
(involves: 129S1/Sv * C57BL/6J)
abnormal orientation of inner hair cell stereociliary bundles J:53432
increased cochlear inner hair cell number J:62727, J:53432
Jag2tm1Grid/Jag2tm1Grid
(involves: 129S1/Sv * 129S1/SvImJ * C57BL/6J)
increased cochlear inner hair cell number J:132241
Jag2tm1Grid/Jag2tm1Grid
Lfngtm1Grid/Lfng+

(involves: 129S1/Sv * C57BL/6J)
decreased cochlear inner hair cell number J:62727
Jag2tm1Grid/Jag2tm1Grid
Lfngtm1Grid/Lfngtm1Grid

(involves: 129S1/Sv * C57BL/6J)
decreased cochlear inner hair cell number J:62727
Kcne1pkr/Kcne1pkr
(C57BL/10J-Kcne1pkr)
absent cochlear inner hair cells J:64772
Kcnj10tm1Lst/Kcnj10tm1Lst
(involves: 129S1/Sv * C57BL/6J)
cochlear inner hair cell degeneration J:108878
Kcnma1tm1Ruth/Kcnma1tm1Ruth
(129-Kcnma1tm1Ruth)
abnormal cochlear IHC afferent innervation pattern J:109217
Kcnq1tm1Kpfe/Kcnq1tm1Kpfe
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6)
cochlear inner hair cell degeneration J:67873
Kcnq1tm2Kpfe/Kcnq1tm2Kpfe
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6 * FVB/N)
cochlear inner hair cell degeneration J:93197
Klc2em1Jgao/Klc2em1Jgao
(involves: C57BL/6J)
abnormal cochlear inner hair cell morphology J:345577
Klhl18lowf/Klhl18lowf
(C57BL/6N-Klhl18lowf)
abnormal inner hair cell stereociliary bundle morphology J:311444
Lhfpl5hscy/Lhfpl5hscy
(B6(MOR)-Lhfpl5hscy/J)
cochlear inner hair cell degeneration J:98396
Lhfpl5tm1Kjn/Lhfpl5tm1Kjn
(B6.129-Lhfpl5tm1Kjn/Kjn)
abnormal cochlear inner hair cell morphology J:125709
Lmx1absd/Lmx1absd
(involves: 129S5/SvEvBrd)
abnormal cochlear inner hair cell morphology J:194385
Lmx1amtl/Lmx1amtl
(involves: 129S5/SvEvBrd)
abnormal cochlear inner hair cell morphology J:194385
Lrrn1em1Dri/Lrrn1em1Dri
(involves: CD-1)
increased cochlear inner hair cell number J:344891
Lrrn1em1Dri/Lrrn1em1Dri
Notch1tm2Agt/Notch1+

(involves: 129/Sv * C57BL/6J * CD-1)
abnormal cochlear inner hair cell morphology J:344891
increased cochlear inner hair cell number J:344891
Lrrn1em2Dri/Lrrn1em2Dri
(involves: C57BL/6J)
increased cochlear inner hair cell number J:344891
Lrrn1em3Dri/Lrrn1em3Dri
(involves: C57BL/6J)
increased cochlear inner hair cell number J:344891
m12Anu/m12Anu
(Not Specified)
abnormal cochlear inner hair cell morphology J:207337
Mafbtm1.1Good/Mafbtm1Jeng
Tg(Neurog1-cre)1Jejo/0

