Excel File Text File All mouse models of kidney disease with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      autosomal dominant polycystic kidney disease Pkd2tm1.1Gwu/Pkd2tm1.1Gwu
Tg(Vil1-cre)997Gum/0		 involves: C57BL/6 * C57BL/6J * SJL J:265516 View
autosomal dominant pseudohypoaldosteronism type 1 Nr3c2tm1Gsc/Nr3c2tm1Gsc involves: 129P2/OlaHsd * C57BL/6 J:77285 View
autosomal recessive polycystic kidney disease Pkhd1tm1.1Ggg/Pkhd1tm1.1Ggg involves: 129S/SvEv * 129S4/SvJae * C57BL/6 J:125113 View
autosomal recessive polycystic kidney disease Pkhd1tm1Cjwa/Pkhd1tm1Cjwa involves: 129S6/SvEvTac * FVB/N J:140302 View
autosomal recessive polycystic kidney disease Pkhd1tm1Gwu/Pkhd1tm1Gwu involves: C57BL/6 J:167782 View
autosomal recessive polycystic kidney disease Pkhd1tm1Gwu/Pkhd1tm1Gwu Not Specified J:143394 View
autosomal recessive polycystic kidney disease Pkhd1tm1Sswi/Pkhd1tm1Sswi B6.Cg-Pkhd1tm1Sswi J:186064 View
autosomal recessive polycystic kidney disease Pkhd1tm2Cjwa/Pkhd1tm2Cjwa either: B6.129(Cg)-Pkhd1tm2Cjwa or C.129(Cg)-Pkhd1tm2Cjwa J:187735 View
Bartter disease type 1 Slc12a1tm1Tkh/Slc12a1tm1Tkh involves: 129S6/SvEvTac J:62224 View
Bartter disease type 1 Slc12a1urehr3/Slc12a1urehr3 involves: C3HeB/FeJ J:159994 View
Bartter disease type 2 Kcnj1tm1Ges/Kcnj1tm1Ges involves: 129X1/SvJ * Black Swiss J:79354 View
Bartter disease type 3 Clcnkbem1Haca/Clcnkbem1Haca C57BL/6-Clcnkbem1Haca J:259681 View
Bartter disease type 4a Bsndtm1.1Suc/Bsndtm1.1Suc involves: 129S4/SvJae * C57BL/6 J:175265 View
Bartter disease type 4a Bsndtm1Tjj/Bsndtm1Tjj
Tg(Sox10-cre)1Wdr/0		 involves: 129/Sv * 129X1/SvJ * C57BL/6 J:143314 View
cystinuria Slc3a1m1Crl/Slc3a1m1Crl 129S2/SvPasCrl J:219017 View
cystinuria Slc3a1pbl/Slc3a1pbl C3HeB/FeJ-Slc3a1pbl J:85461 View
cystinuria Slc3a1pbl/Slc3a1pbl involves: C3HeB/FeJ * MRL/MpJ J:85461 View
cystinuria Slc3a1tm1Jat/Slc3a1tm1Jat involves: 129 * C57BL/6 J:254981, J:254803 View
cystinuria Slc7a9tm1Nune/Slc7a9+ involves: 129P2/OlaHsd * C57BL/6J J:85462 View
cystinuria Slc7a9tm1Nune/Slc7a9tm1Nune involves: 129P2/OlaHsd * C57BL/6J J:85462 View
Dent disease Clcn5tm1Gug/Y involves: 129S1/Sv * 129X1/SvJ * C57BL/6J J:66560 View
Dent disease Clcn5tm1Tjj/Y B6.129-Clcn5tm1Tjj J:77111 View
familial juvenile hyperuricemic nephropathy Tg(Umod*C147W)958Lura/0 involves: FVB J:161532 View
familial juvenile hyperuricemic nephropathy Umodtm1Kuma/Umodtm1Kuma involves: 129 J:96653 View
focal segmental glomerulosclerosis 1 Actn4tm1Mrpk/Actn4tm1Mrpk involves: 129 * C57BL/6 J:83911 View
focal segmental glomerulosclerosis 2 Tg(NPHS2-Trpc6)F419Walz/0 involves: C57BL/6J * CBA/J J:165112 View
focal segmental glomerulosclerosis 2 Tg(NPHS2-Trpc6*E896K)F75aWalz/0 involves: C57BL/6J * CBA/J J:165112 View
focal segmental glomerulosclerosis 2 Tg(NPHS2-Trpc6*P111Q)F615Walz/0 involves: C57BL/6J * CBA/J J:165112 View
focal segmental glomerulosclerosis 3 Cd2apem1Irgu/Cd2apem1Irgu C57BL/6-Cd2apem1Irgu J:294238 View
Gitelman syndrome Slc12a3em3Gpt/Slc12a3em4Gpt involves: C57BL/6 J:336073 View
Gitelman syndrome Slc12a3tm1Ges/Slc12a3tm1Ges Not Specified J:50596 View
hemolytic-uremic syndrome Cfhtm1Mbo/Cfhtm1Mbo
