Automated description from the Alliance of Genome Resources (Release 3.1.1)
Predicted to have metalloendopeptidase activity. Involved in several processes, including mitochondrion organization; nervous system development; and protein processing. Localizes to m-AAA complex. Is expressed in brain. Used to study spinocerebellar ataxia type 28. Human ortholog(s) of this gene implicated in spastic ataxia; spastic ataxia 5; and spinocerebellar ataxia type 28. Orthologous to human AFG3L2 (AFG3 like matrix AAA peptidase subunit 2).