(involves: 129P2/OlaHsd * 129S4/SvJae * C57BL/6 * SJL)
abnormal inner hair cell synaptic ribbon morphology J:207904
Map3k1tm1Yxia/Map3k1tm1Yxia
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6J)
decreased cochlear inner hair cell number J:226897
Marveld2tm1.1Sria/Marveld2tm1.1Sria
(involves: 129X1/SvJ * C57BL/6J)
cochlear inner hair cell degeneration J:201580
Marveld2tm1Sats/Marveld2tm1Sats
(B6.Cg-Marveld2tm1Sats)
cochlear inner hair cell degeneration J:261357
Mctp1dwnd/Nr2f1tm1.1(KOMP)Mbp
(involves: C57BL/6J * C57BL/6NJ * C57BL/10SnJ)
abnormal cochlear inner hair cell morphology J:264553
Mctp1dwnd/Mctp1dwnd
(B6.B10Sn-Mctp1dwnd/Kjn)
abnormal cochlear inner hair cell morphology J:264553
MkksGt(OST367255)Lex/MkksGt(OST367255)Lex
(involves: 129S5/SvEvBrd * C57BL/6J)
abnormal inner hair cell kinocilium location or orientation J:102697
Mob1atm1.2Asuz/Mob1a+
Mob1bGt(CC0690)Wtsi/Mob1bGt(CC0690)Wtsi

(involves: 129P2/OlaHsd * C57BL/6)
abnormal orientation of inner hair cell stereociliary bundles J:193981
Mob1atm1.2Asuz/Mob1atm1.2Asuz
Mob1bGt(CC0690)Wtsi/Mob1b+

(involves: 129P2/OlaHsd * C57BL/6)
abnormal orientation of inner hair cell stereociliary bundles J:193981
Msrb3tm1Hyk/Msrb3tm1Hyk
(involves: 129 * C57BL/6)
cochlear inner hair cell degeneration J:206322
Myo3atm1.1Mckg/Myo3atm1.1Mckg
(C57BL/6-Myo3atm1.1Mckg)
cochlear inner hair cell degeneration J:166812
Myo6chl/Myo6chl
(involves: C57BL/6JAnu)
abnormal orientation of inner hair cell stereociliary bundles J:196601
decreased inner hair cell stereocilia number J:196601
Myo6em1Bcgen/Myo6em1Bcgen
(involves: C57BL/6J * CBA/CaJ)
abnormal inner hair cell stereociliary bundle morphology J:288210
fused inner hair cell stereocilia J:288210
Myo6ksv/Myo6ksv
(B6JJcl.Cg-Myo6ksv)
abnormal inner hair cell stereociliary bundle morphology J:245687
fused inner hair cell stereocilia J:245687
Myo6Mhdatlc/Myo6+
(C3HeB/FeJ-Myo6Mhdatlc/Ieg)
cochlear inner hair cell degeneration J:64900
Myo6rsv/Myo6rsv
(involves: C57BL/6Slc)
abnormal inner hair cell stereociliary bundle morphology J:261136
cochlear inner hair cell degeneration J:261136
fused inner hair cell stereocilia J:261136
Myo6sv/Myo6sv
(involves: B10.HA/(33NX)Sn * C57BL/6J)
cochlear inner hair cell degeneration J:29898
fused inner hair cell stereocilia J:58030
Myo7a4626SB/Myo7a4626SB
(involves: BALB/cRl)
abnormal inner hair cell stereociliary bundle morphology J:135991
Myo7admbo2/Myo7admbo2
(involves: C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:195666
decreased inner hair cell stereocilia number J:195666
Myo7aewaso/Myo7aewaso
(involves: C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:195666
abnormal orientation of inner hair cell stereociliary bundles J:195666
decreased inner hair cell stereocilia number J:195666
fused inner hair cell stereocilia J:195666
Myo7aHdb/Myo7a4626SB
(involves: BALB/c * 47BS/Rl * C3HeB/FeJ * CBA/Ca)
abnormal inner hair cell stereociliary bundle morphology J:93998
fused inner hair cell stereocilia J:93998
Myo7aHdb/Myo7a+
(C3HeB/FeJ-Myo7aHdb/Ieg)
abnormal inner hair cell stereociliary bundle morphology J:93998
fused inner hair cell stereocilia J:93998
Myo7aHdb/Myo7aHdb
(C3HeB/FeJ-Myo7aHdb/Ieg)
abnormal inner hair cell stereociliary bundle morphology J:93998
decreased inner hair cell stereocilia number J:93998
fused inner hair cell stereocilia J:93998
Myo15ash2/Myo15ash2
(STOCK Myo15ash2/J)
abnormal inner hair cell stereociliary bundle morphology J:226820
short inner hair cell stereocilia J:226820
Myo15atm1.1(cre)Ugds/Myo15a+
Ush1gtm1.1Ugds/Ush1gtm1.1Ugds