Tg(CAG-Cfh*)#Mcp/0		 involves: 129/Sv * C57BL/6 * CBA J:125860 View
IgA glomerulonephritis Scgb1a1tm1Abm/Scgb1a1tm1Abm involves: 129S1/Sv * 129X1/SvJ J:57504 View
IgA glomerulonephritis Tg(MMTV-Scgb1a1)#Abm/0 involves: C57BL/6 * SJL J:57504 View
karyomegalic interstitial nephritis Fan1tm1.1Jrou/Fan1tm1.1Jrou involves: 129P2/OlaHsd J:232403 View
karyomegalic interstitial nephritis Fan1tm1a(KOMP)Wtsi/Fan1tm1a(KOMP)Wtsi 129S1.B6-Fan1tm1a(KOMP)Wtsi J:242198 View
karyomegalic interstitial nephritis Fan1tm1d(KOMP)Wtsi/Fan1tm1d(KOMP)Wtsi involves: C57BL/6N * FVB/N J:232402 View
Liddle syndrome Scnn1btm1.1Ipt/Scnn1btm1.1Ipt involves: 129P2/OlaHsd * C57BL/6J * FVB/N J:59840 View
nephrogenic diabetes insipidus Aqp2cph/Aqp2cph C57BL/6J-Aqp2cph J:109463 View
nephrogenic diabetes insipidus Aqp2F204V/Aqp2F204V C57BL/6-Aqp2F204V J:105809 View
nephrogenic diabetes insipidus Aqp2tm1(AQP2)Suc/Aqp2+ involves: 129S4/SvJae * C57BL/6 J:113716 View
nephrogenic diabetes insipidus Aqp2tm1(cre)Blyg/Aqp2tm1(cre)Blyg involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:121445 View
nephrogenic diabetes insipidus Avpr2tm1Jwe/Avpr2+ involves: 129S1/Sv * 129X1/SvJ * CF-1 J:66094 View
nephrogenic diabetes insipidus Avpr2tm1Jwe/Y involves: 129S1/Sv * 129X1/SvJ * CF-1 J:66094 View
nephronophthisis 1 Nphp1em1Lisu/Nphp1em1Lisu C57BL/6J-Nphp1em1Lisu J:324503 View
nephronophthisis 2 Invsinv/Invsinv involves: FVB/N J:132552 View
nephronophthisis 3 Nphp3pcy/Nphp3pcy involves: KK J:91453 View
nephronophthisis 3 Nphp3pcy/Nphp3tm1Cbe involves: C57BL/6 * CD-1 * KK/Upj J:139258 View
nephronophthisis 4 Nphp4nmf192/Nphp4nmf192 involves: C57BL/6J J:167232 View
nephronophthisis 7 Glis2tm1Tre/Glis2tm1Tre B6.129P2-Glis2tm1Tre J:123510 View
neurohypophyseal diabetes insipidus Avptm1Hari/Avp+ involves: 129S1/Sv * 129X1/SvJ * C57BL/6J J:147993 View
neurohypophyseal diabetes insipidus Avptm1Lja/Avp+ involves: 129S1/Sv * 129X1/SvJ J:148012 View
polycystic kidney disease 1 Gpsm1tm1.1Lajb/Gpsm1tm1.1Lajb
Pkd1tm1.1Fqi/Pkd1tm1.1Fqi		 involves: 129S6/SvEvTac J:193175 View
polycystic kidney disease 1 Pkd1b2b1585Clo/Pkd1b2b1585Clo C57BL/6J-Pkd1b2b1585Clo J:175213 View
polycystic kidney disease 1 Pkd1tm1.1Fqi/Pkd1tm1.1Fqi involves: 129S6/SvEvTac J:193175 View
polycystic kidney disease 1 Pkd1tm1.1Pcha/Pkd1tm1.1Pcha involves: 129S1/Sv * C57BL/6 J:193544 View
polycystic kidney disease 1 Pkd1tm1.1Pcha/Pkd1tm2Som
Tg(Cdh16-cre)91Igr/0		 involves: 129 * 129S4/SvJae * C57BL/6 * ICR J:244067 View
polycystic kidney disease 1 Pkd1tm1Bdgz/Pkd1+ involves: 129S1/Sv * 129X1/SvJ J:130086 View
polycystic kidney disease 1 Pkd1tm1Djmp/Pkd1tm1Djmp involves: 129P2/OlaHsd * C57BL/6 J:94582 View
polycystic kidney disease 1 Pkd1tm1Ggg/Pkd1tm1Ggg Not Specified J:76062 View
polycystic kidney disease 1 Pkd1tm1Gztn/Pkd1tm1Gztn
Gt(ROSA)26Sortm9(cre/ESR1)Arte/Gt(ROSA)26Sor+		 involves: 129S/Sv * 129S7/SvEvBrd * C57BL/6 J:162080 View
polycystic kidney disease 1 Pkd1tm1Jzh/Pkd1+ either: (involves: 129S4/SvJae * C57BL/6) or (involves: 129S4/SvJae * BALB/c) J:43193, J:52573, J:72627 View
polycystic kidney disease 1 Pkd1tm1Jzh/Pkd1tm1Jzh either: (involves: 129S4/SvJae * C57BL/6) or (involves: 129S4/SvJae * BALB/c) J:43193, J:72627, J:81443 View
