Automated description from the Alliance of Genome Resources
Predicted to contribute to methylcrotonoyl-CoA carboxylase activity. Localizes to the mitochondrial inner membrane. Human ortholog(s) of this gene implicated in 3-Methylcrotonyl-CoA carboxylase 1 deficiency. Is expressed in several structures, including alimentary system; genitourinary system; heart; nervous system; and sensory organ. Orthologous to human MCCC1 (methylcrotonoyl-CoA carboxylase 1).