(involves: 129S1/SvImJ * C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:171218
decreased inner hair cell stereocilia number J:171218
short inner hair cell stereocilia J:171218
Ndptm1Wbrg/Y
(involves: 129/Sv * 129P2/OlaHsd * C57BL/6 * CBA/CaJ * CD-1)
cochlear inner hair cell degeneration J:77024
Nfkb1tm1Bal/Nfkb1tm1Bal
(B6;129P-Nfkb1tm1Bal/J)
abnormal cochlear inner hair cell morphology J:107245
Nogtm1Amc/Nogtm1Amc
(involves: 129S1/Sv * C57BL/6J * FVB/N)
increased cochlear inner hair cell number J:156945
Notch1tm1Grid/Notch1tm2Rko
Foxg1tm1(cre)Skm/Foxg1+

(involves: 129 * C57BL/6J * Swiss Webster)
increased cochlear inner hair cell number J:132241
Nptnpitch/Nptnpitch
(involves: C3H * C57BL/6J)
abnormal inner hair cell synaptic ribbon morphology J:228717
Nr2f1tm1Mjts/Nr2f1tm1Mjts
(involves: 129S7/SvEvBrd)
abnormal orientation of inner hair cell stereociliary bundles J:112461
increased cochlear inner hair cell number J:112461
Ntrk3tm1Bbd/Ntrk3tm1Bbd
(involves: 129S2/SvPas * C57BL/6)
abnormal cochlear IHC afferent innervation pattern J:29245
Ocmtm1.1Ddsi/Ocmtm1.1Ddsi
(involves: 129X1/SvJ * FVB/N)
cochlear inner hair cell degeneration J:231626
Osbpl2em1Cya/Osbpl2em1Cya
(C57BL/6-Osbpl2em1Cya)
abnormal inner hair cell kinocilium morphology J:324115
Otoftm1Ugds/Otoftm1Ugds
(involves: 129S2/SvPas * C57BL/6)
abnormal cochlear inner hair cell morphology J:116097
abnormal inner hair cell synaptic ribbon morphology J:116097
P2rx2em1Xzl/P2rx2+
(CBA/J-P2rx2em1Xzl)
abnormal cochlear inner hair cell morphology J:315007
abnormal inner hair cell synaptic ribbon morphology J:315007
Pax8tm1Pgr/Pax8tm1Pgr
(either: (involves: 129S1/Sv * 129X1/SvJ) or (involves: 129S1/Sv * 129X1/SvJ * C57BL/6))
abnormal cochlear IHC efferent innervation pattern J:119450
abnormal inner hair cell synaptic ribbon morphology J:119450
Pcdh15av-2J/Pcdh15av-2J
(B6C3Fe a/a-Pcdh15av-2J/J)
abnormal inner hair cell stereociliary bundle morphology J:106625
Pcdh15av-3J/Pcdh15av-3J
(C57BL/6J-Pcdh15av-3J/J)
abnormal inner hair cell kinocilium morphology J:135991
abnormal inner hair cell stereociliary bundle morphology J:106625, J:135991
Pcdh15av-5J/Pcdh15av-5J
(C57BL/6J-Pcdh15av-5J/J)
abnormal inner hair cell stereociliary bundle morphology J:97048
Pcdh15av-6J/Pcdh15av-6J
(B6(129P2)-Pcdh15av-6J)
cochlear inner hair cell degeneration J:111661
Pcdh15av-J/Pcdh15av-J
(B6.BKS-Pcdh15av-J/J)
abnormal inner hair cell stereociliary bundle morphology J:106625
abnormal orientation of inner hair cell stereociliary bundles J:106625
Pcdh15av-Tg2742Rpw/Pcdh15av-Tg2742Rpw
(FVB/N-Pcdh15av-Tg2742Rpw)
abnormal inner hair cell stereociliary bundle morphology J:66738
Pcdh15roda/Pcdh15roda
(BALB/c-Pcdh15roda)
abnormal inner hair cell kinocilium location or orientation J:220658
decreased inner hair cell stereocilia number J:220658
fused inner hair cell stereocilia J:220658
Pcdh15tm1.1Ugds/Pcdh15tm1.1Ugds
Myo15atm1.1(cre)Ugds/Myo15a+