polycystic kidney disease 1 Pkd1tm1Rsa/Pkd1+ involves: 129S4/SvJaeSor J:72238 View
polycystic kidney disease 1 Pkd1tm1Shh/Pkd1tm1.1Pcha involves: 129P2/OlaHsd * 129S1/Sv * C57BL/6 J:193544 View
polycystic kidney disease 1 Pkd1tm1Som/Pkd1+
Tg(Pkd1*)39Mtru/0		 involves: 129/Sv * C57BL/6J * CBA/J * SJL J:198147 View
polycystic kidney disease 1 Pkd1tm2.1Ggg/Pkd1tm2.1Ggg involves: 129S4/SvJae * Black Swiss * C57BL/6 J:103719 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(Col1a1-cre)1Bek/0		 involves: 129S4/SvJae * CD-1 J:191967 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(Hoxb7-cre)13Amc/0		 involves: 129S4/SvJae * C57BL/6 J:171619 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(MMTV-cre)4Mam/0		 involves: 129S4/SvJae * FVB J:103719 View
polycystic kidney disease 1 Pkd1tm2Ggg/Pkd1tm2Ggg
Tg(Nes-cre)Wme/0		 involves: 129S4/SvJae * C57BL/6 * CBA J:185855 View
polycystic kidney disease 1 Pkd1tm2Jzh/Pkd1+ either: (involves: 129S4/SvJae * BALB/c) or (involves: 129S4/SvJae * C57BL/6) J:72627 View
polycystic kidney disease 1 Pkd1tm2Jzh/Pkd1tm2Jzh either: (involves: 129S4/SvJae * BALB/c) or (involves: 129S4/SvJae * C57BL/6) J:72627 View
polycystic kidney disease 1 Pkd1tm2Jzh/Pkd1tm2Jzh involves: 129S4/SvJae * C57BL/6 J:140012 View
polycystic kidney disease 1 Pkd1tm2Som/Pkd1tm2.1Som
Tg(Cdh16-cre)91Igr/0		 involves: C57BL/6 * ICR * SJL J:135301 View
polycystic kidney disease 1 Pkd1tm2Som/Pkd1tm2Som
Tg(Cdh16-cre)91Igr/0		 involves: 129S4/SvJae * C57BL/6 * ICR J:244067 View
polycystic kidney disease 1 Pkd1tm3.1Jzh/Pkd1tm3.1Jzh involves: 129P2/OlaHsd * C57BL/6 J:140012 View
polycystic kidney disease 1 Pkd1tm3Jzh/Pkd1tm3Jzh
Tg(Ggt1-cre)M3Egn/0		 involves: 129P2/OlaHsd * C57BL/6 * SJL J:140012 View
polycystic kidney disease 1 Tg(Pkd1*)39Mtru/0 involves: C57BL/6J * CBA/J J:198147 View
polycystic kidney disease 2 Pkd2tm1Dwo/Pkd2tm1Dwo either: (involves: 129S1/Sv * 129X1/SvJ) or (involves: 129S1/Sv * 129X1/SvJ * C57BL/6) J:77401 View
polycystic kidney disease 2 Pkd2tm1Som/Pkd2+ involves: 129/Sv * C57BL/6J * SJL J:47035 View
polycystic kidney disease 2 Pkd2tm1Som/Pkd2tm1Som involves: 129/Sv * C57BL/6J * SJL J:47035 View
polycystic kidney disease 2 Pkd2tm1Som/Pkd2tm2Som involves: 129/Sv * C57BL/6J * SJL J:47035 View
polycystic kidney disease 2 Pkd2tm2Som/Pkd2+ involves: 129/Sv * C57BL/6J * SJL J:59314 View
polycystic kidney disease 2 Pkd2tm2Som/Pkd2tm2Som involves: 129/Sv * C57BL/6J * SJL J:59314 View
polycystic kidney disease 2 Pkd2tm3Som/Pkd2tm3Som
Tg(Pkhd1-cre)1Igr/0		 involves: 129S4/SvJae * C57BL/6 J:244067 View
polycystic kidney disease 4 Pkhd1em1Mrug/Pkhd1+ involves: C57BL/6J J:281464 View
polycystic kidney disease 4 Pkhd1em1Mrug/Pkhd1em1Mrug involves: C57BL/6J J:281464 View
pseudohypoaldosteronism Klhl3tm1.1Esoh/Klhl3+ involves: C57BL/6 J:214330 View
pseudohypoaldosteronism Klhl3tm1.1Slin/Klhl3+ Not Specified J:284284 View
pseudohypoaldosteronism Klhl3tm1.1Slin/Klhl3tm1.1Slin Not Specified J:284284 View
pseudohypoaldosteronism Klhl3tm2.1Esoh/Klhl3tm2.1Esoh involves: C57BL/6 * C57BL/6J J:244278 View
pseudohypoaldosteronism Wnk4em1Cjc/Wnk4em1Cjc Not Specified J:274218 View
