Automated description from the Alliance of Genome Resources
Predicted to have metallopeptidase activity. Involved in several processes, including cristae formation; nervous system development; and protein maturation. Localizes to the m-AAA complex. Used to study spinocerebellar ataxia type 28. Human ortholog(s) of this gene implicated in spastic ataxia; spastic ataxia 5; and spinocerebellar ataxia type 28. Orthologous to human AFG3L2 (AFG3 like matrix AAA peptidase subunit 2).