(involves: 129S1/SvImJ * C57BL/6J)
decreased inner hair cell stereocilia number J:209275
short inner hair cell stereocilia J:209275
Pcdh15tm2.1Mll/Pcdh15tm2.1Mll
(involves: 129P2/OlaHsd * 129S/SvEv * C57BL/6 * SJL)
abnormal inner hair cell kinocilium location or orientation J:171627
Pls1tm1Fri/Pls1tm1Fri
(B6.129-Pls1tm1Fri)
abnormal inner hair cell stereociliary bundle morphology J:216416
decreased inner hair cell stereocilia number J:216416
short inner hair cell stereocilia J:216416
Pou4f3ddl/Pou4f3ddl
(C57BL/6J-Pou4f3ddl/J)
cochlear inner hair cell degeneration J:92833
Pou4f3tm1.1(HBEGF)Rubel/Pou4f3+
(involves: 129S4/SvJaeSor * C57BL/6J * CBA/J)
absent cochlear inner hair cells J:240454
Pou4f3tm1Rsd/Pou4f3tm1Rsd
(involves: 129S4/SvJae)
abnormal cochlear inner hair cell morphology J:33502
absent inner hair cell stereocilia J:33502
Pou4f3tm1Xia/Pou4f3tm1Xia
(involves: 129S7/SvEvBrd * C57BL/6J)
abnormal cochlear inner hair cell morphology J:92833
absent inner hair cell stereocilia J:92833
cochlear inner hair cell degeneration J:42478, J:92833
Psaptm1Suz/Psaptm1Suz
(involves: 129P2/OlaHsd * FVB)
abnormal cochlear IHC afferent innervation pattern J:116349
abnormal cochlear IHC efferent innervation pattern J:116349
abnormal cochlear inner hair cell morphology J:116349
Ptk7Gt(Betageo)1Matl/Ptk7Gt(Betageo)1Matl
(involves: 129P2/Ola)
abnormal cochlear inner hair cell morphology J:91298
abnormal orientation of inner hair cell stereociliary bundles J:91298
increased cochlear inner hair cell number J:91298
Ptprqtm1Bow/Ptprqtm1Bow
(involves: 129/Sv * C57BL/6)
abnormal inner hair cell stereociliary bundle morphology J:85926
abnormal orientation of inner hair cell stereociliary bundles J:85926
decreased inner hair cell stereocilia number J:85926
fused inner hair cell stereocilia J:85926
Ptprqtm2Bow/Ptprqtm2Bow
(involves: 129 * C57BL/6)
abnormal inner hair cell stereociliary bundle morphology J:85926
abnormal orientation of inner hair cell stereociliary bundles J:85926
decreased inner hair cell stereocilia number J:85926
fused inner hair cell stereocilia J:85926
Rb1tm1Tyj/Rb1tm1Tyj
Tg(Rb1)1Blg/0

(involves: 129S2/SvPas * C57BL/6)
increased cochlear inner hair cell number J:98518
Rb1tm2Brn/Rb1tm2Brn
Tg(Col1a1-cre)1Bek/0