renal tubular acidosis Atp6v0a4tm1.1Fekf/Atp6v0a4tm1.1Fekf involves: C57BL/6 J:188593 View
renal tubular acidosis Slc4a1tm1Llp/Slc4a1tm1Llp involves: 129S4/SvJae * C57BL/6J J:148154 View
renal tubular acidosis Slc4a4tm1.1Slin/Slc4a4tm1.1Slin involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:186877 View
X-linked nephrogenic diabetes insipidus Avpr2tm2.1Jwe/Y
Tg(CAG-cre/Esr1*)5Amc/0		 involves: 129 * C57BL/6 J:324922 View
      autosomal dominant polycystic kidney disease Bicc1jcpk/Bicc1+ involves: 101 * C3H * T STOCK J:23047 View
autosomal dominant polycystic kidney disease Nphp3pcy/Nphp3pcy either: D2.KK-Nphp3pcy or (involves: DBA/2Fg * DBA/2J * KK) J:11399 View
autosomal dominant polycystic kidney disease Nphp3pcy/Nphp3pcy involves: KK J:244067 View
autosomal dominant polycystic kidney disease Nphp3pcy/Nphp3pcy KK-Nphp3pcy J:8302 View
autosomal dominant polycystic kidney disease Tg(HBB-Myc)#Cos/0 involves: C57BL/6J * CBA/J J:45203 View
autosomal recessive polycystic kidney disease Arl3Gt(OST263303)Lex/Arl3Gt(OST263303)Lex involves: 129S5/SvEvBrd J:107331 View
autosomal recessive polycystic kidney disease Bicc1jcpk-bpk/Bicc1jcpk-bpk BALB/c-Bicc1jcpk-bpk J:13276, J:21554, J:36348 View
autosomal recessive polycystic kidney disease Bicc1jcpk-bpk/Bicc1jcpk-bpk involves: BALB/c * CAST/EiJ J:36348 View
autosomal recessive polycystic kidney disease Bicc1jcpk/Bicc1jcpk-bpk involves: 101 * BALB/c * C3H * C57BL/6J * T STOCK J:36348 View
autosomal recessive polycystic kidney disease Bicc1jcpk/Bicc1jcpk involves: 101 * C3H * C57BL/6J * T STOCK J:36348 View
autosomal recessive polycystic kidney disease Bicc1jcpk/Bicc1jcpk involves: 101 * C3H * T STOCK J:23047 View
autosomal recessive polycystic kidney disease Bicc1tm1Emdr/Bicc1tm1Emdr B6SJL-Bicc1tm1Emdr J:121683 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk B6(Cg)-Cys1cpk/J J:6718, J:9290 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk B6(Cg)-Cys1cpk/JUnc J:7202 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk C.B6(Cg)-Cys1cpk J:99616 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk D2J.B6(Cg)-Cys1cpk J:99620 View
autosomal recessive polycystic kidney disease Cys1cpk/Cys1cpk involves: C57BL/6J * CD-1 J:33739 View
autosomal recessive polycystic kidney disease Dzip1lwarpy/Dzip1lwarpy involves: C3H * C57BL/6 J:249936 View
autosomal recessive polycystic kidney disease Dzip1lwarpy/Dzip1lwarpy involves: C57BL/6 * CD-1 J:249936 View
autosomal recessive polycystic kidney disease Ift88Tg737Rpw/Ift88Tg737Rpw C3.FVB-Ift88Tg737Rpw J:18508, J:73583 View
autosomal recessive polycystic kidney disease Ift88Tg737Rpw/Ift88Tg737Rpw FVB/N-Ift88Tg737Rpw J:18508, J:37149, J:73583, J:95813 View
autosomal recessive polycystic kidney disease Ift88Tg737Rpw/Ift88Tg737Rpw involves: C3H * FVB/N J:73583 View
autosomal recessive polycystic kidney disease Ift88Tg737Rpw/Ift88Tg737Rpw involves: FVB/N J:65500, J:90990 View
autosomal recessive polycystic kidney disease Nek1kat-2J/Nek1kat-2J C57BL/6J-Nek1kat-2J/J J:37799 View
autosomal recessive polycystic kidney disease Nek1kat/Nek1kat involves: C3HeB/FeJLe * C57BL/6J * RBF/Dn J:37799 View
