Automated description from the Alliance of Genome Resources
Predicted to have several functions, including biotin binding activity; biotin-[propionyl-CoA-carboxylase (ATP-hydrolyzing)] ligase activity; and protein homodimerization activity. Predicted to be involved in cell population proliferation; histone biotinylation; and response to biotin. Localizes to the mitochondrion. Human ortholog(s) of this gene implicated in holocarboxylase synthetase deficiency. Is expressed in several structures, including genitourinary system; gut; nervous system; sensory organ; and thymus. Orthologous to human HLCS (holocarboxylase synthetase).