(involves: 129 * CD-1)
increased cochlear inner hair cell number J:96345
Rb1tm2Brn/Rb1tm2Brn
Tg(Pou4f3-cre)1Devet/0

(involves: 129 * 129S/SvEv)
increased cochlear inner hair cell number J:109453
rda/rda
(C57BL/6J-rda/JKjn)
abnormal inner hair cell stereociliary bundle morphology J:187273
fused inner hair cell stereocilia J:187273
Rdxtm1Sts/Rdxtm1Sts
(involves: 129S4/SvJae * C57BL/6)
abnormal inner hair cell stereociliary bundle morphology J:124151
fused inner hair cell stereocilia J:124151
short inner hair cell stereocilia J:124151
Resttm1.1Bban/Rest+
Gfi1tm1(cre)Gan/Gfi1+

(involves: 129S4/SvJaeSor * 129S7/SvEvBrd * FVB/N)
cochlear inner hair cell degeneration J:265659
Resttm1.2Bban/Rest+
(involves: 129S4/SvJaeSor * FVB/N)
cochlear inner hair cell degeneration J:265659
Ripor2tm1(KOMP)Vlcg/Ripor2tm1(KOMP)Vlcg
(C57BL/6-Ripor2tm1(KOMP)Vlcg)
abnormal inner hair cell stereociliary bundle morphology J:234083
decreased inner hair cell stereocilia number J:234083
Rr388em1Jdai/Rr388em1Jdai
(Not Specified)
decreased cochlear inner hair cell number J:333396
Rr388em1Jdai/Rr388em1Jdai
Rr397em1Zyliu/Rr397em1Zyliu

(Not Specified)
decreased cochlear inner hair cell number J:333396
S1pr2tm1Jch/S1pr2tm1Jch
S1pr3tm1Jch/S1pr3tm1Jch

(involves: 129S1/Sv * 129X1/SvJ * C57BL/6N)
cochlear inner hair cell degeneration J:118369
Scarb2tm1Psa/Scarb2tm1Psa
(involves: 129P2/OlaHsd * C57BL/6J)
cochlear inner hair cell degeneration J:82474
Scribm51206BHubr/Scrib+
Sec24bkrb/Sec24bkrb