autosomal recessive polycystic kidney disease Nek8jck/Nek8jck involves: C57BL/6J J:11885 View
autosomal recessive polycystic kidney disease Pkd1m1Bei/Pkd1m1Bei involves: A/J * FVB/N J:75360 View
autosomal recessive polycystic kidney disease Sclt1Tg(CAG-sb10)1Dla/Sclt1Tg(CAG-sb10)1Dla FVB/N-Sclt1Tg(CAG-sb10)1Dla J:243427 View
autosomal recessive polycystic kidney disease Tg(Pkd1)26Mtru/0 involves: C57BL/6J * CBA/J J:157952 View
autosomal recessive polycystic kidney disease Tsc1tm1Djk/Tsc1tm1Djk
Tg(Pax8-rtTA2S*M2)1Koes/0
Tg(tetO-cre)LC1Bjd/0		 involves: 129S4/SvJae * BALB/c * C57BL/6 * DBA J:140925 View
autosomal recessive pseudohypoaldosteronism type 1 Scnn1btm1Wsh/Scnn1btm1Wsh involves: 129S1/Sv * 129X1/SvJ * C57BL/6J J:53058 View
autosomal recessive pseudohypoaldosteronism type 1 Scnn1gtm1Bhk/Scnn1gtm1Bhk involves: 129P2/OlaHsd * C57BL/6 * DBA/2 J:50528 View
Bartter disease Clcnkbtm1.1Doel/Clcnkbtm1.1Doel involves: 129S1/Sv * 129X1/SvJ J:259639 View
bilateral renal aplasia Npntem1Zhwe/Npntem1Zhwe C57BL/6-Npntem1Zhwe J:314482 View
cystic kidney disease b2b243.2Clo/b2b243.2Clo C57BL/6J-b2b243.2Clo J:175213 View
cystic kidney disease b2b243Clo/b2b243Clo C57BL/6J-b2b243Clo J:175213 View
cystic kidney disease b2b1146Clo/b2b1146Clo C57BL/6J-b2b1146Clo J:175213 View
cystic kidney disease b2b1163Clo/b2b1163Clo C57BL/6J-b2b1163Clo J:175213 View
cystic kidney disease b2b1200.2Clo/b2b1200.2Clo C57BL/6J-b2b1200.2Clo J:175213 View
cystic kidney disease b2b1200Clo/b2b1200Clo C57BL/6J-b2b1200Clo J:175213 View
cystic kidney disease b2b1291.2Clo/b2b1291.2Clo C57BL/6J-b2b1291.2Clo J:175213 View
cystic kidney disease b2b1291Clo/b2b1291Clo C57BL/6J-b2b1291Clo J:175213 View
cystic kidney disease b2b2059Clo/b2b2059Clo C57BL/6J-b2b2059Clo J:175213 View
cystic kidney disease b2b2459Clo/b2b2459Clo C57BL/6J-b2b2459Clo J:175213 View
cystic kidney disease Bicc1b2b222Clo/Bicc1b2b222Clo C57BL/6J-Bicc1b2b222Clo J:175213 View
cystic kidney disease Cep290b2b1454Clo/Cep290b2b1454Clo C57BL/6J-Cep290b2b1454Clo J:175213 View
cystic kidney disease Dnm2b2b2159Clo/Dnm2b2b2159Clo C57BL/6J-Dnm2b2b2159Clo J:175213 View
cystic kidney disease Ephb4b2b2412Clo/Ephb4b2b2412Clo C57BL/6J-Ephb4b2b2412Clo J:175213 View
cystic kidney disease Lama5tm3Jhm/Lama5tm3Jhm involves: 129S1/Sv * 129X1/SvJ J:128225 View
cystic kidney disease Robo1b2b872Clo/Robo1b2b872Clo C57BL/6J-Robo1b2b872Clo J:175213 View
cystic kidney disease Slit2b2b1200.1Clo/Slit2b2b1200.1Clo C57BL/6J-Slit2b2b1200.1Clo J:175213 View
cystic kidney disease Tmem67b2b1163.1Clo/Tmem67b2b1163.1Clo C57BL/6J-Tmem67b2b1163.1Clo J:175213 View
cystic kidney disease Tmem67b2b1291.1Clo/Tmem67b2b1291.1Clo C57BL/6J-Tmem67b2b1291.1Clo J:175213 View
cystic kidney disease Ttc21btm2c(KOMP)Wtsi/Ttc21baln
Gt(ROSA)26Sortm1(cre/ERT)Nat/Gt(ROSA)26Sor+		 involves: 129S1/Sv * 129X1/SvJ * A/J * C57BL/6N J:213263 View
end stage renal disease Cd2apem1Irgu/Cd2apem1Irgu C57BL/6-Cd2apem1Irgu J:294238 View
Fanconi syndrome Hnf4atm1Sad/Hnf4atm1Sad
Six2tm1(tTA,tetO-EGFP/cre)Amc/Six2+		 involves: 129 * 129S1/Sv * 129X1/SvJ * C57BL/6J J:266356 View
Fanconi syndrome Lrp2tm1Her/Lrp2tm1Her involves: 129S7/SvEvBrd J:108230 View
focal segmental glomerulosclerosis Cmastm1.1Bwei/Cmastm1.1Bwei
