Automated description from the Alliance of Genome Resources
Predicted to have metalloendopeptidase activity. Involved in cristae formation; mitochondrial fusion; and mitochondrial protein processing. Localizes to the m-AAA complex. Human ortholog(s) of this gene implicated in spastic ataxia; spastic ataxia 5; and spinocerebellar ataxia type 28. Orthologous to several human genes including AFG3L2 (AFG3 like matrix AAA peptidase subunit 2).