(involves: C57BL/6 * FVB/N)
abnormal cochlear inner hair cell morphology J:158680
Scribm51206BHubr/Scribm51206BHubr
(involves: C57BL/6 * FVB/N)
abnormal cochlear inner hair cell morphology J:158680
Sec24bkrb/Sec24bkrb
(involves: C57BL/6 * FVB/N)
abnormal cochlear inner hair cell morphology J:158680
Sec24bY613X/Sec24bY613X
(involves: C3H/He * C57BL/6)
abnormal orientation of inner hair cell stereociliary bundles J:158452
Six1Cwe/Six1+
(C3HeB/FeJ-Six1Cwe)
increased cochlear inner hair cell number J:149467
Six1Cwe/Six1Cwe
(C3HeB/FeJ-Six1Cwe)
decreased cochlear inner hair cell number J:149467
Slc1a3tm1Kta/Slc1a3tm1Kta
(involves: 129P2/OlaHsd)
cochlear inner hair cell degeneration J:99715
Slc4a7tm1Krtz/Slc4a7tm1Krtz
(involves: 129S5/SvEvBrd * C57BL/6)
cochlear inner hair cell degeneration J:102942, J:86635
Slc7a14em1Jin/Slc7a14em1Jin
(C57BL/6J-Slc7a14em1Jin)
absent cochlear inner hair cells J:323825
absent inner hair cell stereocilia J:323825
decreased inner hair cell stereocilia number J:323825
fused inner hair cell stereocilia J:323825
Slc7a14em1Jqu/Slc7a14em1Jqu
(C57BL/6-Slc7a14em1Jqu)
absent inner hair cell stereocilia J:323825
decreased inner hair cell stereocilia number J:323825
fused inner hair cell stereocilia J:323825
Slc12a2tm1Ges/Slc12a2tm1Ges
(Not Specified)
decreased cochlear inner hair cell number J:57651
Slc12a2tm2Bhk/Slc12a2tm2Bhk
(involves: 129P2/OlaHsd * C57BL/6J * DBA/2J)
abnormal cochlear inner hair cell morphology J:106383
Slc12a6tm1Tjj/Slc12a6tm1Tjj
(involves: 129/Sv * C57BL/6)
cochlear inner hair cell degeneration J:86183
Slc17a8tm1Edw/Slc17a8tm1Edw
(involves: 129P2/OlaHsd * C57BL/6)
abnormal inner hair cell synaptic ribbon morphology J:132704
Slc17a8tm1Selm/Slc17a8tm1Selm
(involves: 129/Sv * C57BL/6)
abnormal cochlear IHC efferent innervation pattern J:139493
abnormal inner hair cell synaptic ribbon morphology J:139493
decreased cochlear inner hair cell number J:139493
Slc19a2tm1Ejn/Slc19a2tm1Ejn
(involves: 129S4/SvJae * 129S6/SvEvTac)
cochlear inner hair cell degeneration J:118928
Slc26a4em1Jgao/Slc26a4em1Jgao
(involves: CBA/CaJ)
fused inner hair cell stereocilia J:291230
Slc26a4loop/Slc26a4loop
(C3HeB/FeJ-Slc26a4loop)
cochlear inner hair cell degeneration J:216847
Slc26a4tm1.1Dontu/Slc26a4tm1.1Dontu
(involves: 129S1/Sv * 129X1/SvJ * C57BL/6)
cochlear inner hair cell degeneration J:175861
Slc26a4tm1Egr/Slc26a4tm1Egr
(either: (involves: 129S6/SvEvTac) or (involves: 129S6/SvEvTac * Black Swiss))
cochlear inner hair cell degeneration J:67072
fused inner hair cell stereocilia J:67072
Slc26a5tm1Jnz/Slc26a5+
(involves: 129S7/SvEvBrd * C57BL/6J)
cochlear inner hair cell degeneration J:79029
Slc26a5tm1Jnz/Slc26a5tm1Jnz
(involves: 129S7/SvEvBrd * C57BL/6J)
cochlear inner hair cell degeneration J:79029, J:91680
Slc44a2tm1.2Tec/Slc44a2tm1.2Tec
(FVB.129(Cg)-Slc44a2tm1.2Tec)
decreased cochlear inner hair cell number J:239440
Slitrk6tm1.1Jaru/Slitrk6tm1.1Jaru
(B6.129P2-Slitrk6tm1.1Jaru)
abnormal cochlear IHC afferent innervation pattern J:155405
abnormal cochlear IHC efferent innervation pattern J:155405
Sod1tm1Cep/Sod1+
(involves: 129S1/Sv * 129X1/SvJ * CD-1)
cochlear inner hair cell degeneration J:118910
Sod1tm1Cep/Sod1tm1Cep
(involves: 129S1/Sv * 129X1/SvJ * CD-1)
cochlear inner hair cell degeneration J:118910, J:57435
Srrm4bv/Srrm4bv
(involves: 129)
abnormal cochlear inner hair cell morphology J:31165
cochlear inner hair cell degeneration J:31165
Srrm4bv/Srrm4bv
(Not Specified)
abnormal cochlear inner hair cell morphology J:6106, J:13866
absent cochlear inner hair cells J:6106
cochlear inner hair cell degeneration J:39922
decreased cochlear inner hair cell number J:193641
Synj2mozart/Synj2mozart
(C57BL/6-Synj2mozart)
cochlear inner hair cell degeneration J:171701
fused inner hair cell stereocilia J:171701
Tg(CAG-Diap3)924Lesp/0
(FVB/NJ-Tg(CAG-Diap3)924Lesp)
abnormal inner hair cell stereociliary bundle morphology J:193237
abnormal inner hair cell synaptic ribbon morphology J:193237
decreased inner hair cell stereocilia number J:193237
Tg(CAG-Diaph3)771Lesp/0
(FVB/NJ-Tg(CAG-Diaph3)771Lesp)
abnormal inner hair cell stereociliary bundle morphology J:193237
abnormal inner hair cell synaptic ribbon morphology J:193237
decreased inner hair cell stereocilia number J:193237
Tg(Pax2-cre)1Akg/0
Vangl2tm1.2Mdea/Vangl2tm2.1Mdea