Tg(NPHS2-cre)295Lbh/0		 involves: 129P2/OlaHsd * C57BL/6 * SJL J:286022 View
focal segmental glomerulosclerosis Gt(ROSA)26Sortm3(tetO-Mir193)Arte/Gt(ROSA)26Sor+ involves: 129 * BALB/c * C57BL/6 J:197989 View
focal segmental glomerulosclerosis Gt(ROSA)26Sortm3(tetO-Mir193)Arte/Gt(ROSA)26Sortm3(tetO-Mir193)Arte involves: 129 * BALB/c * C57BL/6 J:197989 View
focal segmental glomerulosclerosis Myo9aem1Atuf/Myo9a+ C57BL/6J-Myo9aem1Atuf J:302901 View
focal segmental glomerulosclerosis Srgap1tm1a(KOMP)Wtsi/Srgap1tm1a(KOMP)Wtsi
Six2tm1(tTA,tetO-EGFP/cre)Amc/Six2+		 involves: 129 * C57BL/6J * C57BL/6N J:333727 View
focal segmental glomerulosclerosis Tnfaip2tm1.1Ohno/Tnfaip2tm1.1Ohno C.Cg-Tnfaip2tm1.1Ohno J:343202 View
Gitelman syndrome Stk39tm1.2Slin/Stk39tm1.2Slin involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:165706 View
Gitelman syndrome Stk39tm1Pawe/Stk39tm1Pawe involves: 129S6/SvEvTac * C57BL/6J J:287773 View
Gitelman syndrome Stk39tm2.1Arte/Stk39tm2.1Arte involves: C57BL/6J J:224087 View
Gitelman syndrome Wnk4tm1Pfi/Wnk4tm1Pfi involves: 129S6/SvEvTac * C57BL/6J J:184790 View
glomerulonephritis Cfiem1Jiwe/Cfiem1Jiwe involves: C57BL/6J J:308307 View
IgA glomerulonephritis B4galt1tm1Yiw/B4galt1tm1Yiw involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:117891 View
IgA glomerulonephritis Tg(Lck-Tnfsf14)24Yxf/? C57BL/6-Tg(Lck-Tnfsf14)24Yxf J:128976 View
IgA glomerulonephritis Tg(Tnfsf13b)1Fma/Tg(Tnfsf13b)1Fma involves: C57BL/6 * DBA/2 J:178227 View
IgA glomerulonephritis Wastm1Sbs/Wastm1Sbs 129S6/SvEvTac-Wastm1Sbs/J J:180407 View
kidney disease Col4a1tm1.1Ics/Col4a1+ involves: 129S2/SvPas * C57BL/6 J:240798 View
kidney disease Col4a1tm1.1Ics/Col4a1tm1.1Ics involves: 129S2/SvPas * C57BL/6 J:240798 View
kidney disease Tg(Umod*C147W)958Lura/0 involves: FVB J:161532 View
kidney disease Umodem1Duf/Umod+ C57BL/6J-Umodem1Duf J:252597 View
kidney disease UmodUrehd1/Umod+ involves: C3HeB/FeJ J:201084 View
kidney disease UmodUrehd1/UmodUrehd1 involves: C3HeB/FeJ J:201084 View
kidney disease Umodurehr4/Umodurehr4 C3HeB/FeJ-Umodurehr4 J:153895 View
membranoproliferative glomerulonephritis Cfhtm1Mbo/Cfhtm1Mbo involves: 129/Sv * C57BL/6 J:78193 View
membranoproliferative glomerulonephritis Tg(Lck-Tslp)1Chea/0 B6.Cg-Tg(Lck-Tslp)1Chea J:72982 View
nephroblastoma Tg(Ddx4-cre)1Dcas/0
Tg(EIF1AX-Lin28a)#Gqda/0		 involves: 129S4/SvJae * C57BL/6 * CD-1 * FVB/N J:211179 View
nephrocalcinosis Brd4M1Rvt/Brd4+ involves: BALB/cAnNCrl * C3H/HeH J:277882 View
nephrocalcinosis Polg2M1Rvt/Polg2+ involves: BALB/c * C3H/HeH J:277879 View
nephrogenic diabetes insipidus Aqp3tm1Ask/Aqp3tm1Ask involves: C57BL/6J J:61675 View
nephrogenic diabetes insipidus Clcnkatm1Suc/Clcnkatm1Suc involves: 129P2/OlaHsd * C57BL/6 J:51917 View
nephrogenic diabetes insipidus Grntm1.1Aidi/Grntm1.1Aidi involves: C57BL/6J J:268827 View
nephrogenic diabetes insipidus Sirt1tm1Mcby/Sirt1tm1Mcby involves: 129S1/Sv * 129X1/SvJ * CD-1 J:160869 View
nephrogenic diabetes insipidus Uoxtm1Bay/Uoxtm1Bay involves: 129S7/SvEvBrd * C57BL/6J J:103187 View
nephronophthisis Ahi1tm1Jgg/Ahi1+
Lrp6Gt(Ex187)Byg/Lrp6+		 involves: 129P2/OlaHsd * 129S1/Sv * 129X1/SvJ J:154321 View
nephronophthisis Ahi1tm1Jgg/Ahi1tm1Jgg
Tg(TCF/Lef1-lacZ)34Efu/0		 involves: 129S1/Sv * 129X1/SvJ J:154321 View
nephronophthisis Cntrlb2b1468.1Clo/Cntrlb2b1468.1Clo C57BL/6J-Cntrlb2b1468.1Clo J:175213 View
nephronophthisis Sdccag8Gt(OST40418)Lex/Sdccag8Gt(OST40418)Lex involves: 129S5/SvEvBrd * C57BL/6J J:226661 View
nephronophthisis Wwtr1tm1Whun/Wwtr1tm1Whun either: (involves: 129S6/SvEvTac) or (involves: 129S6/SvEvTac * C57BL/6) J:119488 View
nephrosis Lamb2tm1Jrs/Lamb2tm1Jrs involves: 129S1/Sv * 129X1/SvJ J:27732 View
nephrotic syndrome Arhgdiatm1Ytk/Arhgdiatm1Ytk involves: 129S/SvEv * C57BL/6 * DBA J:57995 View
nephrotic syndrome Fat1tm1.1Nsib/Fat1tm1.1Nsib
Tg(NPHS2-cre)295Lbh/0		 involves: 129/Sv * 129S4/SvJaeSor * C57BL/6 * C57BL/6J * SJL J:234732 View
nephrotic syndrome Itsn2tm1Kure/Itsn2tm1Kure involves: C57BL/6 J:262845 View
nephrotic syndrome Mpv17/Mpv17 CFW-Mpv17/J J:10661, J:108252 View
nephrotic syndrome Nphs1Gt(pT1Betageo)1Ruiz/Nphs1+ involves: 129P2/OlaHsd * C57BL/6 J:86048 View
nephrotic syndrome Nphs1Gt(pT1Betageo)1Ruiz/Nphs1Gt(pT1Betageo)1Ruiz involves: 129P2/OlaHsd * C57BL/6 J:86048 View
nephrotic syndrome Nphs1tm1Ktry/Nphs1tm1Ktry involves: 129X1/SvJ * C57BL/6 J:66970 View
nephrotic syndrome Nphs1tm1Rkl/Nphs1tm1Rkl involves: 129S2/SvPasCrl J:78616 View
nephrotic syndrome Nphs2tm1Antc/Nphs2tm1Antc 129-Nphs2tm1Antc J:87577 View
nephrotic syndrome Nphs2tm1Antc/Nphs2tm1Antc involves: 129 * C57BL/6J J:87577 View
nephrotic syndrome Nphs2tm1Antc/Nphs2tm3.1Antc
Tg(CAG-cre/Esr1*)86Lbgn/0		 involves: 129 * C57BL/6 * DBA J:166320 View
nephrotic syndrome Nphs2tm2.1Antc/Nphs2tm3.1Antc
Tg(CAG-cre/Esr1*)86Lbgn/0		 involves: 129S2/SvPas * C57BL/6 * DBA J:245693 View
nonpapillary renal cell carcinoma Flcntm1Btt/Flcntm1Btt
Tg(Cdh16-cre)91Igr/0		 involves: 129S4/SvJaeSor * C57BL/6 * ICR J:143922 View
obstructive nephropathy Exoc5tm1c(KOMP)Mbp/Exoc5tm1c(KOMP)Mbp
Tg(Cdh16-cre)91Igr/0		 involves: 129S4/SvJaeSor * C57BL/6N * ICR J:226950, J:250161 View
obstructive nephropathy Mocosem2(IMPC)Ics/Mocosem2(IMPC)Ics involves: C57BL/6N J:336718 View
oligomeganephronia Bcl2tm1Dlo/Bcl2tm1Dlo involves: 129P2/OlaHsd * C57BL/6 J:111022 View
polycystic kidney disease Kif3atm1Gsn/Kif3atm2Gsn
Tg(Cdh16-cre)91Igr/0		 involves: 129S1/Sv * 129X1/SvJ * C57BL/6 * ICR J:83293 View
polycystic kidney disease Tg(Actb-Ptma)T12Clwu/Tg(Actb-Ptma)T12Clwu involves: FVB/N J:128557 View
polycystic kidney disease Tulp3m1Kflj/Tulp3m1Kflj involves: C57BL/6J * FVB/NJ J:284006 View
polycystic kidney disease Xylt2tm1Meh/Xylt2tm1Meh involves: 129P2/OlaHsd J:122291 View
pseudohypoaldosteronism Stk39tm1Pawe/Stk39tm1Pawe
Pvalbtm1(cre)Arbr/Pvalb+		 B6.129-Stk39tm1Pawe Pvalbtm1(cre)Arbr J:287773 View
renal cell carcinoma Nf2tm2Gth/Nf2tm2Gth
Tg(Vil1-cre)20Syr/0		 involves: 129P2/OlaHsd * C57BL/6 * DBA/2 J:150071 View
renal glycosuria Hnrnpftm1Jsdc/Hnrnpftm1Jsdc
Pax8tm1.1(cre)Mbu/Pax8+		 involves: 129P2/OlaHsd * C57BL/6 J:284239 View
      Dent disease Inpp5btm1Nbm/Inpp5btm1Nbm
Ocrltm1Nbm/Ocrltm1Nbm
Tg(INPP5B)CNbm/0		 involves: 129S/SvEv * 129S6/SvEvTac * FVB/N J:185879 View
Dent disease Inpp5btm1Nbm/Inpp5btm1Nbm
Ocrltm1Nbm/Y