(involves: 129S6/SvEvTac * C57BL/6 * SJL)
abnormal orientation of inner hair cell stereociliary bundles J:201321
Tg(Tek-cre)1Ywa/Tg(Tek-cre)1Ywa
(involves: C57BL/6 * SJL)
abnormal cochlear inner hair cell morphology J:242313
abnormal inner hair cell stereociliary bundle morphology J:242313
Tmc1baringo/Tmc1baringo
(involves: C57BL/6)
cochlear inner hair cell degeneration J:181985
Tmc1nice/Tmc1nice
(involves: C57BL/6)
cochlear inner hair cell degeneration J:181985
Tmc1stitch/Tmc1stitch
(involves: C57BL/6)
cochlear inner hair cell degeneration J:181985
Tmc1tm1.1Ajg/Tmc1tm1.1Ajg
(B6.129-Tmc1tm1.1Ajg)
cochlear inner hair cell degeneration J:184419
Tmc1tm1.1Ajg/Tmc1tm1.1Ajg
Tmc2tm1.1Ajg/Tmc2tm1.1Ajg

(B6.129-Tmc2tm1.1Ajg Tmc1tm1.1Ajg)
cochlear inner hair cell degeneration J:184419
Tmem43em1Cby/Tmem43+
(involves: 129 * C57BL/6J)
decreased cochlear inner hair cell number J:314357
Tmprss3m1Ingm/Tmprss3m1Ingm
(C3HeB/FeJ-Tmprss3m1Ingm)
abnormal inner hair cell stereociliary bundle morphology J:172676
absent cochlear inner hair cells J:172676
cochlear inner hair cell degeneration J:172676
Tmtc4tm1(KOMP)Vlcg/Tmtc4tm1(KOMP)Vlcg
(involves: C57BL/6J * C57BL/6NTac)
cochlear inner hair cell degeneration J:268046
Tomtm1Btlr/Tomtm1Btlr
(C57BL/6J-Tomtm1Btlr)
cochlear inner hair cell degeneration J:137493
Tprnem1Pghu/Tprnem1Pghu
(B6.Cg-Tprnem1Pghu)
cochlear inner hair cell degeneration J:240563
decreased inner hair cell stereocilia number J:240563
Triobptm1Tbf/Triobptm1Tbf
(C57BL/6-Triobptm1Tbf)
abnormal inner hair cell stereociliary bundle morphology J:167947
fused inner hair cell stereocilia J:167947
Tubtub/Tubtub
(B6(AU)-Tubtub/J)
cochlear inner hair cell degeneration J:121993
Ush1cdfcr-2J/Ush1cdfcr-2J
(B6;129S4)
abnormal inner hair cell stereociliary bundle morphology J:85400
cochlear inner hair cell degeneration J:85400
Ush1cdfcr/Ush1cdfcr
(involves: BALB/cByJ)
abnormal inner hair cell stereociliary bundle morphology J:85400
cochlear inner hair cell degeneration J:85400
Ush1ctm1.1Ugds/Ush1ctm1.1Ugds
(involves: 129S2/SvPas)
abnormal inner hair cell stereociliary bundle morphology J:135991
Ush1ctm1Xzl/Ush1ctm1Xzl
(B6.129-Ush1ctm1Xzl)
abnormal orientation of inner hair cell stereociliary bundles J:158047
Ush1gjs/Ush1gjs
(B6.A-Ush1gjs/J)
abnormal inner hair cell stereociliary bundle morphology J:135991
Ush1gtm1.2Ugds/Ush1gtm1.2Ugds
(involves: 129S1/SvImJ * BALB/c * C57BL/6 * C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:171218
Usp53mbo/Usp53mbo
(involves: BALB/cByJ * C57BL/6J)
cochlear inner hair cell degeneration J:227841
Vangl1Gt(XL802)Byg/Vangl1+
Vangl2Lp/Vangl2+