Tg(INPP5B)CNbm/0		 involves: 129S/SvEv * 129S6/SvEvTac * FVB/N J:185879 View
nephroblastoma Col1a1tm2(tetO-LIN28B)Gqda/Col1a1+
Gt(ROSA)26Sortm1(rtTA,EGFP)Nagy/Gt(ROSA)26Sor+
Wt1tm2(cre/ERT2)Wtp/Wt1+		 involves: 129S1/Sv * 129S4/SvJae * 129X1/SvJ * C57BL/6 J:211179 View
Transgenes and
Other Mutations		     autosomal recessive polycystic kidney disease T(2;10)67Gso/T(2;10)67Gso involves: 101 * C3H * C3H/Rl * C57BL/RlGso * SEC/RlGso J:75799 View
cystic kidney disease Tg(Pax8-rtTA2S*M2)1Koes/0
Tg(tetO-MYC)36aBop/0		 involves: C57BL/6 * DBA * FVB/N J:140925 View
cystic kidney disease Tg(Pklr-HRAS*G12V)21Ak/0 involves: C57BL/6 * DBA/2 J:44803 View
familial juvenile hyperuricemic nephropathy Tg(Umod*C217G)1Xrw/0 involves: FVB/N J:252420 View
focal segmental glomerulosclerosis Tg(Thy1/THY1)T6Gsv/0 involves: C57BL/10 * CBA J:294728, J:294621 View
IgA glomerulonephritis Tg(Itgam-FCAR)83Rcmo/0 involves: C57BL/6 * NOD J:120534 View
kidney disease mgb/mgb involves: C57BL/6 * FVB/N J:207566 View
kidney disease Tg(Nphs1-rtTA*3G)8Jhm/0
Tg(tetO-GFP,-APOL1*)#Susz/0		 involves: C57BL/6J * CBA/J * FVB/N J:251848 View
kidney disease Tg(Nphs1-rtTA*3G)8Jhm/0
Tg(tetO-GFP,-APOL1*S342G*I384M)#Susz/0		 involves: C57BL/6J * CBA/J * FVB/N J:251848 View
polycystic kidney disease 2 Tg(CAG-PKD2)#Hwl/? involves: FVB/NJ J:148377 View
Additional
Complex
Models		     autosomal recessive pseudohypoaldosteronism type 1 Scnn1atm1Rss/Scnn1atm1Rss
Tg(CMV-Scnn1a)1352Rss/0		 involves: 129P2/OlaHsd * NMRI J:43583 View
focal segmental glomerulosclerosis Gt(ROSA)26Sortm1Sor/Gt(ROSA)26Sortm1Sor
Tg(NPHS2-rtTA2*M2)1Jbk/Tg(NPHS2-rtTA2*M2)1Jbk
Tg(tetO-cre)LC1Bjd/Tg(tetO-cre)LC1Bjd		 involves: 129S4/SvJaeSor * BALB/c * C57BL/6 * FVB/N J:285673 View
kidney disease Uoxin/Uoxin involves: C57BL/6J * DBA/2J J:70677 View
membranous glomerulonephritis Faslpr/Faslpr
Il27ratm1Mak/Il27ratm1Mak		 MRL.Cg-Il27ratm1Mak Faslpr J:122148 View
nephrogenic diabetes insipidus Nos1tm1Plh/Nos1tm1Plh
Nos2tm1Mrl/Nos2tm1Mrl
Nos3tm1Plh/Nos3tm1Plh		 involves: 129S4/SvJae * 129S7/SvEvBrd J:100308 View
nephrotic syndrome Hprt1tm1(Nphs1-CMIP)Dsah/Hprt1+ B6.Cg-Hprt1tm1(Nphs1-CMIP)Dsah J:185411 View
polycystic kidney disease MitfTg(Tff3-Tmem207)2Tamo/Mitf+ involves: C57BL/6 J:244533 View
polycystic kidney disease MitfTg(Tff3-Tmem207)2Tamo/MitfTg(Tff3-Tmem207)2Tamo involves: C57BL/6 J:244533 View
renal tubular transport disease Igktm1.1Cog/Igktm1.1Cog involves: 129P2/OlaHsd * C57BL/6 * FVB/N J:135758 View
renal tubular transport disease Igktm1.1Cog/Igktm1.2Cog involves: 129P2/OlaHsd * C57BL/6 * FVB/N J:135758 View

       
No similarity to the expected human disease phenotype was found.
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
NOT Models      autosomal recessive polycystic kidney disease Pkhd1tm1Rbu/Pkhd1tm1Rbu involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:112509 View
focal segmental glomerulosclerosis 1 Tg(CMV-Plaur*)19Lbh/0 FVB/N-Tg(CMV-Plaur*)19Lbh J:217443 View
nephronophthisis 1 Nphp1tm1.1Hung/Nphp1tm1.1Hung B6.Cg-Nphp1tm1.1Hung J:140205 View
pseudohypoaldosteronism Cul3tm1Suc/Cul3+ involves: C57BL/6 J:226618 View
pseudohypoaldosteronism Cul3tm2Suc/Cul3tm2Suc involves: C57BL/6 J:226618 View