(involves: 129P2/OlaHsd * C57BL/6J * LPT/LeJ)
abnormal orientation of inner hair cell stereociliary bundles J:132697
Vangl1Gt(XL802)Byg/Vangl1Gt(XL802)Byg
Vangl2Lp/Vangl2+

(involves: 129P2/OlaHsd * A)
abnormal cochlear inner hair cell morphology J:162640
Vangl1Gt(XL802)Byg/Vangl1Gt(XL802)Byg
Vangl2tm1.2Yy/Vangl2tm1.2Yy

(involves: 129P2/OlaHsd * C57BL/6 * CBA)
abnormal cochlear inner hair cell morphology J:162640
Vangl2Lp/Vangl2Lp
(LPT/LeJ)
abnormal orientation of inner hair cell stereociliary bundles J:132697
Vangl2Lp/Vangl2Lp
(involves: A)
abnormal cochlear inner hair cell morphology J:162640
Vangl2Lp/Vangl2tm1.2Mdea
(involves: 129S/Sv * C57BL/6 * FVB/N * LPT/LeJ * SJL)
abnormal cochlear inner hair cell morphology J:185311
Vangl2tm1.2Mdea/Vangl2tm1.2Mdea
(B6NCrl.129S6(Cg)-Vangl2tm1.2Mdea)
abnormal cochlear inner hair cell morphology J:185311
Vangl2tm1.2Yy/Vangl2tm1.2Yy
(involves: C57BL/6 * CBA)
abnormal cochlear inner hair cell morphology J:162640
Vangl2tm2.2Mdea/Vangl2tm2.2Mdea
(involves: 129S6/SvEvTac * C57BL/6 * SJL)
abnormal orientation of inner hair cell stereociliary bundles J:201321
Wbp2tm2a(EUCOMM)Wtsi/Wbp2tm2a(EUCOMM)Wtsi
(involves: C57BL/6N * C57BL/6NTac)
abnormal cochlear IHC afferent innervation pattern J:229594
Wfs1tm1.1Bedel/Wfs1tm1.1Bedel
(involves: C57BL/6N)
fused inner hair cell stereocilia J:342760
Wfs1tm1Koks/Wfs1tm1Koks
(involves: 129S6/SvEvTac * C57BL/6J)
abnormal inner hair cell stereociliary bundle morphology J:342760
Whrnwi/Whrn+
(involves: C57BL/6J * STOCK a Tyrp1b Myo5ad Oca2p Ednrbs)
abnormal cochlear inner hair cell morphology J:77939
short inner hair cell stereocilia J:77939
Whrnwi/Whrnwi
(involves: C57BL/6J * STOCK a Tyrp1b Myo5ad Oca2p Ednrbs)
abnormal cochlear inner hair cell morphology J:48657
cochlear inner hair cell degeneration J:77939, J:48657
short inner hair cell stereocilia J:122600, J:77939, J:48657
Whrnwi/Whrnwi
(involves: STOCK a Tyrp1b Myo5ad Oca2p Ednrbs)
short inner hair cell stereocilia J:235390

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Mouse Genome Database (MGD), Gene Expression Database (GXD), Mouse Models of Human Cancer database (MMHCdb) (formerly Mouse Tumor Biology (MTB)), Gene Ontology (GO)
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last database update
04/09/2024
MGI 6.23
The Jackson Laboratory